id	sid	tid	token	lemma	pos
bam-9798	1	1	exercise	exercise	NOUN
bam-9798	1	2	and	and	CCONJ
bam-9798	1	3	nutrition	nutrition	NOUN
bam-9798	1	4	in	in	ADP
bam-9798	1	5	late	late	ADJ
bam-9798	1	6	onset	onset	ADJ
bam-9798	1	7	pompe	pompe	PROPN
bam-9798	1	8	disease	disease	PROPN
bam-9798	1	9	eur	eur	PROPN
bam-9798	1	10	j	j	PROPN
bam-9798	1	11	transl	transl	PROPN
bam-9798	1	12	myol	myol	ADV
bam-9798	1	13	31	31	NUM
bam-9798	1	14	(	(	PUNCT
bam-9798	1	15	2	2	NUM
bam-9798	1	16	):	):	PUNCT
bam-9798	1	17	9798	9798	NUM
bam-9798	1	18	,	,	PUNCT
bam-9798	1	19	2021	2021	NUM
bam-9798	1	20	doi	doi	NOUN
bam-9798	1	21	:	:	PUNCT
bam-9798	1	22	10.4081	10.4081	NUM
bam-9798	1	23	/	/	SYM
bam-9798	1	24	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	1	25	1	1	NUM
bam-9798	1	26	exercise	exercise	NOUN
bam-9798	1	27	,	,	PUNCT
bam-9798	1	28	nutrition	nutrition	NOUN
bam-9798	1	29	and	and	CCONJ
bam-9798	1	30	enzyme	enzyme	NOUN
bam-9798	1	31	replacement	replacement	NOUN
bam-9798	1	32	therapy	therapy	NOUN
bam-9798	1	33	are	be	AUX
bam-9798	1	34	efficacious	efficacious	ADJ
bam-9798	1	35	in	in	ADP
bam-9798	1	36	adult	adult	NOUN
bam-9798	1	37	pompe	pompe	NOUN
bam-9798	1	38	patients	patient	NOUN
bam-9798	1	39	:	:	PUNCT
bam-9798	1	40	report	report	NOUN
bam-9798	1	41	from	from	ADP
bam-9798	1	42	epoc	epoc	PROPN
bam-9798	1	43	consortium	consortium	PROPN
bam-9798	1	44	corrado	corrado	PROPN
bam-9798	1	45	angelini	angelini	PROPN
bam-9798	1	46	neuromuscular	neuromuscular	ADJ
bam-9798	1	47	laboratory	laboratory	NOUN
bam-9798	1	48	,	,	PUNCT
bam-9798	1	49	department	department	NOUN
bam-9798	1	50	of	of	ADP
bam-9798	1	51	neurosciences	neuroscience	NOUN
bam-9798	1	52	,	,	PUNCT
bam-9798	1	53	university	university	NOUN
bam-9798	1	54	of	of	ADP
bam-9798	1	55	padova	padova	PROPN
bam-9798	1	56	,	,	PUNCT
bam-9798	1	57	padova	padova	PROPN
bam-9798	1	58	,	,	PUNCT
bam-9798	1	59	italy	italy	PROPN
bam-9798	1	60	this	this	DET
bam-9798	1	61	article	article	NOUN
bam-9798	1	62	is	be	AUX
bam-9798	1	63	distributed	distribute	VERB
bam-9798	1	64	under	under	ADP
bam-9798	1	65	the	the	DET
bam-9798	1	66	terms	term	NOUN
bam-9798	1	67	of	of	ADP
bam-9798	1	68	the	the	DET
bam-9798	1	69	creative	creative	ADJ
bam-9798	1	70	commons	common	NOUN
bam-9798	1	71	attribution	attribution	NOUN
bam-9798	1	72	noncommercial	noncommercial	ADJ
bam-9798	1	73	license	license	NOUN
bam-9798	1	74	(	(	PUNCT
bam-9798	1	75	cc	cc	NOUN
bam-9798	1	76	by	by	ADP
bam-9798	1	77	-	-	PUNCT
bam-9798	1	78	nc	nc	PROPN
bam-9798	1	79	4.0	4.0	NUM
bam-9798	1	80	)	)	PUNCT
bam-9798	1	81	which	which	PRON
bam-9798	1	82	permits	permit	VERB
bam-9798	1	83	any	any	DET
bam-9798	1	84	noncommercial	noncommercial	ADJ
bam-9798	1	85	use	use	NOUN
bam-9798	1	86	,	,	PUNCT
bam-9798	1	87	distribution	distribution	NOUN
bam-9798	1	88	,	,	PUNCT
bam-9798	1	89	and	and	CCONJ
bam-9798	1	90	reproduction	reproduction	NOUN
bam-9798	1	91	in	in	ADP
bam-9798	1	92	any	any	DET
bam-9798	1	93	medium	medium	NOUN
bam-9798	1	94	,	,	PUNCT
bam-9798	1	95	provided	provide	VERB
bam-9798	1	96	the	the	DET
bam-9798	1	97	original	original	ADJ
bam-9798	1	98	author(s	author(s	NOUN
bam-9798	1	99	)	)	PUNCT
bam-9798	1	100	and	and	CCONJ
bam-9798	1	101	source	source	NOUN
bam-9798	1	102	are	be	AUX
bam-9798	1	103	credited	credit	VERB
bam-9798	1	104	.	.	PUNCT
bam-9798	2	1	abstract	abstract	ADJ
bam-9798	2	2	pompe	pompe	PROPN
bam-9798	2	3	disease	disease	PROPN
bam-9798	2	4	,	,	PUNCT
bam-9798	2	5	also	also	ADV
bam-9798	2	6	known	know	VERB
bam-9798	2	7	as	as	ADP
bam-9798	2	8	glycogenosis	glycogenosis	NOUN
bam-9798	2	9	type	type	NOUN
bam-9798	2	10	2	2	NUM
bam-9798	2	11	,	,	PUNCT
bam-9798	2	12	is	be	AUX
bam-9798	2	13	due	due	ADJ
bam-9798	2	14	to	to	ADP
bam-9798	2	15	deficiency	deficiency	NOUN
bam-9798	2	16	in	in	ADP
bam-9798	2	17	lysosomal	lysosomal	ADJ
bam-9798	2	18	alpha	alpha	NOUN
bam-9798	2	19	glucosidase	glucosidase	NOUN
bam-9798	2	20	,	,	PUNCT
bam-9798	2	21	a	a	DET
bam-9798	2	22	lysosomal	lysosomal	ADJ
bam-9798	2	23	hydrolase	hydrolase	NOUN
bam-9798	2	24	,	,	PUNCT
bam-9798	2	25	which	which	PRON
bam-9798	2	26	presents	present	VERB
bam-9798	2	27	infantile	infantile	ADJ
bam-9798	2	28	and	and	CCONJ
bam-9798	2	29	late	late	ADJ
bam-9798	2	30	onset	onset	ADJ
bam-9798	2	31	subtypes	subtype	NOUN
bam-9798	2	32	(	(	PUNCT
bam-9798	2	33	lopd	lopd	NOUN
bam-9798	2	34	)	)	PUNCT
bam-9798	2	35	.	.	PUNCT
bam-9798	3	1	the	the	DET
bam-9798	3	2	myopathy	myopathy	NOUN
bam-9798	3	3	in	in	ADP
bam-9798	3	4	lopd	lopd	NOUN
bam-9798	3	5	can	can	AUX
bam-9798	3	6	be	be	AUX
bam-9798	3	7	reversed	reverse	VERB
bam-9798	3	8	by	by	ADP
bam-9798	3	9	enzyme	enzyme	NOUN
bam-9798	3	10	replacement	replacement	NOUN
bam-9798	3	11	therapy	therapy	NOUN
bam-9798	3	12	(	(	PUNCT
bam-9798	3	13	ert	ert	NOUN
bam-9798	3	14	)	)	PUNCT
bam-9798	3	15	,	,	PUNCT
bam-9798	3	16	but	but	CCONJ
bam-9798	3	17	might	might	AUX
bam-9798	3	18	benefit	benefit	VERB
bam-9798	3	19	from	from	ADP
bam-9798	3	20	a	a	DET
bam-9798	3	21	concomitant	concomitant	ADJ
bam-9798	3	22	low	low	ADJ
bam-9798	3	23	carbohydrate	carbohydrate	NOUN
bam-9798	3	24	high	high	ADJ
bam-9798	3	25	protein	protein	NOUN
bam-9798	3	26	diet	diet	NOUN
bam-9798	3	27	and	and	CCONJ
bam-9798	3	28	aerobic	aerobic	ADJ
bam-9798	3	29	exercise	exercise	NOUN
bam-9798	3	30	treatment	treatment	NOUN
bam-9798	3	31	.	.	PUNCT
bam-9798	4	1	from	from	ADP
bam-9798	4	2	65	65	NUM
bam-9798	4	3	late	late	ADJ
bam-9798	4	4	onset	onset	ADJ
bam-9798	4	5	pompe	pompe	PROPN
bam-9798	4	6	cases	case	NOUN
bam-9798	4	7	,	,	PUNCT
bam-9798	4	8	we	we	PRON
bam-9798	4	9	were	be	AUX
bam-9798	4	10	able	able	ADJ
bam-9798	4	11	to	to	PART
bam-9798	4	12	obtain	obtain	VERB
bam-9798	4	13	in	in	ADP
bam-9798	4	14	58	58	NUM
bam-9798	4	15	a	a	DET
bam-9798	4	16	self	self	NOUN
bam-9798	4	17	-	-	PUNCT
bam-9798	4	18	reported	report	VERB
bam-9798	4	19	evaluation	evaluation	NOUN
bam-9798	4	20	,	,	PUNCT
bam-9798	4	21	most	most	ADJ
bam-9798	4	22	of	of	ADP
bam-9798	4	23	them	they	PRON
bam-9798	4	24	gave	give	VERB
bam-9798	4	25	a	a	DET
bam-9798	4	26	positive	positive	ADJ
bam-9798	4	27	efficacy	efficacy	NOUN
bam-9798	4	28	evaluation	evaluation	NOUN
bam-9798	4	29	of	of	ADP
bam-9798	4	30	enzyme	enzyme	NOUN
bam-9798	4	31	replacement	replacement	NOUN
bam-9798	4	32	therapy	therapy	NOUN
bam-9798	4	33	and	and	CCONJ
bam-9798	4	34	they	they	PRON
bam-9798	4	35	were	be	AUX
bam-9798	4	36	classified	classify	VERB
bam-9798	4	37	by	by	ADP
bam-9798	4	38	a	a	DET
bam-9798	4	39	self	self	NOUN
bam-9798	4	40	-	-	PUNCT
bam-9798	4	41	administered	administer	VERB
bam-9798	4	42	scale	scale	NOUN
bam-9798	4	43	as	as	ADP
bam-9798	4	44	responders	responder	NOUN
bam-9798	4	45	or	or	CCONJ
bam-9798	4	46	non	non	NOUN
bam-9798	4	47	-	-	NOUN
bam-9798	4	48	responders	responder	NOUN
bam-9798	4	49	.	.	PUNCT
bam-9798	5	1	a	a	DET
bam-9798	5	2	cooperative	cooperative	ADJ
bam-9798	5	3	study	study	NOUN
bam-9798	5	4	of	of	ADP
bam-9798	5	5	a	a	DET
bam-9798	5	6	clinical	clinical	ADJ
bam-9798	5	7	group	group	NOUN
bam-9798	5	8	on	on	ADP
bam-9798	5	9	lopd	lopd	NOUN
bam-9798	5	10	monitored	monitor	VERB
bam-9798	5	11	age	age	NOUN
bam-9798	5	12	,	,	PUNCT
bam-9798	5	13	sex	sex	NOUN
bam-9798	5	14	,	,	PUNCT
bam-9798	5	15	bmi	bmi	NOUN
bam-9798	5	16	,	,	PUNCT
bam-9798	5	17	gardner	gardner	NOUN
bam-9798	5	18	-	-	PUNCT
bam-9798	5	19	medwin	medwin	PROPN
bam-9798	5	20	-	-	PUNCT
bam-9798	5	21	walton	walton	PROPN
bam-9798	5	22	scale	scale	NOUN
bam-9798	5	23	and	and	CCONJ
bam-9798	5	24	six	six	NUM
bam-9798	5	25	minute	minute	NOUN
bam-9798	5	26	walking	walking	NOUN
bam-9798	5	27	test	test	NOUN
bam-9798	5	28	(	(	PUNCT
bam-9798	5	29	6mwt	6mwt	NUM
bam-9798	5	30	)	)	PUNCT
bam-9798	5	31	.	.	PUNCT
bam-9798	6	1	the	the	DET
bam-9798	6	2	only	only	ADJ
bam-9798	6	3	clinical	clinical	ADJ
bam-9798	6	4	parameters	parameter	NOUN
bam-9798	6	5	that	that	PRON
bam-9798	6	6	were	be	AUX
bam-9798	6	7	significantly	significantly	ADV
bam-9798	6	8	associated	associate	VERB
bam-9798	6	9	with	with	ADP
bam-9798	6	10	a	a	DET
bam-9798	6	11	responder	responder	NOUN
bam-9798	6	12	category	category	NOUN
bam-9798	6	13	were	be	AUX
bam-9798	6	14	the	the	DET
bam-9798	6	15	pre	pre	ADJ
bam-9798	6	16	-	-	ADJ
bam-9798	6	17	ert	ert	ADJ
bam-9798	6	18	walking	walking	NOUN
bam-9798	6	19	distance	distance	NOUN
bam-9798	6	20	(	(	PUNCT
bam-9798	6	21	p<0.035	p<0.035	NOUN
bam-9798	6	22	)	)	PUNCT
bam-9798	6	23	and	and	CCONJ
bam-9798	6	24	the	the	DET
bam-9798	6	25	use	use	NOUN
bam-9798	6	26	of	of	ADP
bam-9798	6	27	regular	regular	ADJ
bam-9798	6	28	diet	diet	NOUN
bam-9798	6	29	,	,	PUNCT
bam-9798	6	30	exercise	exercise	NOUN
bam-9798	6	31	or	or	CCONJ
bam-9798	6	32	both	both	DET
bam-9798	6	33	(	(	PUNCT
bam-9798	6	34	p<0.029	p<0.029	NUM
bam-9798	6	35	)	)	PUNCT
bam-9798	6	36	.	.	PUNCT
bam-9798	7	1	the	the	DET
bam-9798	7	2	present	present	ADJ
bam-9798	7	3	study	study	NOUN
bam-9798	7	4	shows	show	VERB
bam-9798	7	5	that	that	SCONJ
bam-9798	7	6	in	in	ADP
bam-9798	7	7	lopd	lopd	NOUN
bam-9798	7	8	this	this	DET
bam-9798	7	9	condition	condition	NOUN
bam-9798	7	10	can	can	AUX
bam-9798	7	11	be	be	AUX
bam-9798	7	12	treated	treat	VERB
bam-9798	7	13	by	by	ADP
bam-9798	7	14	ert	ert	NOUN
bam-9798	7	15	,	,	PUNCT
bam-9798	7	16	but	but	CCONJ
bam-9798	7	17	also	also	ADV
bam-9798	7	18	benefits	benefit	VERB
bam-9798	7	19	from	from	ADP
bam-9798	7	20	concomitant	concomitant	ADJ
bam-9798	7	21	diet	diet	NOUN
bam-9798	7	22	and	and	CCONJ
bam-9798	7	23	aerobic	aerobic	ADJ
bam-9798	7	24	exercise	exercise	NOUN
bam-9798	7	25	therapy	therapy	NOUN
bam-9798	7	26	.	.	PUNCT
bam-9798	8	1	key	key	ADJ
bam-9798	8	2	words	word	NOUN
bam-9798	8	3	:	:	PUNCT
bam-9798	8	4	glycogenosis	glycogenosis	NOUN
bam-9798	8	5	type	type	NOUN
bam-9798	8	6	2	2	NUM
bam-9798	8	7	;	;	PUNCT
bam-9798	8	8	enzyme	enzyme	NOUN
bam-9798	8	9	replacement	replacement	NOUN
bam-9798	8	10	therapy	therapy	NOUN
bam-9798	8	11	;	;	PUNCT
bam-9798	8	12	exercise	exercise	NOUN
bam-9798	8	13	;	;	PUNCT
bam-9798	8	14	nutrition	nutrition	NOUN
bam-9798	8	15	.	.	PUNCT
bam-9798	9	1	eur	eur	PROPN
bam-9798	9	2	j	j	PROPN
bam-9798	9	3	transl	transl	PROPN
bam-9798	9	4	myol	myol	ADV
bam-9798	9	5	31	31	NUM
bam-9798	9	6	(	(	PUNCT
bam-9798	9	7	2	2	NUM
bam-9798	9	8	):	):	PUNCT
bam-9798	9	9	9798	9798	NUM
bam-9798	9	10	,	,	PUNCT
bam-9798	9	11	2021	2021	NUM
bam-9798	9	12	doi	doi	NOUN
bam-9798	9	13	:	:	PUNCT
bam-9798	9	14	10.4081	10.4081	NUM
bam-9798	9	15	/	/	SYM
bam-9798	9	16	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	9	17	since	since	SCONJ
bam-9798	9	18	2006	2006	NUM
bam-9798	9	19	,	,	PUNCT
bam-9798	9	20	enzyme	enzyme	NOUN
bam-9798	9	21	replacement	replacement	NOUN
bam-9798	9	22	therapy	therapy	NOUN
bam-9798	9	23	(	(	PUNCT
bam-9798	9	24	ert	ert	PROPN
bam-9798	9	25	)	)	PUNCT
bam-9798	9	26	with	with	ADP
bam-9798	9	27	recombinant	recombinant	ADJ
bam-9798	9	28	human	human	ADJ
bam-9798	9	29	acid	acid	NOUN
bam-9798	9	30	α	α	PROPN
bam-9798	9	31	-	-	NOUN
bam-9798	9	32	glucosidase	glucosidase	PROPN
bam-9798	9	33	has	have	AUX
bam-9798	9	34	been	be	AUX
bam-9798	9	35	approved	approve	VERB
bam-9798	9	36	for	for	ADP
bam-9798	9	37	the	the	DET
bam-9798	9	38	treatment	treatment	NOUN
bam-9798	9	39	of	of	ADP
bam-9798	9	40	pompe	pompe	PROPN
bam-9798	9	41	disease	disease	PROPN
bam-9798	9	42	.	.	PUNCT
bam-9798	10	1	studies	study	NOUN
bam-9798	10	2	in	in	ADP
bam-9798	10	3	neonates	neonate	NOUN
bam-9798	10	4	showing	show	VERB
bam-9798	10	5	improved	improved	ADJ
bam-9798	10	6	survival	survival	NOUN
bam-9798	10	7	were	be	AUX
bam-9798	10	8	the	the	DET
bam-9798	10	9	key	key	ADJ
bam-9798	10	10	fact	fact	NOUN
bam-9798	10	11	for	for	ADP
bam-9798	10	12	market	market	NOUN
bam-9798	10	13	approval.1,2	approval.1,2	PROPN
bam-9798	10	14	since	since	SCONJ
bam-9798	10	15	then	then	ADV
bam-9798	10	16	several	several	ADJ
bam-9798	10	17	studies	study	NOUN
bam-9798	10	18	in	in	ADP
bam-9798	10	19	children	child	NOUN
bam-9798	10	20	and	and	CCONJ
bam-9798	10	21	adults	adult	NOUN
bam-9798	10	22	have	have	AUX
bam-9798	10	23	shown	show	VERB
bam-9798	10	24	effects	effect	NOUN
bam-9798	10	25	of	of	ADP
bam-9798	10	26	ert	ert	NOUN
bam-9798	10	27	on	on	ADP
bam-9798	10	28	walking	walking	NOUN
bam-9798	10	29	distance	distance	NOUN
bam-9798	10	30	,	,	PUNCT
bam-9798	10	31	pulmonary	pulmonary	ADJ
bam-9798	10	32	function	function	NOUN
bam-9798	10	33	,	,	PUNCT
bam-9798	10	34	muscle	muscle	NOUN
bam-9798	10	35	strength	strength	NOUN
bam-9798	10	36	/	/	SYM
bam-9798	10	37	function	function	NOUN
bam-9798	10	38	and	and	CCONJ
bam-9798	10	39	also	also	ADV
bam-9798	10	40	on	on	ADP
bam-9798	10	41	survival.3–5	survival.3–5	NOUN
bam-9798	10	42	however	however	ADV
bam-9798	10	43	,	,	PUNCT
bam-9798	10	44	results	result	NOUN
bam-9798	10	45	also	also	ADV
bam-9798	10	46	suggest	suggest	VERB
bam-9798	10	47	that	that	SCONJ
bam-9798	10	48	there	there	PRON
bam-9798	10	49	is	be	VERB
bam-9798	10	50	a	a	DET
bam-9798	10	51	large	large	ADJ
bam-9798	10	52	variation	variation	NOUN
bam-9798	10	53	in	in	ADP
bam-9798	10	54	the	the	DET
bam-9798	10	55	effects	effect	NOUN
bam-9798	10	56	of	of	ADP
bam-9798	10	57	treatment	treatment	NOUN
bam-9798	10	58	in	in	ADP
bam-9798	10	59	these	these	DET
bam-9798	10	60	patients	patient	NOUN
bam-9798	10	61	.	.	PUNCT
bam-9798	11	1	the	the	DET
bam-9798	11	2	question	question	NOUN
bam-9798	11	3	to	to	PART
bam-9798	11	4	be	be	AUX
bam-9798	11	5	addressed	address	VERB
bam-9798	11	6	is	be	AUX
bam-9798	11	7	the	the	DET
bam-9798	11	8	possible	possible	ADJ
bam-9798	11	9	efficacy	efficacy	NOUN
bam-9798	11	10	of	of	ADP
bam-9798	11	11	concomitant	concomitant	ADJ
bam-9798	11	12	exercise	exercise	NOUN
bam-9798	11	13	and	and	CCONJ
bam-9798	11	14	nutrition	nutrition	NOUN
bam-9798	11	15	in	in	ADP
bam-9798	11	16	late	late	ADJ
bam-9798	11	17	-	-	PUNCT
bam-9798	11	18	onset	onset	NOUN
bam-9798	11	19	pompe	pompe	NOUN
bam-9798	11	20	(	(	PUNCT
bam-9798	11	21	lopd	lopd	NOUN
bam-9798	11	22	)	)	PUNCT
bam-9798	11	23	,	,	PUNCT
bam-9798	11	24	thus	thus	ADV
bam-9798	11	25	the	the	DET
bam-9798	11	26	present	present	ADJ
bam-9798	11	27	study	study	NOUN
bam-9798	11	28	documents	document	NOUN
bam-9798	11	29	a	a	DET
bam-9798	11	30	responder	responder	NOUN
bam-9798	11	31	(	(	PUNCT
bam-9798	11	32	r	r	NOUN
bam-9798	11	33	)	)	PUNCT
bam-9798	11	34	and	and	CCONJ
bam-9798	11	35	nonresponder	nonresponder	NOUN
bam-9798	11	36	(	(	PUNCT
bam-9798	11	37	n	n	CCONJ
bam-9798	11	38	)	)	PUNCT
bam-9798	11	39	status	status	NOUN
bam-9798	11	40	based	base	VERB
bam-9798	11	41	on	on	ADP
bam-9798	11	42	patient	patient	ADJ
bam-9798	11	43	derived	derive	VERB
bam-9798	11	44	outcomes	outcome	NOUN
bam-9798	11	45	.	.	PUNCT
bam-9798	12	1	with	with	ADP
bam-9798	12	2	an	an	DET
bam-9798	12	3	incidence	incidence	NOUN
bam-9798	12	4	of	of	ADP
bam-9798	12	5	approximately	approximately	ADV
bam-9798	12	6	1:40.000	1:40.000	NUM
bam-9798	12	7	to	to	PART
bam-9798	12	8	1:200.000	1:200.000	NUM
bam-9798	12	9	births	birth	NOUN
bam-9798	12	10	,	,	PUNCT
bam-9798	12	11	research	research	NOUN
bam-9798	12	12	progress	progress	NOUN
bam-9798	12	13	on	on	ADP
bam-9798	12	14	this	this	DET
bam-9798	12	15	rare	rare	ADJ
bam-9798	12	16	disease	disease	NOUN
bam-9798	12	17	is	be	AUX
bam-9798	12	18	slow	slow	ADJ
bam-9798	12	19	,	,	PUNCT
bam-9798	12	20	hampered	hamper	VERB
bam-9798	12	21	by	by	ADP
bam-9798	12	22	the	the	DET
bam-9798	12	23	difficulty	difficulty	NOUN
bam-9798	12	24	to	to	PART
bam-9798	12	25	obtain	obtain	VERB
bam-9798	12	26	sufficient	sufficient	ADJ
bam-9798	12	27	patient	patient	ADJ
bam-9798	12	28	numbers	number	NOUN
bam-9798	12	29	.	.	PUNCT
bam-9798	13	1	for	for	ADP
bam-9798	13	2	example	example	NOUN
bam-9798	13	3	,	,	PUNCT
bam-9798	13	4	very	very	ADV
bam-9798	13	5	little	little	ADJ
bam-9798	13	6	is	be	AUX
bam-9798	13	7	known	know	VERB
bam-9798	13	8	about	about	ADP
bam-9798	13	9	which	which	DET
bam-9798	13	10	factors	factor	NOUN
bam-9798	13	11	explain	explain	VERB
bam-9798	13	12	the	the	DET
bam-9798	13	13	variability	variability	NOUN
bam-9798	13	14	in	in	ADP
bam-9798	13	15	the	the	DET
bam-9798	13	16	response	response	NOUN
bam-9798	13	17	to	to	PART
bam-9798	13	18	ert	ert	VERB
bam-9798	13	19	treatment	treatment	NOUN
bam-9798	13	20	that	that	PRON
bam-9798	13	21	is	be	AUX
bam-9798	13	22	observed	observe	VERB
bam-9798	13	23	both	both	CCONJ
bam-9798	13	24	in	in	ADP
bam-9798	13	25	children	child	NOUN
bam-9798	13	26	and	and	CCONJ
bam-9798	13	27	adults	adult	NOUN
bam-9798	13	28	.	.	PUNCT
bam-9798	14	1	also	also	ADV
bam-9798	14	2	,	,	PUNCT
bam-9798	14	3	guidance	guidance	NOUN
bam-9798	14	4	on	on	ADP
bam-9798	14	5	monitoring	monitoring	NOUN
bam-9798	14	6	and	and	CCONJ
bam-9798	14	7	treating	treat	VERB
bam-9798	14	8	these	these	DET
bam-9798	14	9	patients	patient	NOUN
bam-9798	14	10	is	be	AUX
bam-9798	14	11	relatively	relatively	ADV
bam-9798	14	12	scarce	scarce	ADJ
bam-9798	14	13	.	.	PUNCT
bam-9798	15	1	there	there	PRON
bam-9798	15	2	are	be	VERB
bam-9798	15	3	currently	currently	ADV
bam-9798	15	4	no	no	DET
bam-9798	15	5	internationally	internationally	ADV
bam-9798	15	6	accepted	accept	VERB
bam-9798	15	7	guidelines	guideline	NOUN
bam-9798	15	8	for	for	ADP
bam-9798	15	9	the	the	DET
bam-9798	15	10	ert	ert	NOUN
bam-9798	15	11	treatment	treatment	NOUN
bam-9798	15	12	of	of	ADP
bam-9798	15	13	older	old	ADJ
bam-9798	15	14	children	child	NOUN
bam-9798	15	15	and	and	CCONJ
bam-9798	15	16	adults	adult	NOUN
bam-9798	15	17	with	with	ADP
bam-9798	15	18	pompe	pompe	PROPN
bam-9798	15	19	disease	disease	PROPN
bam-9798	15	20	,	,	PUNCT
bam-9798	15	21	although	although	SCONJ
bam-9798	15	22	national	national	ADJ
bam-9798	15	23	guidelines	guideline	NOUN
bam-9798	15	24	have	have	AUX
bam-9798	15	25	been	be	AUX
bam-9798	15	26	published	publish	VERB
bam-9798	15	27	for	for	ADP
bam-9798	15	28	several	several	ADJ
bam-9798	15	29	european	european	ADJ
bam-9798	15	30	and	and	CCONJ
bam-9798	15	31	non	non	ADJ
bam-9798	15	32	-	-	ADJ
bam-9798	15	33	european	european	ADJ
bam-9798	15	34	countries.6–10	countries.6–10	NOUN
bam-9798	15	35	finally	finally	ADV
bam-9798	15	36	,	,	PUNCT
bam-9798	15	37	development	development	NOUN
bam-9798	15	38	of	of	ADP
bam-9798	15	39	expert	expert	NOUN
bam-9798	15	40	consortia	consortium	NOUN
bam-9798	15	41	to	to	PART
bam-9798	15	42	provide	provide	VERB
bam-9798	15	43	advice	advice	NOUN
bam-9798	15	44	and	and	CCONJ
bam-9798	15	45	leadership	leadership	NOUN
bam-9798	15	46	is	be	AUX
bam-9798	15	47	described	describe	VERB
bam-9798	15	48	.	.	PUNCT
bam-9798	16	1	formation	formation	NOUN
bam-9798	16	2	of	of	ADP
bam-9798	16	3	the	the	DET
bam-9798	16	4	european	european	PROPN
bam-9798	16	5	pompe	pompe	PROPN
bam-9798	16	6	consortium	consortium	PROPN
bam-9798	16	7	(	(	PUNCT
bam-9798	16	8	epoc	epoc	NOUN
bam-9798	16	9	)	)	PUNCT
bam-9798	16	10	and	and	CCONJ
bam-9798	16	11	report	report	NOUN
bam-9798	16	12	of	of	ADP
bam-9798	16	13	the	the	DET
bam-9798	16	14	5th	5th	ADJ
bam-9798	16	15	epoc	epoc	NOUN
bam-9798	16	16	meeting	meet	VERB
bam-9798	16	17	the	the	DET
bam-9798	16	18	organization	organization	NOUN
bam-9798	16	19	of	of	ADP
bam-9798	16	20	the	the	DET
bam-9798	16	21	network	network	NOUN
bam-9798	16	22	with	with	ADP
bam-9798	16	23	a	a	DET
bam-9798	16	24	steering	steering	NOUN
bam-9798	16	25	board	board	NOUN
bam-9798	16	26	group	group	NOUN
bam-9798	16	27	,	,	PUNCT
bam-9798	16	28	one	one	NUM
bam-9798	16	29	representative	representative	NOUN
bam-9798	16	30	for	for	ADP
bam-9798	16	31	each	each	DET
bam-9798	16	32	country	country	NOUN
bam-9798	16	33	,	,	PUNCT
bam-9798	16	34	and	and	CCONJ
bam-9798	16	35	other	other	ADJ
bam-9798	16	36	members	member	NOUN
bam-9798	16	37	,	,	PUNCT
bam-9798	16	38	was	be	AUX
bam-9798	16	39	discussed	discuss	VERB
bam-9798	16	40	at	at	ADP
bam-9798	16	41	the	the	DET
bam-9798	16	42	european	european	ADJ
bam-9798	16	43	neuromuscular	neuromuscular	ADJ
bam-9798	16	44	center	center	NOUN
bam-9798	16	45	(	(	PUNCT
bam-9798	16	46	enmc	enmc	PROPN
bam-9798	16	47	)	)	PUNCT
bam-9798	16	48	meeting	meeting	NOUN
bam-9798	16	49	in	in	ADP
bam-9798	16	50	2014	2014	NUM
bam-9798	16	51	.	.	PUNCT
bam-9798	17	1	it	it	PRON
bam-9798	17	2	was	be	AUX
bam-9798	17	3	agreed	agree	VERB
bam-9798	17	4	by	by	ADP
bam-9798	17	5	the	the	DET
bam-9798	17	6	organizers	organizer	NOUN
bam-9798	17	7	to	to	PART
bam-9798	17	8	propose	propose	VERB
bam-9798	17	9	a	a	DET
bam-9798	17	10	formal	formal	ADJ
bam-9798	17	11	governance	governance	NOUN
bam-9798	17	12	structure	structure	NOUN
bam-9798	17	13	for	for	ADP
bam-9798	17	14	the	the	DET
bam-9798	17	15	network	network	NOUN
bam-9798	17	16	.	.	PUNCT
bam-9798	18	1	this	this	PRON
bam-9798	18	2	was	be	AUX
bam-9798	18	3	incorporated	incorporate	VERB
bam-9798	18	4	in	in	ADP
bam-9798	18	5	a	a	DET
bam-9798	18	6	final	final	ADJ
bam-9798	18	7	consortium	consortium	NOUN
bam-9798	18	8	agreement	agreement	NOUN
bam-9798	18	9	,	,	PUNCT
bam-9798	18	10	outlining	outline	VERB
bam-9798	18	11	the	the	DET
bam-9798	18	12	structure	structure	NOUN
bam-9798	18	13	and	and	CCONJ
bam-9798	18	14	rules	rule	NOUN
bam-9798	18	15	of	of	ADP
bam-9798	18	16	the	the	DET
bam-9798	18	17	network	network	NOUN
bam-9798	18	18	.	.	PUNCT
bam-9798	19	1	combining	combine	VERB
bam-9798	19	2	clinical	clinical	ADJ
bam-9798	19	3	,	,	PUNCT
bam-9798	19	4	biological	biological	ADJ
bam-9798	19	5	and	and	CCONJ
bam-9798	19	6	genetic	genetic	ADJ
bam-9798	19	7	data	datum	NOUN
bam-9798	19	8	from	from	ADP
bam-9798	19	9	different	different	ADJ
bam-9798	19	10	european	european	ADJ
bam-9798	19	11	countries	country	NOUN
bam-9798	19	12	might	might	AUX
bam-9798	19	13	generate	generate	VERB
bam-9798	19	14	a	a	DET
bam-9798	19	15	sufficiently	sufficiently	ADV
bam-9798	19	16	large	large	ADJ
bam-9798	19	17	dataset	dataset	NOUN
bam-9798	19	18	to	to	PART
bam-9798	19	19	allow	allow	VERB
bam-9798	19	20	research	research	NOUN
bam-9798	19	21	into	into	ADP
bam-9798	19	22	prognostic	prognostic	ADJ
bam-9798	19	23	factors	factor	NOUN
bam-9798	19	24	to	to	PART
bam-9798	19	25	progress	progress	VERB
bam-9798	19	26	.	.	PUNCT
bam-9798	20	1	furthermore	furthermore	ADV
bam-9798	20	2	,	,	PUNCT
bam-9798	20	3	the	the	DET
bam-9798	20	4	joint	joint	ADJ
bam-9798	20	5	experience	experience	NOUN
bam-9798	20	6	of	of	ADP
bam-9798	20	7	experts	expert	NOUN
bam-9798	20	8	who	who	PRON
bam-9798	20	9	monitor	monitor	VERB
bam-9798	20	10	and	and	CCONJ
bam-9798	20	11	treat	treat	VERB
bam-9798	20	12	relatively	relatively	ADV
bam-9798	20	13	large	large	ADJ
bam-9798	20	14	numbers	number	NOUN
bam-9798	20	15	of	of	ADP
bam-9798	20	16	patients	patient	NOUN
bam-9798	20	17	with	with	ADP
bam-9798	20	18	pompe	pompe	PROPN
bam-9798	20	19	disease	disease	NOUN
bam-9798	20	20	would	would	AUX
bam-9798	20	21	create	create	VERB
bam-9798	20	22	a	a	DET
bam-9798	20	23	platform	platform	NOUN
bam-9798	20	24	to	to	PART
bam-9798	20	25	develop	develop	VERB
bam-9798	20	26	recommendations	recommendation	NOUN
bam-9798	20	27	on	on	ADP
bam-9798	20	28	monitoring	monitor	VERB
bam-9798	20	29	and	and	CCONJ
bam-9798	20	30	treating	treat	VERB
bam-9798	20	31	patients	patient	NOUN
bam-9798	20	32	.	.	PUNCT
bam-9798	21	1	finally	finally	ADV
bam-9798	21	2	,	,	PUNCT
bam-9798	21	3	the	the	DET
bam-9798	21	4	shared	share	VERB
bam-9798	21	5	knowledge	knowledge	NOUN
bam-9798	21	6	and	and	CCONJ
bam-9798	21	7	experience	experience	NOUN
bam-9798	21	8	makes	make	VERB
bam-9798	21	9	it	it	PRON
bam-9798	21	10	an	an	DET
bam-9798	21	11	ideal	ideal	ADJ
bam-9798	21	12	organization	organization	NOUN
bam-9798	21	13	to	to	PART
bam-9798	21	14	provide	provide	VERB
bam-9798	21	15	advice	advice	NOUN
bam-9798	21	16	and	and	CCONJ
bam-9798	21	17	knowledge	knowledge	NOUN
bam-9798	21	18	to	to	ADP
bam-9798	21	19	health	health	NOUN
bam-9798	21	20	authorities	authority	NOUN
bam-9798	21	21	and	and	CCONJ
bam-9798	21	22	policy	policy	NOUN
bam-9798	21	23	makers	maker	NOUN
bam-9798	21	24	.	.	PUNCT
bam-9798	22	1	a	a	DET
bam-9798	22	2	consensus	consensus	NOUN
bam-9798	22	3	about	about	ADP
bam-9798	22	4	start	start	NOUN
bam-9798	22	5	/stop	/stop	VERB
bam-9798	22	6	criteria	criterion	NOUN
bam-9798	22	7	that	that	PRON
bam-9798	22	8	were	be	AUX
bam-9798	22	9	developed	develop	VERB
bam-9798	22	10	by	by	ADP
bam-9798	22	11	different	different	ADJ
bam-9798	22	12	centers	center	NOUN
bam-9798	22	13	and	and	CCONJ
bam-9798	22	14	initiated	initiate	VERB
bam-9798	22	15	the	the	DET
bam-9798	22	16	epoc	epoc	NOUN
bam-9798	22	17	work.11	work.11	ADP
bam-9798	22	18	the	the	DET
bam-9798	22	19	epoc	epoc	NOUN
bam-9798	22	20	group	group	NOUN
bam-9798	22	21	has	have	AUX
bam-9798	22	22	met	meet	VERB
bam-9798	22	23	regularly	regularly	ADV
bam-9798	22	24	and	and	CCONJ
bam-9798	22	25	here	here	ADV
bam-9798	22	26	are	be	AUX
bam-9798	22	27	reported	report	VERB
bam-9798	22	28	data	datum	NOUN
bam-9798	22	29	presented	present	VERB
bam-9798	22	30	and	and	CCONJ
bam-9798	22	31	discussed	discuss	VERB
bam-9798	22	32	on	on	ADP
bam-9798	22	33	ert	ert	ADJ
bam-9798	22	34	treatment	treatment	NOUN
bam-9798	22	35	at	at	ADP
bam-9798	22	36	the	the	DET
bam-9798	22	37	5th	5th	ADJ
bam-9798	22	38	epoc	epoc	NOUN
bam-9798	22	39	meeting	meeting	NOUN
bam-9798	22	40	in	in	ADP
bam-9798	22	41	hamburg	hamburg	PROPN
bam-9798	22	42	in	in	ADP
bam-9798	22	43	february	february	PROPN
bam-9798	22	44	2020	2020	NUM
bam-9798	22	45	,	,	PUNCT
bam-9798	22	46	organized	organize	VERB
bam-9798	22	47	by	by	ADP
bam-9798	22	48	zoltan	zoltan	PROPN
bam-9798	22	49	lukacs	lukacs	PROPN
bam-9798	22	50	and	and	CCONJ
bam-9798	22	51	benedikt	benedikt	NOUN
bam-9798	22	52	scoser	scoser	NOUN
bam-9798	22	53	,	,	PUNCT
bam-9798	22	54	at	at	ADP
bam-9798	22	55	this	this	DET
bam-9798	22	56	meeting	meeting	NOUN
bam-9798	22	57	the	the	DET
bam-9798	22	58	participation	participation	NOUN
bam-9798	22	59	was	be	AUX
bam-9798	22	60	limited	limit	VERB
bam-9798	22	61	by	by	ADP
bam-9798	22	62	the	the	DET
bam-9798	22	63	covid-19	covid-19	PROPN
bam-9798	22	64	pandemic	pandemic	ADJ
bam-9798	22	65	restrictions	restriction	NOUN
bam-9798	22	66	.	.	PUNCT
bam-9798	23	1	exercise	exercise	NOUN
bam-9798	23	2	and	and	CCONJ
bam-9798	23	3	nutrition	nutrition	NOUN
bam-9798	23	4	in	in	ADP
bam-9798	23	5	late	late	ADJ
bam-9798	23	6	onset	onset	ADJ
bam-9798	23	7	pompe	pompe	PROPN
bam-9798	23	8	disease	disease	PROPN
bam-9798	23	9	eur	eur	PROPN
bam-9798	23	10	j	j	PROPN
bam-9798	23	11	transl	transl	PROPN
bam-9798	23	12	myol	myol	ADV
bam-9798	23	13	31	31	NUM
bam-9798	23	14	(	(	PUNCT
bam-9798	23	15	2	2	NUM
bam-9798	23	16	):	):	PUNCT
bam-9798	23	17	9798	9798	NUM
bam-9798	23	18	,	,	PUNCT
bam-9798	23	19	2021	2021	NUM
bam-9798	23	20	doi	doi	NOUN
bam-9798	23	21	:	:	PUNCT
bam-9798	23	22	10.4081	10.4081	NUM
bam-9798	23	23	/	/	SYM
bam-9798	23	24	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	23	25	2	2	NUM
bam-9798	23	26	the	the	DET
bam-9798	23	27	fifth	fifth	PROPN
bam-9798	23	28	epoc	epoc	NOUN
bam-9798	23	29	consortium	consortium	PROPN
bam-9798	23	30	started	start	VERB
bam-9798	23	31	on	on	ADP
bam-9798	23	32	february	february	PROPN
bam-9798	23	33	,	,	PUNCT
bam-9798	23	34	28	28	NUM
bam-9798	23	35	,	,	PUNCT
bam-9798	23	36	2020	2020	NUM
bam-9798	23	37	and	and	CCONJ
bam-9798	23	38	ended	end	VERB
bam-9798	23	39	on	on	ADP
bam-9798	23	40	february	february	PROPN
bam-9798	23	41	29	29	NUM
bam-9798	23	42	at	at	ADP
bam-9798	23	43	the	the	DET
bam-9798	23	44	erika	erika	PROPN
bam-9798	23	45	house	house	PROPN
bam-9798	23	46	,	,	PUNCT
bam-9798	23	47	an	an	DET
bam-9798	23	48	historical	historical	ADJ
bam-9798	23	49	nurse	nurse	NOUN
bam-9798	23	50	house	house	PROPN
bam-9798	23	51	of	of	ADP
bam-9798	23	52	hamburg	hamburg	PROPN
bam-9798	23	53	-	-	PUNCT
bam-9798	23	54	eppendorf	eppendorf	PROPN
bam-9798	23	55	hospital	hospital	NOUN
bam-9798	23	56	(	(	PUNCT
bam-9798	23	57	figure	figure	NOUN
bam-9798	23	58	1	1	NUM
bam-9798	23	59	)	)	PUNCT
bam-9798	23	60	.	.	PUNCT
bam-9798	24	1	there	there	PRON
bam-9798	24	2	was	be	VERB
bam-9798	24	3	a	a	DET
bam-9798	24	4	welcome	welcome	NOUN
bam-9798	24	5	-	-	PUNCT
bam-9798	24	6	introduction	introduction	NOUN
bam-9798	24	7	from	from	ADP
bam-9798	24	8	zoltan	zoltan	PROPN
bam-9798	24	9	lukas	lukas	PROPN
bam-9798	24	10	,	,	PUNCT
bam-9798	24	11	which	which	PRON
bam-9798	24	12	gave	give	VERB
bam-9798	24	13	an	an	DET
bam-9798	24	14	overview	overview	NOUN
bam-9798	24	15	of	of	ADP
bam-9798	24	16	pompe	pompe	PROPN
bam-9798	24	17	screening	screen	VERB
bam-9798	24	18	status	status	NOUN
bam-9798	24	19	,	,	PUNCT
bam-9798	24	20	its	its	PRON
bam-9798	24	21	world	world	NOUN
bam-9798	24	22	-	-	PUNCT
bam-9798	24	23	wide	wide	ADJ
bam-9798	24	24	use	use	NOUN
bam-9798	24	25	,	,	PUNCT
bam-9798	24	26	its	its	PRON
bam-9798	24	27	problems	problem	NOUN
bam-9798	24	28	,	,	PUNCT
bam-9798	24	29	the	the	DET
bam-9798	24	30	outlooks	outlook	NOUN
bam-9798	24	31	and	and	CCONJ
bam-9798	24	32	new	new	ADJ
bam-9798	24	33	developments	development	NOUN
bam-9798	24	34	.	.	PUNCT
bam-9798	25	1	this	this	PRON
bam-9798	25	2	was	be	AUX
bam-9798	25	3	followed	follow	VERB
bam-9798	25	4	by	by	ADP
bam-9798	25	5	discussion	discussion	NOUN
bam-9798	25	6	on	on	ADP
bam-9798	25	7	different	different	ADJ
bam-9798	25	8	methodologies	methodology	NOUN
bam-9798	25	9	and	and	CCONJ
bam-9798	25	10	recommendation	recommendation	NOUN
bam-9798	25	11	for	for	ADP
bam-9798	25	12	a	a	DET
bam-9798	25	13	more	more	ADV
bam-9798	25	14	widespread	widespread	ADJ
bam-9798	25	15	use	use	NOUN
bam-9798	25	16	.	.	PUNCT
bam-9798	26	1	simon	simon	PROPN
bam-9798	26	2	heales	heales	PROPN
bam-9798	26	3	reviewed	review	VERB
bam-9798	26	4	the	the	DET
bam-9798	26	5	use	use	NOUN
bam-9798	26	6	of	of	ADP
bam-9798	26	7	urinary	urinary	ADJ
bam-9798	26	8	tetrasaccaride	tetrasaccaride	ADV
bam-9798	26	9	(	(	PUNCT
bam-9798	26	10	hex4	hex4	PROPN
bam-9798	26	11	/	/	SYM
bam-9798	26	12	glc	glc	PROPN
bam-9798	26	13	4	4	NUM
bam-9798	26	14	)	)	PUNCT
bam-9798	26	15	in	in	ADP
bam-9798	26	16	his	his	PRON
bam-9798	26	17	experience	experience	NOUN
bam-9798	26	18	in	in	ADP
bam-9798	26	19	diagnosis	diagnosis	NOUN
bam-9798	26	20	and	and	CCONJ
bam-9798	26	21	followup	followup	NOUN
bam-9798	26	22	of	of	ADP
bam-9798	26	23	pompe	pompe	PROPN
bam-9798	26	24	children	child	NOUN
bam-9798	26	25	used	use	VERB
bam-9798	26	26	at	at	ADP
bam-9798	26	27	great	great	ADJ
bam-9798	26	28	ormon	ormon	ADJ
bam-9798	26	29	street	street	PROPN
bam-9798	26	30	hospital	hospital	NOUN
bam-9798	26	31	(	(	PUNCT
bam-9798	26	32	gosh	gosh	INTJ
bam-9798	26	33	)	)	PUNCT
bam-9798	26	34	,	,	PUNCT
bam-9798	26	35	as	as	ADP
bam-9798	26	36	an	an	DET
bam-9798	26	37	efficient	efficient	ADJ
bam-9798	26	38	support	support	NOUN
bam-9798	26	39	to	to	PART
bam-9798	26	40	enzyme	enzyme	VERB
bam-9798	26	41	analysis	analysis	NOUN
bam-9798	26	42	that	that	PRON
bam-9798	26	43	usually	usually	ADV
bam-9798	26	44	is	be	AUX
bam-9798	26	45	done	do	VERB
bam-9798	26	46	with	with	ADP
bam-9798	26	47	acarbose	acarbose	NOUN
bam-9798	26	48	inhibition	inhibition	NOUN
bam-9798	26	49	.	.	PUNCT
bam-9798	27	1	vacuolated	vacuolate	VERB
bam-9798	27	2	lymphocytes	lymphocyte	NOUN
bam-9798	27	3	represent	represent	VERB
bam-9798	27	4	a	a	DET
bam-9798	27	5	good	good	ADJ
bam-9798	27	6	disease	disease	NOUN
bam-9798	27	7	hallmark	hallmark	NOUN
bam-9798	27	8	,	,	PUNCT
bam-9798	27	9	as	as	ADV
bam-9798	27	10	well	well	ADV
bam-9798	27	11	as	as	ADP
bam-9798	27	12	hex4	hex4	PROPN
bam-9798	27	13	/	/	SYM
bam-9798	27	14	glc4	glc4	PROPN
bam-9798	27	15	are	be	AUX
bam-9798	27	16	useful	useful	ADJ
bam-9798	27	17	diagnostic	diagnostic	ADJ
bam-9798	27	18	prognostic	prognostic	ADJ
bam-9798	27	19	biomarkers	biomarker	NOUN
bam-9798	27	20	of	of	ADP
bam-9798	27	21	pompe	pompe	PROPN
bam-9798	27	22	disease	disease	PROPN
bam-9798	27	23	.	.	PUNCT
bam-9798	28	1	dr	dr	PROPN
bam-9798	28	2	mark	mark	PROPN
bam-9798	28	3	roberts	roberts	PROPN
bam-9798	28	4	discussed	discuss	VERB
bam-9798	28	5	advances	advance	NOUN
bam-9798	28	6	in	in	ADP
bam-9798	28	7	treatment	treatment	NOUN
bam-9798	28	8	and	and	CCONJ
bam-9798	28	9	possible	possible	ADJ
bam-9798	28	10	gene	gene	NOUN
bam-9798	28	11	therapy	therapy	NOUN
bam-9798	28	12	application	application	NOUN
bam-9798	28	13	in	in	ADP
bam-9798	28	14	these	these	DET
bam-9798	28	15	patients	patient	NOUN
bam-9798	28	16	.	.	PUNCT
bam-9798	29	1	james	james	PROPN
bam-9798	29	2	davison	davison	PROPN
bam-9798	29	3	presented	present	VERB
bam-9798	29	4	his	his	PRON
bam-9798	29	5	experience	experience	NOUN
bam-9798	29	6	with	with	ADP
bam-9798	29	7	low	low	ADJ
bam-9798	29	8	dose	dose	NOUN
bam-9798	29	9	ert	ert	NOUN
bam-9798	29	10	(	(	PUNCT
bam-9798	29	11	20	20	NUM
bam-9798	29	12	mg	mg	NUM
bam-9798	29	13	/	/	SYM
bam-9798	29	14	every	every	DET
bam-9798	29	15	week	week	NOUN
bam-9798	29	16	)	)	PUNCT
bam-9798	29	17	in	in	ADP
bam-9798	29	18	children	child	NOUN
bam-9798	29	19	,	,	PUNCT
bam-9798	29	20	promising	promise	VERB
bam-9798	29	21	for	for	ADP
bam-9798	29	22	heart	heart	NOUN
bam-9798	29	23	treatment	treatment	NOUN
bam-9798	29	24	.	.	PUNCT
bam-9798	30	1	in	in	ADP
bam-9798	30	2	his	his	PRON
bam-9798	30	3	series	series	NOUN
bam-9798	30	4	of	of	ADP
bam-9798	30	5	33	33	NUM
bam-9798	30	6	infants	infant	NOUN
bam-9798	30	7	treated	treat	VERB
bam-9798	30	8	at	at	ADP
bam-9798	30	9	gosh	gosh	PROPN
bam-9798	30	10	:	:	PUNCT
bam-9798	30	11	14	14	NUM
bam-9798	30	12	were	be	AUX
bam-9798	30	13	alive	alive	ADJ
bam-9798	30	14	,	,	PUNCT
bam-9798	30	15	12	12	NUM
bam-9798	30	16	deceased	deceased	ADJ
bam-9798	30	17	,	,	PUNCT
bam-9798	30	18	5	5	NUM
bam-9798	30	19	children	child	NOUN
bam-9798	30	20	none	none	NOUN
bam-9798	30	21	treated	treat	VERB
bam-9798	30	22	.	.	PUNCT
bam-9798	31	1	discussion	discussion	NOUN
bam-9798	31	2	of	of	ADP
bam-9798	31	3	data	datum	NOUN
bam-9798	31	4	presented	present	VERB
bam-9798	31	5	followed	follow	VERB
bam-9798	31	6	and	and	CCONJ
bam-9798	31	7	continued	continue	VERB
bam-9798	31	8	at	at	ADP
bam-9798	31	9	a	a	DET
bam-9798	31	10	dinner	dinner	NOUN
bam-9798	31	11	at	at	ADP
bam-9798	31	12	dorint	dorint	NOUN
bam-9798	31	13	hotel	hotel	NOUN
bam-9798	31	14	.	.	PUNCT
bam-9798	32	1	on	on	ADP
bam-9798	32	2	february	february	PROPN
bam-9798	32	3	29	29	NUM
bam-9798	32	4	,	,	PUNCT
bam-9798	32	5	2020	2020	NUM
bam-9798	32	6	benedikt	benedikt	NOUN
bam-9798	32	7	schoser	schoser	NOUN
bam-9798	32	8	introduced	introduce	VERB
bam-9798	32	9	the	the	DET
bam-9798	32	10	second	second	ADJ
bam-9798	32	11	session	session	NOUN
bam-9798	32	12	,	,	PUNCT
bam-9798	32	13	while	while	SCONJ
bam-9798	32	14	zoltan	zoltan	PROPN
bam-9798	32	15	lukacs	lukacs	PROPN
bam-9798	32	16	was	be	AUX
bam-9798	32	17	hospitalized	hospitalize	VERB
bam-9798	32	18	for	for	ADP
bam-9798	32	19	a	a	DET
bam-9798	32	20	covid-19	covid-19	PROPN
bam-9798	32	21	infection	infection	NOUN
bam-9798	32	22	.	.	PUNCT
bam-9798	33	1	dr	dr	PROPN
bam-9798	33	2	jordi	jordi	PROPN
bam-9798	33	3	manera	manera	PROPN
bam-9798	33	4	diaz	diaz	PROPN
bam-9798	33	5	discussed	discuss	VERB
bam-9798	33	6	the	the	DET
bam-9798	33	7	role	role	NOUN
bam-9798	33	8	of	of	ADP
bam-9798	33	9	muscle	muscle	NOUN
bam-9798	33	10	imaging	imaging	NOUN
bam-9798	33	11	detecting	detect	VERB
bam-9798	33	12	fat	fat	ADJ
bam-9798	33	13	and	and	CCONJ
bam-9798	33	14	connective	connective	ADJ
bam-9798	33	15	tissue	tissue	NOUN
bam-9798	33	16	infiltration	infiltration	NOUN
bam-9798	33	17	during	during	ADP
bam-9798	33	18	ert	ert	NOUN
bam-9798	33	19	,	,	PUNCT
bam-9798	33	20	while	while	SCONJ
bam-9798	33	21	stefan	stefan	PROPN
bam-9798	33	22	hinze	hinze	PROPN
bam-9798	33	23	presented	present	VERB
bam-9798	33	24	experimental	experimental	ADJ
bam-9798	33	25	data	datum	NOUN
bam-9798	33	26	on	on	ADP
bam-9798	33	27	pompe	pompe	PROPN
bam-9798	33	28	myoblasts	myoblast	NOUN
bam-9798	33	29	.	.	PUNCT
bam-9798	34	1	this	this	PRON
bam-9798	34	2	was	be	AUX
bam-9798	34	3	followed	follow	VERB
bam-9798	34	4	by	by	ADP
bam-9798	34	5	a	a	DET
bam-9798	34	6	presentation	presentation	NOUN
bam-9798	34	7	by	by	ADP
bam-9798	34	8	corrado	corrado	PROPN
bam-9798	34	9	angelini	angelini	PROPN
bam-9798	34	10	on	on	ADP
bam-9798	34	11	ert	ert	NOUN
bam-9798	34	12	treatment	treatment	NOUN
bam-9798	34	13	results	result	NOUN
bam-9798	34	14	and	and	CCONJ
bam-9798	34	15	effect	effect	NOUN
bam-9798	34	16	of	of	ADP
bam-9798	34	17	exercise	exercise	NOUN
bam-9798	34	18	and	and	CCONJ
bam-9798	34	19	nutrition	nutrition	NOUN
bam-9798	34	20	as	as	SCONJ
bam-9798	34	21	concomitant	concomitant	ADJ
bam-9798	34	22	supportive	supportive	ADJ
bam-9798	34	23	therapy	therapy	NOUN
bam-9798	34	24	to	to	PART
bam-9798	34	25	ert	ert	PROPN
bam-9798	34	26	.	.	PROPN
bam-9798	35	1	jon	jon	PROPN
bam-9798	35	2	muir	muir	PROPN
bam-9798	35	3	of	of	ADP
bam-9798	35	4	international	international	PROPN
bam-9798	35	5	pompe	pompe	PROPN
bam-9798	35	6	association	association	PROPN
bam-9798	35	7	presented	present	VERB
bam-9798	35	8	the	the	DET
bam-9798	35	9	patient	patient	NOUN
bam-9798	35	10	prospective	prospective	ADJ
bam-9798	35	11	after	after	ADP
bam-9798	35	12	several	several	ADJ
bam-9798	35	13	years	year	NOUN
bam-9798	35	14	of	of	ADP
bam-9798	35	15	various	various	ADJ
bam-9798	35	16	ert	ert	NOUN
bam-9798	35	17	regimens	regimen	NOUN
bam-9798	35	18	and	and	CCONJ
bam-9798	35	19	opinions	opinion	NOUN
bam-9798	35	20	about	about	ADP
bam-9798	35	21	screening	screening	NOUN
bam-9798	35	22	and	and	CCONJ
bam-9798	35	23	diagnosis	diagnosis	NOUN
bam-9798	35	24	options	option	NOUN
bam-9798	35	25	.	.	PUNCT
bam-9798	36	1	he	he	PRON
bam-9798	36	2	underlined	underline	VERB
bam-9798	36	3	future	future	ADJ
bam-9798	36	4	public	public	ADJ
bam-9798	36	5	initiative	initiative	NOUN
bam-9798	36	6	such	such	ADJ
bam-9798	36	7	as	as	ADP
bam-9798	36	8	an	an	DET
bam-9798	36	9	international	international	ADJ
bam-9798	36	10	pompe	pompe	PROPN
bam-9798	36	11	day	day	NOUN
bam-9798	36	12	and	and	CCONJ
bam-9798	36	13	status	status	NOUN
bam-9798	36	14	of	of	ADP
bam-9798	36	15	the	the	DET
bam-9798	36	16	art	art	NOUN
bam-9798	36	17	in	in	ADP
bam-9798	36	18	collaboration	collaboration	NOUN
bam-9798	36	19	,	,	PUNCT
bam-9798	36	20	since	since	SCONJ
bam-9798	36	21	participants	participant	NOUN
bam-9798	36	22	collaborated	collaborate	VERB
bam-9798	36	23	describing	describe	VERB
bam-9798	36	24	which	which	DET
bam-9798	36	25	assessments	assessment	NOUN
bam-9798	36	26	and	and	CCONJ
bam-9798	36	27	progresses	progress	NOUN
bam-9798	36	28	obtained	obtain	VERB
bam-9798	36	29	for	for	ADP
bam-9798	36	30	pompe	pompe	PROPN
bam-9798	36	31	patients	patient	NOUN
bam-9798	36	32	and	and	CCONJ
bam-9798	36	33	whatever	whatever	DET
bam-9798	36	34	research	research	NOUN
bam-9798	36	35	activity	activity	NOUN
bam-9798	36	36	were	be	AUX
bam-9798	36	37	applied	apply	VERB
bam-9798	36	38	in	in	ADP
bam-9798	36	39	the	the	DET
bam-9798	36	40	participants	participant	NOUN
bam-9798	36	41	’	'	PUNCT
bam-9798	36	42	center	center	NOUN
bam-9798	36	43	and/or	and/or	CCONJ
bam-9798	36	44	clinic	clinic	NOUN
bam-9798	36	45	.	.	PUNCT
bam-9798	37	1	through	through	ADP
bam-9798	37	2	discussion	discussion	NOUN
bam-9798	37	3	between	between	ADP
bam-9798	37	4	all	all	DET
bam-9798	37	5	participants	participant	NOUN
bam-9798	37	6	,	,	PUNCT
bam-9798	37	7	consensus	consensus	NOUN
bam-9798	37	8	was	be	AUX
bam-9798	37	9	reached	reach	VERB
bam-9798	37	10	on	on	ADP
bam-9798	37	11	all	all	DET
bam-9798	37	12	topics	topic	NOUN
bam-9798	37	13	.	.	PUNCT
bam-9798	38	1	because	because	SCONJ
bam-9798	38	2	the	the	DET
bam-9798	38	3	assessments	assessment	NOUN
bam-9798	38	4	used	use	VERB
bam-9798	38	5	and	and	CCONJ
bam-9798	38	6	criteria	criterion	NOUN
bam-9798	38	7	applied	apply	VERB
bam-9798	38	8	may	may	AUX
bam-9798	38	9	differ	differ	VERB
bam-9798	38	10	between	between	ADP
bam-9798	38	11	infants	infant	NOUN
bam-9798	38	12	,	,	PUNCT
bam-9798	38	13	children	child	NOUN
bam-9798	38	14	and	and	CCONJ
bam-9798	38	15	adults	adult	NOUN
bam-9798	38	16	,	,	PUNCT
bam-9798	38	17	this	this	DET
bam-9798	38	18	meeting	meeting	NOUN
bam-9798	38	19	focused	focus	VERB
bam-9798	38	20	on	on	ADP
bam-9798	38	21	reaching	reach	VERB
bam-9798	38	22	consensus	consensus	NOUN
bam-9798	38	23	on	on	ADP
bam-9798	38	24	several	several	ADJ
bam-9798	38	25	research	research	NOUN
bam-9798	38	26	and	and	CCONJ
bam-9798	38	27	clinical	clinical	ADJ
bam-9798	38	28	topics	topic	NOUN
bam-9798	38	29	relevant	relevant	ADJ
bam-9798	38	30	for	for	ADP
bam-9798	38	31	adult	adult	NOUN
bam-9798	38	32	and	and	CCONJ
bam-9798	38	33	children	child	NOUN
bam-9798	38	34	patients	patient	NOUN
bam-9798	38	35	.	.	PUNCT
bam-9798	39	1	the	the	DET
bam-9798	39	2	presentation	presentation	NOUN
bam-9798	39	3	on	on	ADP
bam-9798	39	4	the	the	DET
bam-9798	39	5	effect	effect	NOUN
bam-9798	39	6	of	of	ADP
bam-9798	39	7	concomitant	concomitant	ADJ
bam-9798	39	8	effect	effect	NOUN
bam-9798	39	9	of	of	ADP
bam-9798	39	10	nutrition	nutrition	NOUN
bam-9798	39	11	and	and	CCONJ
bam-9798	39	12	exercise	exercise	VERB
bam-9798	39	13	to	to	PART
bam-9798	39	14	ert	ert	AUX
bam-9798	39	15	done	do	VERB
bam-9798	39	16	by	by	ADP
bam-9798	39	17	corrado	corrado	PROPN
bam-9798	39	18	angelini	angelini	PROPN
bam-9798	39	19	on	on	ADP
bam-9798	39	20	behalf	behalf	NOUN
bam-9798	39	21	of	of	ADP
bam-9798	39	22	italian	italian	ADJ
bam-9798	39	23	pompe	pompe	PROPN
bam-9798	39	24	group	group	PROPN
bam-9798	39	25	follows	follow	VERB
bam-9798	39	26	below	below	ADV
bam-9798	39	27	.	.	PUNCT
bam-9798	40	1	fig	fig	NOUN
bam-9798	40	2	1	1	NUM
bam-9798	40	3	.	.	PUNCT
bam-9798	41	1	participants	participant	NOUN
bam-9798	41	2	to	to	ADP
bam-9798	41	3	5th	5th	ADJ
bam-9798	41	4	epoc	epoc	NOUN
bam-9798	41	5	2020	2020	NUM
bam-9798	41	6	,	,	PUNCT
bam-9798	41	7	erika	erika	PROPN
bam-9798	41	8	house	house	PROPN
bam-9798	41	9	on	on	ADP
bam-9798	41	10	29	29	NUM
bam-9798	41	11	february	february	NOUN
bam-9798	41	12	,	,	PUNCT
bam-9798	41	13	universitatsklinikum	universitatsklinikum	NOUN
bam-9798	41	14	,	,	PUNCT
bam-9798	41	15	hamburg	hamburg	NOUN
bam-9798	41	16	-	-	PUNCT
bam-9798	41	17	eppendorf	eppendorf	PROPN
bam-9798	41	18	,	,	PUNCT
bam-9798	41	19	from	from	ADP
bam-9798	41	20	left	left	ADV
bam-9798	41	21	:	:	PUNCT
bam-9798	41	22	thomas	thomas	PROPN
bam-9798	41	23	hundsberger	hundsberger	PROPN
bam-9798	41	24	,	,	PUNCT
bam-9798	41	25	st	st	PROPN
bam-9798	41	26	gallen	gallen	PROPN
bam-9798	41	27	,	,	PUNCT
bam-9798	41	28	switzerland	switzerland	PROPN
bam-9798	41	29	;	;	PUNCT
bam-9798	41	30	george	george	PROPN
bam-9798	41	31	papadimas	papadimas	PROPN
bam-9798	41	32	,	,	PUNCT
bam-9798	41	33	athens	athens	PROPN
bam-9798	41	34	,	,	PUNCT
bam-9798	41	35	greece	greece	PROPN
bam-9798	41	36	;	;	PUNCT
bam-9798	41	37	corrado	corrado	PROPN
bam-9798	41	38	angelini	angelini	PROPN
bam-9798	41	39	,	,	PUNCT
bam-9798	41	40	venice	venice	PROPN
bam-9798	41	41	,	,	PUNCT
bam-9798	41	42	italy	italy	PROPN
bam-9798	41	43	;	;	PUNCT
bam-9798	41	44	jordi	jordi	PROPN
bam-9798	41	45	diaz	diaz	PROPN
bam-9798	41	46	-	-	PUNCT
bam-9798	41	47	manera	manera	PROPN
bam-9798	41	48	,	,	PUNCT
bam-9798	41	49	barcelona	barcelona	PROPN
bam-9798	41	50	,	,	PUNCT
bam-9798	41	51	spain	spain	PROPN
bam-9798	41	52	;	;	PUNCT
bam-9798	41	53	stefan	stefan	PROPN
bam-9798	41	54	hinze	hinze	PROPN
bam-9798	41	55	,	,	PUNCT
bam-9798	41	56	munich	munich	PROPN
bam-9798	41	57	,	,	PUNCT
bam-9798	41	58	gemany	gemany	NOUN
bam-9798	41	59	;	;	PUNCT
bam-9798	41	60	benedikt	benedikt	NOUN
bam-9798	41	61	schoser	schoser	NOUN
bam-9798	41	62	,	,	PUNCT
bam-9798	41	63	munich	munich	PROPN
bam-9798	41	64	,	,	PUNCT
bam-9798	41	65	germany	germany	PROPN
bam-9798	41	66	;	;	PUNCT
bam-9798	41	67	peter	peter	PROPN
bam-9798	41	68	meinke	meinke	PROPN
bam-9798	41	69	,	,	PUNCT
bam-9798	41	70	munich	munich	PROPN
bam-9798	41	71	,	,	PUNCT
bam-9798	41	72	germany	germany	PROPN
bam-9798	41	73	;	;	PUNCT
bam-9798	41	74	robin	robin	PROPN
bam-9798	41	75	lachmann	lachmann	PROPN
bam-9798	41	76	,	,	PUNCT
bam-9798	41	77	london	london	PROPN
bam-9798	41	78	,	,	PUNCT
bam-9798	41	79	uk	uk	PROPN
bam-9798	41	80	;	;	PUNCT
bam-9798	41	81	james	james	PROPN
bam-9798	41	82	davison	davison	PROPN
bam-9798	41	83	,	,	PUNCT
bam-9798	41	84	london	london	PROPN
bam-9798	41	85	,	,	PUNCT
bam-9798	41	86	uk	uk	PROPN
bam-9798	41	87	;	;	PUNCT
bam-9798	41	88	mark	mark	PROPN
bam-9798	41	89	roberts	roberts	PROPN
bam-9798	41	90	,	,	PUNCT
bam-9798	41	91	manchester	manchester	PROPN
bam-9798	41	92	,	,	PUNCT
bam-9798	41	93	uk	uk	PROPN
bam-9798	41	94	.	.	PROPN
bam-9798	41	95	exercise	exercise	NOUN
bam-9798	41	96	and	and	CCONJ
bam-9798	41	97	nutrition	nutrition	NOUN
bam-9798	41	98	in	in	ADP
bam-9798	41	99	late	late	ADJ
bam-9798	41	100	onset	onset	ADJ
bam-9798	41	101	pompe	pompe	PROPN
bam-9798	41	102	disease	disease	PROPN
bam-9798	41	103	eur	eur	PROPN
bam-9798	41	104	j	j	PROPN
bam-9798	41	105	transl	transl	PROPN
bam-9798	41	106	myol	myol	ADV
bam-9798	41	107	31	31	NUM
bam-9798	41	108	(	(	PUNCT
bam-9798	41	109	2	2	NUM
bam-9798	41	110	):	):	PUNCT
bam-9798	41	111	9798	9798	NUM
bam-9798	41	112	,	,	PUNCT
bam-9798	41	113	2021	2021	NUM
bam-9798	41	114	doi	doi	NOUN
bam-9798	41	115	:	:	PUNCT
bam-9798	41	116	10.4081	10.4081	NUM
bam-9798	41	117	/	/	SYM
bam-9798	41	118	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	41	119	3	3	NUM
bam-9798	41	120	exercise	exercise	NOUN
bam-9798	41	121	and	and	CCONJ
bam-9798	41	122	nutrition	nutrition	NOUN
bam-9798	41	123	in	in	ADP
bam-9798	41	124	late	late	ADJ
bam-9798	41	125	onset	onset	ADJ
bam-9798	41	126	pompe	pompe	PROPN
bam-9798	41	127	disease	disease	NOUN
bam-9798	41	128	this	this	DET
bam-9798	41	129	report	report	NOUN
bam-9798	41	130	presents	present	VERB
bam-9798	41	131	the	the	DET
bam-9798	41	132	results	result	NOUN
bam-9798	41	133	of	of	ADP
bam-9798	41	134	the	the	DET
bam-9798	41	135	italian	italian	ADJ
bam-9798	41	136	lopd	lopd	NOUN
bam-9798	41	137	study	study	NOUN
bam-9798	41	138	group	group	NOUN
bam-9798	41	139	on	on	ADP
bam-9798	41	140	65	65	NUM
bam-9798	41	141	patients	patient	NOUN
bam-9798	41	142	.	.	PUNCT
bam-9798	42	1	the	the	DET
bam-9798	42	2	investigation	investigation	NOUN
bam-9798	42	3	aimed	aim	VERB
bam-9798	42	4	to	to	PART
bam-9798	42	5	improve	improve	VERB
bam-9798	42	6	response	response	NOUN
bam-9798	42	7	to	to	PART
bam-9798	42	8	ert	ert	VERB
bam-9798	42	9	in	in	ADP
bam-9798	42	10	adult	adult	NOUN
bam-9798	42	11	patients	patient	NOUN
bam-9798	42	12	,	,	PUNCT
bam-9798	42	13	assessing	assess	VERB
bam-9798	42	14	if	if	SCONJ
bam-9798	42	15	the	the	DET
bam-9798	42	16	prescription	prescription	NOUN
bam-9798	42	17	of	of	ADP
bam-9798	42	18	a	a	DET
bam-9798	42	19	regular	regular	ADJ
bam-9798	42	20	diet	diet	NOUN
bam-9798	42	21	and	and	CCONJ
bam-9798	42	22	exercise	exercise	NOUN
bam-9798	42	23	proved	prove	VERB
bam-9798	42	24	to	to	PART
bam-9798	42	25	be	be	AUX
bam-9798	42	26	beneficial	beneficial	ADJ
bam-9798	42	27	and	and	CCONJ
bam-9798	42	28	should	should	AUX
bam-9798	42	29	be	be	AUX
bam-9798	42	30	included	include	VERB
bam-9798	42	31	in	in	ADP
bam-9798	42	32	recommendations	recommendation	NOUN
bam-9798	42	33	.	.	PUNCT
bam-9798	43	1	materials	material	NOUN
bam-9798	43	2	and	and	CCONJ
bam-9798	43	3	methods	method	NOUN
bam-9798	43	4	patients	patient	NOUN
bam-9798	43	5	patients	patient	NOUN
bam-9798	43	6	were	be	AUX
bam-9798	43	7	enrolled	enrol	VERB
bam-9798	43	8	by	by	ADP
bam-9798	43	9	several	several	ADJ
bam-9798	43	10	italian	italian	ADJ
bam-9798	43	11	centres	centre	NOUN
bam-9798	43	12	:	:	PUNCT
bam-9798	43	13	the	the	DET
bam-9798	43	14	coordinator	coordinator	NOUN
bam-9798	43	15	centre	centre	NOUN
bam-9798	43	16	for	for	ADP
bam-9798	43	17	pompe	pompe	PROPN
bam-9798	43	18	analyzed	analyze	VERB
bam-9798	43	19	the	the	DET
bam-9798	43	20	data	datum	NOUN
bam-9798	43	21	by	by	ADP
bam-9798	43	22	non	non	ADJ
bam-9798	43	23	parametric	parametric	PROPN
bam-9798	43	24	mann	mann	PROPN
bam-9798	43	25	-	-	PUNCT
bam-9798	43	26	whitney	whitney	PROPN
bam-9798	43	27	and	and	CCONJ
bam-9798	43	28	pearson	pearson	PROPN
bam-9798	43	29	’s	’s	PART
bam-9798	43	30	chi	chi	ADJ
bam-9798	43	31	-	-	PUNCT
bam-9798	43	32	squared	square	VERB
bam-9798	43	33	tests	test	NOUN
bam-9798	43	34	and	and	CCONJ
bam-9798	43	35	studied	studied	ADJ
bam-9798	43	36	correlations	correlation	NOUN
bam-9798	43	37	.	.	PUNCT
bam-9798	44	1	it	it	PRON
bam-9798	44	2	was	be	AUX
bam-9798	44	3	agreed	agree	VERB
bam-9798	44	4	that	that	SCONJ
bam-9798	44	5	in	in	ADP
bam-9798	44	6	order	order	NOUN
bam-9798	44	7	to	to	PART
bam-9798	44	8	start	start	VERB
bam-9798	44	9	treatment	treatment	NOUN
bam-9798	44	10	a	a	DET
bam-9798	44	11	patient	patient	NOUN
bam-9798	44	12	needs	need	VERB
bam-9798	44	13	to	to	PART
bam-9798	44	14	be	be	AUX
bam-9798	44	15	symptomatic	symptomatic	ADJ
bam-9798	44	16	.	.	PUNCT
bam-9798	45	1	asymptomatic	asymptomatic	ADJ
bam-9798	45	2	patients	patient	NOUN
bam-9798	45	3	should	should	AUX
bam-9798	45	4	be	be	AUX
bam-9798	45	5	closely	closely	ADV
bam-9798	45	6	monitored	monitor	VERB
bam-9798	45	7	.	.	PUNCT
bam-9798	46	1	severely	severely	ADV
bam-9798	46	2	affected	affect	VERB
bam-9798	46	3	patients	patient	NOUN
bam-9798	46	4	can	can	AUX
bam-9798	46	5	also	also	ADV
bam-9798	46	6	start	start	VERB
bam-9798	46	7	treatment	treatment	NOUN
bam-9798	46	8	,	,	PUNCT
bam-9798	46	9	as	as	ADV
bam-9798	46	10	long	long	ADV
bam-9798	46	11	as	as	SCONJ
bam-9798	46	12	they	they	PRON
bam-9798	46	13	have	have	VERB
bam-9798	46	14	some	some	DET
bam-9798	46	15	remaining	remain	VERB
bam-9798	46	16	muscle	muscle	NOUN
bam-9798	46	17	function	function	NOUN
bam-9798	46	18	.	.	PUNCT
bam-9798	47	1	after	after	ADP
bam-9798	47	2	starting	start	VERB
bam-9798	47	3	treatment	treatment	NOUN
bam-9798	47	4	a	a	DET
bam-9798	47	5	patient	patient	NOUN
bam-9798	47	6	enters	enter	VERB
bam-9798	47	7	a	a	DET
bam-9798	47	8	two	two	NUM
bam-9798	47	9	-	-	PUNCT
bam-9798	47	10	year	year	NOUN
bam-9798	47	11	trial	trial	NOUN
bam-9798	47	12	period	period	NOUN
bam-9798	47	13	,	,	PUNCT
bam-9798	47	14	in	in	ADP
bam-9798	47	15	which	which	PRON
bam-9798	47	16	he	he	PRON
bam-9798	47	17	/	/	SYM
bam-9798	47	18	she	she	PRON
bam-9798	47	19	is	be	AUX
bam-9798	47	20	being	be	AUX
bam-9798	47	21	evaluated	evaluate	VERB
bam-9798	47	22	using	use	VERB
bam-9798	47	23	the	the	DET
bam-9798	47	24	clinical	clinical	ADJ
bam-9798	47	25	outcome	outcome	NOUN
bam-9798	47	26	measures	measure	NOUN
bam-9798	47	27	further	far	ADV
bam-9798	47	28	described	describe	VERB
bam-9798	47	29	.	.	PUNCT
bam-9798	48	1	in	in	ADP
bam-9798	48	2	principle	principle	NOUN
bam-9798	48	3	,	,	PUNCT
bam-9798	48	4	treatment	treatment	NOUN
bam-9798	48	5	will	will	AUX
bam-9798	48	6	be	be	AUX
bam-9798	48	7	discontinued	discontinue	VERB
bam-9798	48	8	if	if	SCONJ
bam-9798	48	9	during	during	ADP
bam-9798	48	10	the	the	DET
bam-9798	48	11	two	two	NUM
bam-9798	48	12	-	-	PUNCT
bam-9798	48	13	year	year	NOUN
bam-9798	48	14	trial	trial	NOUN
bam-9798	48	15	period	period	NOUN
bam-9798	48	16	there	there	PRON
bam-9798	48	17	is	be	VERB
bam-9798	48	18	no	no	DET
bam-9798	48	19	sign	sign	NOUN
bam-9798	48	20	of	of	ADP
bam-9798	48	21	stabilization	stabilization	NOUN
bam-9798	48	22	or	or	CCONJ
bam-9798	48	23	improvement	improvement	NOUN
bam-9798	48	24	.	.	PUNCT
bam-9798	49	1	however	however	ADV
bam-9798	49	2	,	,	PUNCT
bam-9798	49	3	if	if	SCONJ
bam-9798	49	4	the	the	DET
bam-9798	49	5	patient	patient	NOUN
bam-9798	49	6	deteriorates	deteriorate	VERB
bam-9798	49	7	after	after	ADP
bam-9798	49	8	stopping	stop	VERB
bam-9798	49	9	treatment	treatment	NOUN
bam-9798	49	10	,	,	PUNCT
bam-9798	49	11	restarting	restart	VERB
bam-9798	49	12	treatment	treatment	NOUN
bam-9798	49	13	can	can	AUX
bam-9798	49	14	be	be	AUX
bam-9798	49	15	considered	consider	VERB
bam-9798	49	16	.	.	PUNCT
bam-9798	50	1	the	the	DET
bam-9798	50	2	main	main	ADJ
bam-9798	50	3	inclusion	inclusion	NOUN
bam-9798	50	4	criteria	criterion	NOUN
bam-9798	50	5	were	be	AUX
bam-9798	50	6	:	:	PUNCT
bam-9798	50	7	age	age	NOUN
bam-9798	50	8	≥	≥	NUM
bam-9798	50	9	18	18	NUM
bam-9798	50	10	years	year	NOUN
bam-9798	50	11	;	;	PUNCT
bam-9798	50	12	diagnosis	diagnosis	NOUN
bam-9798	50	13	of	of	ADP
bam-9798	50	14	lopd	lopd	NOUN
bam-9798	50	15	confirmed	confirm	VERB
bam-9798	50	16	by	by	ADP
bam-9798	50	17	enzymatic	enzymatic	ADJ
bam-9798	50	18	test	test	NOUN
bam-9798	50	19	and/or	and/or	CCONJ
bam-9798	50	20	genetic	genetic	ADJ
bam-9798	50	21	analysis	analysis	NOUN
bam-9798	50	22	;	;	PUNCT
bam-9798	50	23	regular	regular	ADJ
bam-9798	50	24	ert	ert	NOUN
bam-9798	50	25	for	for	ADP
bam-9798	50	26	at	at	ADV
bam-9798	50	27	least	least	ADV
bam-9798	50	28	2	2	NUM
bam-9798	50	29	years	year	NOUN
bam-9798	50	30	.	.	PUNCT
bam-9798	51	1	main	main	ADJ
bam-9798	51	2	exclusion	exclusion	NOUN
bam-9798	51	3	criteria	criterion	NOUN
bam-9798	51	4	were	be	AUX
bam-9798	51	5	:	:	PUNCT
bam-9798	51	6	presence	presence	NOUN
bam-9798	51	7	of	of	ADP
bam-9798	51	8	significant	significant	ADJ
bam-9798	51	9	cardiovascular	cardiovascular	ADJ
bam-9798	51	10	diseases	disease	NOUN
bam-9798	51	11	(	(	PUNCT
bam-9798	51	12	assessed	assess	VERB
bam-9798	51	13	by	by	ADP
bam-9798	51	14	electrocardiogram	electrocardiogram	NOUN
bam-9798	51	15	or	or	CCONJ
bam-9798	51	16	echocardiography	echocardiography	NOUN
bam-9798	51	17	)	)	PUNCT
bam-9798	51	18	;	;	PUNCT
bam-9798	51	19	wheelchair	wheelchair	NOUN
bam-9798	51	20	bound	bind	VERB
bam-9798	51	21	patients	patient	NOUN
bam-9798	51	22	.	.	PUNCT
bam-9798	52	1	outcome	outcome	NOUN
bam-9798	52	2	dataset	dataset	VERB
bam-9798	52	3	for	for	ADP
bam-9798	52	4	adult	adult	NOUN
bam-9798	52	5	patients	patient	NOUN
bam-9798	52	6	according	accord	VERB
bam-9798	52	7	to	to	ADP
bam-9798	52	8	the	the	DET
bam-9798	52	9	epoc	epoc	NOUN
bam-9798	52	10	study	study	NOUN
bam-9798	52	11	the	the	DET
bam-9798	52	12	results	result	NOUN
bam-9798	52	13	of	of	ADP
bam-9798	52	14	the	the	DET
bam-9798	52	15	different	different	ADJ
bam-9798	52	16	outcome	outcome	NOUN
bam-9798	52	17	measures	measure	NOUN
bam-9798	52	18	were	be	AUX
bam-9798	52	19	used	use	VERB
bam-9798	52	20	,	,	PUNCT
bam-9798	52	21	but	but	CCONJ
bam-9798	52	22	also	also	ADV
bam-9798	52	23	indicated	indicate	VERB
bam-9798	52	24	by	by	ADP
bam-9798	52	25	a	a	DET
bam-9798	52	26	minimal	minimal	ADJ
bam-9798	52	27	dataset	dataset	NOUN
bam-9798	52	28	.	.	PUNCT
bam-9798	53	1	this	this	PRON
bam-9798	53	2	was	be	AUX
bam-9798	53	3	discussed	discuss	VERB
bam-9798	53	4	for	for	ADP
bam-9798	53	5	each	each	PRON
bam-9798	53	6	of	of	ADP
bam-9798	53	7	the	the	DET
bam-9798	53	8	different	different	ADJ
bam-9798	53	9	clinical	clinical	ADJ
bam-9798	53	10	domains	domain	NOUN
bam-9798	53	11	affected	affect	VERB
bam-9798	53	12	in	in	ADP
bam-9798	53	13	adult	adult	NOUN
bam-9798	53	14	patients	patient	NOUN
bam-9798	53	15	(	(	PUNCT
bam-9798	53	16	i.e.	i.e.	X
bam-9798	53	17	skeletal	skeletal	ADJ
bam-9798	53	18	muscle	muscle	NOUN
bam-9798	53	19	strength	strength	NOUN
bam-9798	53	20	and	and	CCONJ
bam-9798	53	21	function	function	NOUN
bam-9798	53	22	)	)	PUNCT
bam-9798	53	23	.	.	PUNCT
bam-9798	54	1	muscle	muscle	NOUN
bam-9798	54	2	function	function	NOUN
bam-9798	54	3	:	:	PUNCT
bam-9798	54	4	6	6	NUM
bam-9798	54	5	minute	minute	NOUN
bam-9798	54	6	walk	walk	NOUN
bam-9798	54	7	test	test	NOUN
bam-9798	54	8	,	,	PUNCT
bam-9798	54	9	gardner	gardner	NOUN
bam-9798	54	10	-	-	PUNCT
bam-9798	54	11	medwinwalton	medwinwalton	NOUN
bam-9798	54	12	(	(	PUNCT
bam-9798	54	13	gmw	gmw	NOUN
bam-9798	54	14	)	)	PUNCT
bam-9798	54	15	the	the	DET
bam-9798	54	16	6	6	NUM
bam-9798	54	17	minute	minute	NOUN
bam-9798	54	18	walk	walk	NOUN
bam-9798	54	19	test	test	NOUN
bam-9798	54	20	(	(	PUNCT
bam-9798	54	21	6mwt	6mwt	NUM
bam-9798	54	22	)	)	PUNCT
bam-9798	54	23	and	and	CCONJ
bam-9798	54	24	gmw	gmw	NOUN
bam-9798	54	25	were	be	AUX
bam-9798	54	26	selected	select	VERB
bam-9798	54	27	to	to	PART
bam-9798	54	28	assess	assess	VERB
bam-9798	54	29	muscle	muscle	NOUN
bam-9798	54	30	function	function	NOUN
bam-9798	54	31	.	.	PUNCT
bam-9798	55	1	the	the	DET
bam-9798	55	2	6mwt	6mwt	PROPN
bam-9798	55	3	provides	provide	VERB
bam-9798	55	4	information	information	NOUN
bam-9798	55	5	on	on	ADP
bam-9798	55	6	endurance	endurance	NOUN
bam-9798	55	7	as	as	ADV
bam-9798	55	8	well	well	ADV
bam-9798	55	9	as	as	ADP
bam-9798	55	10	walking	walk	VERB
bam-9798	55	11	speed.12	speed.12	NOUN
bam-9798	55	12	a	a	DET
bam-9798	55	13	major	major	ADJ
bam-9798	55	14	reason	reason	NOUN
bam-9798	55	15	to	to	PART
bam-9798	55	16	include	include	VERB
bam-9798	55	17	the	the	DET
bam-9798	55	18	6mwt	6mwt	PROPN
bam-9798	55	19	is	be	AUX
bam-9798	55	20	that	that	SCONJ
bam-9798	55	21	it	it	PRON
bam-9798	55	22	has	have	AUX
bam-9798	55	23	been	be	AUX
bam-9798	55	24	used	use	VERB
bam-9798	55	25	as	as	ADP
bam-9798	55	26	a	a	DET
bam-9798	55	27	major	major	ADJ
bam-9798	55	28	clinical	clinical	ADJ
bam-9798	55	29	outcome	outcome	NOUN
bam-9798	55	30	measure	measure	NOUN
bam-9798	55	31	in	in	ADP
bam-9798	55	32	all	all	DET
bam-9798	55	33	clinical	clinical	ADJ
bam-9798	55	34	trials	trial	NOUN
bam-9798	55	35	of	of	ADP
bam-9798	55	36	adults	adult	NOUN
bam-9798	55	37	,	,	PUNCT
bam-9798	55	38	and	and	CCONJ
bam-9798	55	39	gmw	gmw	NOUN
bam-9798	55	40	scale	scale	NOUN
bam-9798	55	41	as	as	ADP
bam-9798	55	42	monitoring	monitor	VERB
bam-9798	55	43	tool	tool	NOUN
bam-9798	55	44	used	use	VERB
bam-9798	55	45	in	in	ADP
bam-9798	55	46	many	many	ADJ
bam-9798	55	47	centres	centre	NOUN
bam-9798	55	48	,	,	PUNCT
bam-9798	55	49	allowing	allow	VERB
bam-9798	55	50	for	for	ADP
bam-9798	55	51	long	long	ADJ
bam-9798	55	52	-	-	PUNCT
bam-9798	55	53	term	term	NOUN
bam-9798	55	54	follow	follow	NOUN
bam-9798	55	55	-	-	PUNCT
bam-9798	55	56	up	up	NOUN
bam-9798	55	57	and	and	CCONJ
bam-9798	55	58	comparability	comparability	NOUN
bam-9798	55	59	.	.	PUNCT
bam-9798	56	1	the	the	DET
bam-9798	56	2	grade	grade	NOUN
bam-9798	56	3	of	of	ADP
bam-9798	56	4	gmw	gmw	NOUN
bam-9798	56	5	scale	scale	NOUN
bam-9798	56	6	was	be	AUX
bam-9798	56	7	obtained	obtain	VERB
bam-9798	56	8	for	for	ADP
bam-9798	56	9	each	each	DET
bam-9798	56	10	patient	patient	NOUN
bam-9798	56	11	as	as	ADP
bam-9798	56	12	follow	follow	NOUN
bam-9798	56	13	:	:	PUNCT
bam-9798	57	1	grade	grade	NOUN
bam-9798	57	2	0	0	NUM
bam-9798	57	3	=	=	SYM
bam-9798	57	4	hyperckemia	hyperckemia	NOUN
bam-9798	57	5	,	,	PUNCT
bam-9798	57	6	all	all	DET
bam-9798	57	7	activities	activity	NOUN
bam-9798	57	8	normal	normal	ADJ
bam-9798	57	9	;	;	PUNCT
bam-9798	57	10	grade	grade	NOUN
bam-9798	57	11	1	1	NUM
bam-9798	57	12	=	=	SYM
bam-9798	57	13	normal	normal	ADJ
bam-9798	57	14	gait	gait	NOUN
bam-9798	57	15	,	,	PUNCT
bam-9798	57	16	unable	unable	ADJ
bam-9798	57	17	to	to	PART
bam-9798	57	18	run	run	VERB
bam-9798	57	19	freely	freely	ADV
bam-9798	57	20	,	,	PUNCT
bam-9798	57	21	myalgia	myalgia	NOUN
bam-9798	57	22	;	;	PUNCT
bam-9798	57	23	grade	grade	NOUN
bam-9798	57	24	2	2	NUM
bam-9798	57	25	=	=	NOUN
bam-9798	57	26	incapacity	incapacity	NOUN
bam-9798	57	27	to	to	PART
bam-9798	57	28	walk	walk	VERB
bam-9798	57	29	on	on	ADP
bam-9798	57	30	tiptoes	tiptoe	NOUN
bam-9798	57	31	,	,	PUNCT
bam-9798	57	32	waddling	waddling	NOUN
bam-9798	57	33	gait	gait	NOUN
bam-9798	57	34	;	;	PUNCT
bam-9798	57	35	grade	grade	NOUN
bam-9798	57	36	3	3	NUM
bam-9798	57	37	=	=	SYM
bam-9798	57	38	evident	evident	ADJ
bam-9798	57	39	muscular	muscular	ADJ
bam-9798	57	40	weakness	weakness	NOUN
bam-9798	57	41	,	,	PUNCT
bam-9798	57	42	steppage	steppage	NOUN
bam-9798	57	43	and	and	CCONJ
bam-9798	57	44	climbing	climb	VERB
bam-9798	57	45	stairs	stair	NOUN
bam-9798	57	46	with	with	ADP
bam-9798	57	47	banister	banister	NOUN
bam-9798	57	48	;	;	PUNCT
bam-9798	57	49	grade	grade	NOUN
bam-9798	57	50	4	4	NUM
bam-9798	57	51	=	=	NOUN
bam-9798	57	52	difficulty	difficulty	NOUN
bam-9798	57	53	to	to	PART
bam-9798	57	54	rise	rise	VERB
bam-9798	57	55	from	from	ADP
bam-9798	57	56	the	the	DET
bam-9798	57	57	floor	floor	NOUN
bam-9798	57	58	,	,	PUNCT
bam-9798	57	59	gowers	gower	NOUN
bam-9798	57	60	’	'	PUNCT
bam-9798	57	61	sign	sign	NOUN
bam-9798	57	62	;	;	PUNCT
bam-9798	57	63	grade	grade	NOUN
bam-9798	57	64	5	5	NUM
bam-9798	57	65	=	=	NOUN
bam-9798	57	66	incapacity	incapacity	NOUN
bam-9798	57	67	to	to	PART
bam-9798	57	68	rise	rise	VERB
bam-9798	57	69	from	from	ADP
bam-9798	57	70	the	the	DET
bam-9798	57	71	floor	floor	NOUN
bam-9798	57	72	;	;	PUNCT
bam-9798	57	73	grade	grade	NOUN
bam-9798	57	74	6	6	NUM
bam-9798	57	75	=	=	NOUN
bam-9798	57	76	incapacity	incapacity	NOUN
bam-9798	57	77	to	to	PART
bam-9798	57	78	climb	climb	VERB
bam-9798	57	79	stairs	stair	NOUN
bam-9798	57	80	;	;	PUNCT
bam-9798	57	81	grade	grade	NOUN
bam-9798	57	82	7	7	NUM
bam-9798	57	83	=	=	NOUN
bam-9798	57	84	incapacity	incapacity	NOUN
bam-9798	57	85	to	to	PART
bam-9798	57	86	rise	rise	VERB
bam-9798	57	87	,	,	PUNCT
bam-9798	57	88	from	from	ADP
bam-9798	57	89	a	a	DET
bam-9798	57	90	chair	chair	NOUN
bam-9798	57	91	;	;	PUNCT
bam-9798	57	92	grade	grade	NOUN
bam-9798	57	93	8	8	NUM
bam-9798	57	94	=	=	SYM
bam-9798	57	95	unable	unable	ADJ
bam-9798	57	96	to	to	PART
bam-9798	57	97	walk	walk	VERB
bam-9798	57	98	unassisted	unassiste	VERB
bam-9798	57	99	;	;	PUNCT
bam-9798	57	100	grade	grade	NOUN
bam-9798	57	101	9	9	NUM
bam-9798	57	102	=	=	SYM
bam-9798	57	103	unable	unable	ADJ
bam-9798	57	104	to	to	PART
bam-9798	57	105	eat	eat	VERB
bam-9798	57	106	unassisted	unassiste	VERB
bam-9798	57	107	.	.	PUNCT
bam-9798	58	1	the	the	DET
bam-9798	58	2	gsgc	gsgc	PROPN
bam-9798	58	3	scale	scale	NOUN
bam-9798	58	4	provides	provide	VERB
bam-9798	58	5	a	a	DET
bam-9798	58	6	time	time	NOUN
bam-9798	58	7	quantitative	quantitative	ADJ
bam-9798	58	8	and	and	CCONJ
bam-9798	58	9	scored	score	VERB
bam-9798	58	10	measurement	measurement	NOUN
bam-9798	58	11	of	of	ADP
bam-9798	58	12	four	four	NUM
bam-9798	58	13	main	main	ADJ
bam-9798	58	14	motor	motor	NOUN
bam-9798	58	15	performances:12	performances:12	X
bam-9798	58	16	g	g	NOUN
bam-9798	58	17	:	:	PUNCT
bam-9798	58	18	gait	gait	NOUN
bam-9798	58	19	(	(	PUNCT
bam-9798	58	20	walk	walk	VERB
bam-9798	58	21	10	10	NUM
bam-9798	58	22	meters	meter	NOUN
bam-9798	58	23	)	)	PUNCT
bam-9798	58	24	s	s	VERB
bam-9798	58	25	:	:	PUNCT
bam-9798	58	26	stairs	stair	NOUN
bam-9798	58	27	(	(	PUNCT
bam-9798	58	28	climb	climb	VERB
bam-9798	58	29	4	4	NUM
bam-9798	58	30	steps	step	NOUN
bam-9798	58	31	)	)	PUNCT
bam-9798	59	1	g	g	NOUN
bam-9798	59	2	:	:	PUNCT
bam-9798	59	3	gowers	gowers	PROPN
bam-9798	59	4	’	'	PUNCT
bam-9798	59	5	maneuver	maneuver	NOUN
bam-9798	59	6	(	(	PUNCT
bam-9798	59	7	raise	raise	VERB
bam-9798	59	8	from	from	ADP
bam-9798	59	9	the	the	DET
bam-9798	59	10	floor	floor	NOUN
bam-9798	59	11	)	)	PUNCT
bam-9798	60	1	c	c	X
bam-9798	60	2	:	:	PUNCT
bam-9798	60	3	chair	chair	NOUN
bam-9798	60	4	(	(	PUNCT
bam-9798	60	5	rise	rise	VERB
bam-9798	60	6	from	from	ADP
bam-9798	60	7	a	a	DET
bam-9798	60	8	chair	chair	NOUN
bam-9798	60	9	)	)	PUNCT
bam-9798	60	10	.	.	PUNCT
bam-9798	61	1	it	it	PRON
bam-9798	61	2	was	be	AUX
bam-9798	61	3	agreed	agree	VERB
bam-9798	61	4	that	that	SCONJ
bam-9798	61	5	in	in	ADP
bam-9798	61	6	order	order	NOUN
bam-9798	61	7	to	to	PART
bam-9798	61	8	start	start	VERB
bam-9798	61	9	treatment	treatment	NOUN
bam-9798	61	10	a	a	DET
bam-9798	61	11	patient	patient	NOUN
bam-9798	61	12	needs	need	VERB
bam-9798	61	13	to	to	PART
bam-9798	61	14	be	be	AUX
bam-9798	61	15	symptomatic	symptomatic	ADJ
bam-9798	61	16	.	.	PUNCT
bam-9798	62	1	severely	severely	ADV
bam-9798	62	2	affected	affect	VERB
bam-9798	62	3	patients	patient	NOUN
bam-9798	62	4	can	can	AUX
bam-9798	62	5	also	also	ADV
bam-9798	62	6	start	start	VERB
bam-9798	62	7	treatment	treatment	NOUN
bam-9798	62	8	,	,	PUNCT
bam-9798	62	9	as	as	ADV
bam-9798	62	10	long	long	ADV
bam-9798	62	11	as	as	SCONJ
bam-9798	62	12	they	they	PRON
bam-9798	62	13	have	have	VERB
bam-9798	62	14	some	some	DET
bam-9798	62	15	remaining	remain	VERB
bam-9798	62	16	muscle	muscle	NOUN
bam-9798	62	17	function	function	NOUN
bam-9798	62	18	,	,	PUNCT
bam-9798	62	19	after	after	SCONJ
bam-9798	62	20	a	a	DET
bam-9798	62	21	patient	patient	NOUN
bam-9798	62	22	enters	enter	VERB
bam-9798	62	23	a	a	DET
bam-9798	62	24	two	two	NUM
bam-9798	62	25	-	-	PUNCT
bam-9798	62	26	year	year	NOUN
bam-9798	62	27	trial	trial	NOUN
bam-9798	62	28	period	period	NOUN
bam-9798	62	29	,	,	PUNCT
bam-9798	62	30	in	in	ADP
bam-9798	62	31	which	which	PRON
bam-9798	62	32	he	he	PRON
bam-9798	62	33	/	/	SYM
bam-9798	62	34	she	she	PRON
bam-9798	62	35	is	be	AUX
bam-9798	62	36	being	be	AUX
bam-9798	62	37	evaluated	evaluate	VERB
bam-9798	62	38	using	use	VERB
bam-9798	62	39	the	the	DET
bam-9798	62	40	clinical	clinical	ADJ
bam-9798	62	41	outcome	outcome	NOUN
bam-9798	62	42	measures	measure	NOUN
bam-9798	62	43	described	describe	VERB
bam-9798	62	44	,	,	PUNCT
bam-9798	62	45	treatment	treatment	NOUN
bam-9798	62	46	will	will	AUX
bam-9798	62	47	be	be	AUX
bam-9798	62	48	discontinued	discontinue	VERB
bam-9798	62	49	if	if	SCONJ
bam-9798	62	50	during	during	ADP
bam-9798	62	51	the	the	DET
bam-9798	62	52	two	two	NUM
bam-9798	62	53	-	-	PUNCT
bam-9798	62	54	year	year	NOUN
bam-9798	62	55	trial	trial	NOUN
bam-9798	62	56	period	period	NOUN
bam-9798	62	57	there	there	PRON
bam-9798	62	58	is	be	VERB
bam-9798	62	59	no	no	DET
bam-9798	62	60	sign	sign	NOUN
bam-9798	62	61	of	of	ADP
bam-9798	62	62	stabilization	stabilization	NOUN
bam-9798	62	63	or	or	CCONJ
bam-9798	62	64	improvement	improvement	NOUN
bam-9798	62	65	.	.	PUNCT
bam-9798	63	1	however	however	ADV
bam-9798	63	2	,	,	PUNCT
bam-9798	63	3	if	if	SCONJ
bam-9798	63	4	the	the	DET
bam-9798	63	5	patient	patient	NOUN
bam-9798	63	6	deteriorates	deteriorate	VERB
bam-9798	63	7	after	after	ADP
bam-9798	63	8	stopping	stop	VERB
bam-9798	63	9	treatment	treatment	NOUN
bam-9798	63	10	,	,	PUNCT
bam-9798	63	11	restarting	restart	VERB
bam-9798	63	12	treatment	treatment	NOUN
bam-9798	63	13	can	can	AUX
bam-9798	63	14	be	be	AUX
bam-9798	63	15	considered	consider	VERB
bam-9798	63	16	.	.	PUNCT
bam-9798	64	1	muscle	muscle	NOUN
bam-9798	64	2	strength	strength	NOUN
bam-9798	64	3	manual	manual	ADJ
bam-9798	64	4	muscle	muscle	NOUN
bam-9798	64	5	testing	testing	NOUN
bam-9798	64	6	using	use	VERB
bam-9798	64	7	the	the	DET
bam-9798	64	8	medical	medical	ADJ
bam-9798	64	9	research	research	PROPN
bam-9798	64	10	council	council	PROPN
bam-9798	64	11	(	(	PUNCT
bam-9798	64	12	mrc	mrc	NOUN
bam-9798	64	13	)	)	PUNCT
bam-9798	64	14	grading	grading	NOUN
bam-9798	64	15	scale	scale	NOUN
bam-9798	64	16	was	be	AUX
bam-9798	64	17	selected	select	VERB
bam-9798	64	18	to	to	PART
bam-9798	64	19	assess	assess	VERB
bam-9798	64	20	muscle	muscle	NOUN
bam-9798	64	21	strength	strength	NOUN
bam-9798	64	22	.	.	PUNCT
bam-9798	65	1	to	to	PART
bam-9798	65	2	ensure	ensure	VERB
bam-9798	65	3	these	these	DET
bam-9798	65	4	data	datum	NOUN
bam-9798	65	5	are	be	AUX
bam-9798	65	6	consistent	consistent	ADJ
bam-9798	65	7	,	,	PUNCT
bam-9798	65	8	a	a	DET
bam-9798	65	9	scale	scale	NOUN
bam-9798	65	10	ranging	range	VERB
bam-9798	65	11	from	from	ADP
bam-9798	65	12	0	0	NUM
bam-9798	65	13	to	to	ADP
bam-9798	65	14	five	five	NUM
bam-9798	65	15	without	without	ADP
bam-9798	65	16	+	+	ADJ
bam-9798	65	17	/	/	SYM
bam-9798	65	18	–	–	PUNCT
bam-9798	65	19	notification	notification	NOUN
bam-9798	65	20	should	should	AUX
bam-9798	65	21	be	be	AUX
bam-9798	65	22	used	use	VERB
bam-9798	65	23	.	.	PUNCT
bam-9798	66	1	muscle	muscle	NOUN
bam-9798	66	2	groups	group	NOUN
bam-9798	66	3	to	to	PART
bam-9798	66	4	include	include	VERB
bam-9798	66	5	are	be	AUX
bam-9798	66	6	(	(	PUNCT
bam-9798	66	7	left	left	ADJ
bam-9798	66	8	and	and	CCONJ
bam-9798	66	9	right	right	ADJ
bam-9798	66	10	side	side	NOUN
bam-9798	66	11	if	if	SCONJ
bam-9798	66	12	applicable	applicable	ADJ
bam-9798	66	13	):	):	PUNCT
bam-9798	66	14	neck	neck	NOUN
bam-9798	66	15	extensors	extensor	NOUN
bam-9798	66	16	,	,	PUNCT
bam-9798	66	17	neck	neck	NOUN
bam-9798	66	18	flexors	flexor	NOUN
bam-9798	66	19	,	,	PUNCT
bam-9798	66	20	shoulder	shoulder	NOUN
bam-9798	66	21	abductors	abductor	NOUN
bam-9798	66	22	,	,	PUNCT
bam-9798	66	23	elbow	elbow	NOUN
bam-9798	66	24	flexors	flexor	NOUN
bam-9798	66	25	,	,	PUNCT
bam-9798	66	26	elbow	elbow	VERB
bam-9798	66	27	extensors	extensor	NOUN
bam-9798	66	28	,	,	PUNCT
bam-9798	66	29	hip	hip	NOUN
bam-9798	66	30	flexors	flexor	NOUN
bam-9798	66	31	,	,	PUNCT
bam-9798	66	32	hip	hip	NOUN
bam-9798	66	33	extensors	extensor	NOUN
bam-9798	66	34	,	,	PUNCT
bam-9798	66	35	hip	hip	NOUN
bam-9798	66	36	abductors	abductor	NOUN
bam-9798	66	37	,	,	PUNCT
bam-9798	66	38	knee	knee	NOUN
bam-9798	66	39	flexors	flexor	NOUN
bam-9798	66	40	,	,	PUNCT
bam-9798	66	41	knee	knee	NOUN
bam-9798	66	42	extensors	extensor	NOUN
bam-9798	66	43	.	.	PUNCT
bam-9798	67	1	excluded	exclude	VERB
bam-9798	67	2	muscle	muscle	NOUN
bam-9798	67	3	groups	group	NOUN
bam-9798	67	4	were	be	AUX
bam-9798	67	5	the	the	DET
bam-9798	67	6	shoulder	shoulder	NOUN
bam-9798	67	7	adductors	adductor	NOUN
bam-9798	67	8	,	,	PUNCT
bam-9798	67	9	arm	arm	VERB
bam-9798	67	10	extra	extra	ADJ
bam-9798	67	11	-	-	NOUN
bam-9798	67	12	rotators	rotator	NOUN
bam-9798	67	13	and	and	CCONJ
bam-9798	67	14	endo	endo	NOUN
bam-9798	67	15	-	-	PUNCT
bam-9798	67	16	rotators	rotator	NOUN
bam-9798	67	17	muscle	muscle	NOUN
bam-9798	67	18	groups	group	NOUN
bam-9798	67	19	,	,	PUNCT
bam-9798	67	20	since	since	SCONJ
bam-9798	67	21	these	these	PRON
bam-9798	67	22	are	be	AUX
bam-9798	67	23	relatively	relatively	ADV
bam-9798	67	24	difficult	difficult	ADJ
bam-9798	67	25	to	to	PART
bam-9798	67	26	measure	measure	VERB
bam-9798	67	27	and	and	CCONJ
bam-9798	67	28	to	to	PART
bam-9798	67	29	standardize	standardize	VERB
bam-9798	67	30	,	,	PUNCT
bam-9798	67	31	and	and	CCONJ
bam-9798	67	32	the	the	DET
bam-9798	67	33	strength	strength	NOUN
bam-9798	67	34	of	of	ADP
bam-9798	67	35	these	these	DET
bam-9798	67	36	muscles	muscle	NOUN
bam-9798	67	37	is	be	AUX
bam-9798	67	38	usually	usually	ADV
bam-9798	67	39	reflected	reflect	VERB
bam-9798	67	40	by	by	ADP
bam-9798	67	41	that	that	PRON
bam-9798	67	42	of	of	ADP
bam-9798	67	43	the	the	DET
bam-9798	67	44	arm	arm	NOUN
bam-9798	67	45	abductors	abductor	NOUN
bam-9798	67	46	.	.	PUNCT
bam-9798	68	1	pulmonary	pulmonary	ADJ
bam-9798	68	2	function	function	NOUN
bam-9798	68	3	:	:	PUNCT
bam-9798	68	4	forced	force	VERB
bam-9798	68	5	vital	vital	ADJ
bam-9798	68	6	capacity	capacity	NOUN
bam-9798	68	7	(	(	PUNCT
bam-9798	68	8	fvc	fvc	PROPN
bam-9798	68	9	)	)	PUNCT
bam-9798	68	10	in	in	ADP
bam-9798	68	11	sitting	sit	VERB
bam-9798	68	12	and	and	CCONJ
bam-9798	68	13	supine	supine	ADJ
bam-9798	68	14	position	position	NOUN
bam-9798	68	15	were	be	AUX
bam-9798	68	16	included	include	VERB
bam-9798	68	17	to	to	PART
bam-9798	68	18	assess	assess	VERB
bam-9798	68	19	pulmonary	pulmonary	ADJ
bam-9798	68	20	function	function	NOUN
bam-9798	68	21	.	.	PUNCT
bam-9798	69	1	it	it	PRON
bam-9798	69	2	is	be	AUX
bam-9798	69	3	important	important	ADJ
bam-9798	69	4	to	to	PART
bam-9798	69	5	measure	measure	VERB
bam-9798	69	6	fvc	fvc	PROPN
bam-9798	69	7	in	in	ADP
bam-9798	69	8	both	both	PRON
bam-9798	69	9	sitting	sit	VERB
bam-9798	69	10	and	and	CCONJ
bam-9798	69	11	supine	supine	ADJ
bam-9798	69	12	position	position	NOUN
bam-9798	69	13	,	,	PUNCT
bam-9798	69	14	because	because	SCONJ
bam-9798	69	15	diaphragmatic	diaphragmatic	ADJ
bam-9798	69	16	weakness	weakness	NOUN
bam-9798	69	17	is	be	AUX
bam-9798	69	18	common	common	ADJ
bam-9798	69	19	in	in	ADP
bam-9798	69	20	pompe	pompe	PROPN
bam-9798	69	21	disease	disease	PROPN
bam-9798	69	22	patient	patient	NOUN
bam-9798	69	23	reported	report	VERB
bam-9798	69	24	outcomes	outcome	NOUN
bam-9798	69	25	for	for	ADP
bam-9798	69	26	ert	ert	NOUN
bam-9798	69	27	treatment	treatment	NOUN
bam-9798	69	28	as	as	ADP
bam-9798	69	29	a	a	DET
bam-9798	69	30	new	new	ADJ
bam-9798	69	31	item	item	NOUN
bam-9798	69	32	of	of	ADP
bam-9798	69	33	response	response	NOUN
bam-9798	69	34	in	in	ADP
bam-9798	69	35	this	this	DET
bam-9798	69	36	study	study	NOUN
bam-9798	69	37	was	be	AUX
bam-9798	69	38	used	use	VERB
bam-9798	69	39	a	a	DET
bam-9798	69	40	disease	disease	NOUN
bam-9798	69	41	-	-	PUNCT
bam-9798	69	42	specific	specific	ADJ
bam-9798	69	43	activity	activity	NOUN
bam-9798	69	44	scale	scale	NOUN
bam-9798	69	45	,	,	PUNCT
bam-9798	69	46	here	here	ADV
bam-9798	69	47	presented	present	VERB
bam-9798	69	48	(	(	PUNCT
bam-9798	69	49	figure	figure	NOUN
bam-9798	69	50	2	2	NUM
bam-9798	69	51	)	)	PUNCT
bam-9798	69	52	.	.	PUNCT
bam-9798	70	1	this	this	DET
bam-9798	70	2	brief	brief	ADJ
bam-9798	70	3	questionnaire	questionnaire	NOUN
bam-9798	70	4	consists	consist	VERB
bam-9798	70	5	of	of	ADP
bam-9798	70	6	5	5	NUM
bam-9798	70	7	items	item	NOUN
bam-9798	70	8	and	and	CCONJ
bam-9798	70	9	was	be	AUX
bam-9798	70	10	developed	develop	VERB
bam-9798	70	11	to	to	PART
bam-9798	70	12	measure	measure	VERB
bam-9798	70	13	the	the	DET
bam-9798	70	14	change	change	NOUN
bam-9798	70	15	of	of	ADP
bam-9798	70	16	function	function	NOUN
bam-9798	70	17	evaluated	evaluate	VERB
bam-9798	70	18	by	by	ADP
bam-9798	70	19	late	late	ADJ
bam-9798	70	20	-	-	PUNCT
bam-9798	70	21	onset	onset	NOUN
bam-9798	70	22	pompe	pompe	PROPN
bam-9798	70	23	patients	patient	NOUN
bam-9798	70	24	’	'	PUNCT
bam-9798	70	25	in	in	ADP
bam-9798	70	26	their	their	PRON
bam-9798	70	27	ability	ability	NOUN
bam-9798	70	28	to	to	PART
bam-9798	70	29	carry	carry	VERB
bam-9798	70	30	out	out	ADP
bam-9798	70	31	daily	daily	ADJ
bam-9798	70	32	life	life	NOUN
bam-9798	70	33	activities	activity	NOUN
bam-9798	70	34	and	and	CCONJ
bam-9798	70	35	functions	function	NOUN
bam-9798	70	36	similar	similar	ADJ
bam-9798	70	37	to	to	ADP
bam-9798	70	38	what	what	PRON
bam-9798	70	39	described	describe	VERB
bam-9798	70	40	in	in	ADP
bam-9798	70	41	gsgc	gsgc	ADJ
bam-9798	70	42	scale	scale	NOUN
bam-9798	70	43	.	.	PUNCT
bam-9798	71	1	this	this	DET
bam-9798	71	2	scale	scale	NOUN
bam-9798	71	3	was	be	AUX
bam-9798	71	4	validated	validate	VERB
bam-9798	71	5	in	in	ADP
bam-9798	71	6	40	40	NUM
bam-9798	71	7	patients	patient	NOUN
bam-9798	71	8	in	in	ADP
bam-9798	71	9	a	a	DET
bam-9798	71	10	previous	previous	ADJ
bam-9798	71	11	study	study	NOUN
bam-9798	71	12	showing	show	VERB
bam-9798	71	13	improvement	improvement	NOUN
bam-9798	71	14	of	of	ADP
bam-9798	71	15	functions.13	functions.13	PROPN
bam-9798	71	16	nutrition	nutrition	NOUN
bam-9798	71	17	and	and	CCONJ
bam-9798	71	18	exercise	exercise	VERB
bam-9798	71	19	information	information	NOUN
bam-9798	71	20	collected	collect	VERB
bam-9798	71	21	in	in	ADP
bam-9798	71	22	the	the	DET
bam-9798	71	23	study	study	NOUN
bam-9798	71	24	to	to	PART
bam-9798	71	25	allow	allow	VERB
bam-9798	71	26	objective	objective	ADJ
bam-9798	71	27	and	and	CCONJ
bam-9798	71	28	self	self	NOUN
bam-9798	71	29	-	-	PUNCT
bam-9798	71	30	reported	report	VERB
bam-9798	71	31	dataset	dataset	NOUN
bam-9798	71	32	to	to	PART
bam-9798	71	33	be	be	AUX
bam-9798	71	34	used	use	VERB
bam-9798	71	35	for	for	ADP
bam-9798	71	36	analysis	analysis	NOUN
bam-9798	71	37	of	of	ADP
bam-9798	71	38	the	the	DET
bam-9798	71	39	effects	effect	NOUN
bam-9798	71	40	of	of	ADP
bam-9798	71	41	treatment	treatment	NOUN
bam-9798	71	42	and	and	CCONJ
bam-9798	71	43	prognostic	prognostic	ADJ
bam-9798	71	44	factors	factor	NOUN
bam-9798	71	45	,	,	PUNCT
bam-9798	71	46	it	it	PRON
bam-9798	71	47	is	be	AUX
bam-9798	71	48	important	important	ADJ
bam-9798	71	49	to	to	PART
bam-9798	71	50	collect	collect	VERB
bam-9798	71	51	information	information	NOUN
bam-9798	71	52	on	on	ADP
bam-9798	71	53	treatment	treatment	NOUN
bam-9798	71	54	exercise	exercise	NOUN
bam-9798	71	55	and	and	CCONJ
bam-9798	71	56	nutrition	nutrition	NOUN
bam-9798	71	57	in	in	ADP
bam-9798	71	58	late	late	ADJ
bam-9798	71	59	onset	onset	ADJ
bam-9798	71	60	pompe	pompe	PROPN
bam-9798	71	61	disease	disease	PROPN
bam-9798	71	62	eur	eur	PROPN
bam-9798	71	63	j	j	PROPN
bam-9798	71	64	transl	transl	PROPN
bam-9798	71	65	myol	myol	ADV
bam-9798	71	66	31	31	NUM
bam-9798	71	67	(	(	PUNCT
bam-9798	71	68	2	2	NUM
bam-9798	71	69	):	):	PUNCT
bam-9798	71	70	9798	9798	NUM
bam-9798	71	71	,	,	PUNCT
bam-9798	71	72	2021	2021	NUM
bam-9798	71	73	doi	doi	NOUN
bam-9798	71	74	:	:	PUNCT
bam-9798	71	75	10.4081	10.4081	NUM
bam-9798	71	76	/	/	SYM
bam-9798	71	77	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	71	78	4	4	NUM
bam-9798	71	79	(	(	PUNCT
bam-9798	71	80	has	have	AUX
bam-9798	71	81	the	the	DET
bam-9798	71	82	patient	patient	NOUN
bam-9798	71	83	regularly	regularly	ADV
bam-9798	71	84	received	receive	VERB
bam-9798	71	85	medication	medication	NOUN
bam-9798	71	86	for	for	ADP
bam-9798	71	87	pompe	pompe	PROPN
bam-9798	71	88	disease	disease	NOUN
bam-9798	71	89	,	,	PUNCT
bam-9798	71	90	and	and	CCONJ
bam-9798	71	91	if	if	SCONJ
bam-9798	71	92	so	so	ADV
bam-9798	71	93	,	,	PUNCT
bam-9798	71	94	which	which	DET
bam-9798	71	95	treatment	treatment	NOUN
bam-9798	71	96	and	and	CCONJ
bam-9798	71	97	since	since	SCONJ
bam-9798	71	98	/	/	SYM
bam-9798	71	99	until	until	ADP
bam-9798	71	100	when	when	SCONJ
bam-9798	71	101	)	)	PUNCT
bam-9798	71	102	as	as	ADV
bam-9798	71	103	well	well	ADV
bam-9798	71	104	as	as	ADP
bam-9798	71	105	type	type	NOUN
bam-9798	71	106	of	of	ADP
bam-9798	71	107	exercise	exercise	NOUN
bam-9798	71	108	and	and	CCONJ
bam-9798	71	109	nutrition	nutrition	NOUN
bam-9798	71	110	status	status	NOUN
bam-9798	71	111	(	(	PUNCT
bam-9798	71	112	including	include	VERB
bam-9798	71	113	daily	daily	ADJ
bam-9798	71	114	diet	diet	NOUN
bam-9798	71	115	and	and	CCONJ
bam-9798	71	116	type	type	NOUN
bam-9798	71	117	of	of	ADP
bam-9798	71	118	diet	diet	NOUN
bam-9798	71	119	)	)	PUNCT
bam-9798	71	120	as	as	ADP
bam-9798	71	121	supportive	supportive	ADJ
bam-9798	71	122	therapy	therapy	NOUN
bam-9798	71	123	.	.	PUNCT
bam-9798	72	1	a	a	DET
bam-9798	72	2	study	study	NOUN
bam-9798	72	3	published	publish	VERB
bam-9798	72	4	in	in	ADP
bam-9798	72	5	the	the	DET
bam-9798	72	6	pre	pre	ADJ
bam-9798	72	7	-	-	ADJ
bam-9798	72	8	ert	ert	ADJ
bam-9798	72	9	era	era	NOUN
bam-9798	72	10	,	,	PUNCT
bam-9798	72	11	dealing	deal	VERB
bam-9798	72	12	with	with	ADP
bam-9798	72	13	lopd	lopd	NOUN
bam-9798	72	14	patients	patient	NOUN
bam-9798	72	15	on	on	ADP
bam-9798	72	16	high	high	ADJ
bam-9798	72	17	-	-	PUNCT
bam-9798	72	18	protein	protein	NOUN
bam-9798	72	19	diets	diet	NOUN
bam-9798	72	20	,	,	PUNCT
bam-9798	72	21	reported	report	VERB
bam-9798	72	22	that	that	SCONJ
bam-9798	72	23	only	only	ADV
bam-9798	72	24	25	25	NUM
bam-9798	72	25	%	%	NOUN
bam-9798	72	26	of	of	ADP
bam-9798	72	27	patients	patient	NOUN
bam-9798	72	28	showed	show	VERB
bam-9798	72	29	improvement	improvement	NOUN
bam-9798	72	30	in	in	ADP
bam-9798	72	31	muscle	muscle	NOUN
bam-9798	72	32	or	or	CCONJ
bam-9798	72	33	respiratory	respiratory	ADJ
bam-9798	72	34	function	function	NOUN
bam-9798	72	35	.	.	PUNCT
bam-9798	73	1	however	however	ADV
bam-9798	73	2	,	,	PUNCT
bam-9798	73	3	the	the	DET
bam-9798	73	4	compliance	compliance	NOUN
bam-9798	73	5	to	to	ADP
bam-9798	73	6	the	the	DET
bam-9798	73	7	diet	diet	NOUN
bam-9798	73	8	was	be	AUX
bam-9798	73	9	very	very	ADV
bam-9798	73	10	poor	poor	ADJ
bam-9798	73	11	.	.	PUNCT
bam-9798	74	1	the	the	DET
bam-9798	74	2	authors	author	NOUN
bam-9798	74	3	attributed	attribute	VERB
bam-9798	74	4	the	the	DET
bam-9798	74	5	problems	problem	NOUN
bam-9798	74	6	of	of	ADP
bam-9798	74	7	compliance	compliance	NOUN
bam-9798	74	8	to	to	ADP
bam-9798	74	9	the	the	DET
bam-9798	74	10	large	large	ADJ
bam-9798	74	11	amount	amount	NOUN
bam-9798	74	12	of	of	ADP
bam-9798	74	13	prescribed	prescribed	ADJ
bam-9798	74	14	proteins	protein	NOUN
bam-9798	74	15	and	and	CCONJ
bam-9798	74	16	to	to	ADP
bam-9798	74	17	the	the	DET
bam-9798	74	18	associated	associate	VERB
bam-9798	74	19	perceived	perceive	VERB
bam-9798	74	20	risk	risk	NOUN
bam-9798	74	21	of	of	ADP
bam-9798	74	22	weight	weight	NOUN
bam-9798	74	23	gain.12	gain.12	NOUN
bam-9798	74	24	the	the	DET
bam-9798	74	25	lopd	lopd	NOUN
bam-9798	74	26	patients	patient	NOUN
bam-9798	74	27	interviewed	interview	VERB
bam-9798	74	28	personalized	personalize	VERB
bam-9798	74	29	their	their	PRON
bam-9798	74	30	own	own	ADJ
bam-9798	74	31	diet	diet	NOUN
bam-9798	74	32	and	and	CCONJ
bam-9798	74	33	exercise	exercise	NOUN
bam-9798	74	34	regimen	regiman	NOUN
bam-9798	74	35	.	.	PUNCT
bam-9798	75	1	the	the	DET
bam-9798	75	2	lack	lack	NOUN
bam-9798	75	3	of	of	ADP
bam-9798	75	4	studies	study	NOUN
bam-9798	75	5	on	on	ADP
bam-9798	75	6	nutritional	nutritional	ADJ
bam-9798	75	7	interventions	intervention	NOUN
bam-9798	75	8	in	in	ADP
bam-9798	75	9	lopd	lopd	NOUN
bam-9798	75	10	patients	patient	NOUN
bam-9798	75	11	receiving	receive	VERB
bam-9798	75	12	chronic	chronic	ADJ
bam-9798	75	13	ert	ert	NOUN
bam-9798	75	14	was	be	AUX
bam-9798	75	15	only	only	ADV
bam-9798	75	16	recently	recently	ADV
bam-9798	75	17	partially	partially	ADV
bam-9798	75	18	filled	fill	VERB
bam-9798	75	19	by	by	ADP
bam-9798	75	20	a	a	DET
bam-9798	75	21	study	study	NOUN
bam-9798	75	22	in	in	ADP
bam-9798	75	23	11	11	NUM
bam-9798	75	24	patients	patient	NOUN
bam-9798	75	25	evaluating	evaluate	VERB
bam-9798	75	26	their	their	PRON
bam-9798	75	27	vo2	vo2	NOUN
bam-9798	75	28	max.14	max.14	PROPN
bam-9798	75	29	results	result	VERB
bam-9798	75	30	in	in	ADP
bam-9798	75	31	65	65	NUM
bam-9798	75	32	lopd	lopd	NOUN
bam-9798	75	33	cases	case	NOUN
bam-9798	75	34	,	,	PUNCT
bam-9798	75	35	followed	follow	VERB
bam-9798	75	36	by	by	ADP
bam-9798	75	37	the	the	DET
bam-9798	75	38	italian	italian	ADJ
bam-9798	75	39	group	group	NOUN
bam-9798	75	40	,	,	PUNCT
bam-9798	75	41	coordinated	coordinate	VERB
bam-9798	75	42	by	by	ADP
bam-9798	75	43	three	three	NUM
bam-9798	75	44	physicians	physician	NOUN
bam-9798	75	45	(	(	PUNCT
bam-9798	75	46	c.	c.	PROPN
bam-9798	75	47	angelini	angelini	PROPN
bam-9798	75	48	,	,	PUNCT
bam-9798	75	49	a.	a.	PROPN
bam-9798	75	50	toscano	toscano	PROPN
bam-9798	75	51	,	,	PUNCT
bam-9798	75	52	t.	t.	PROPN
bam-9798	75	53	mongini	mongini	PROPN
bam-9798	75	54	)	)	PUNCT
bam-9798	75	55	most	most	ADJ
bam-9798	75	56	of	of	ADP
bam-9798	75	57	the	the	DET
bam-9798	75	58	patients	patient	NOUN
bam-9798	75	59	gave	give	VERB
bam-9798	75	60	a	a	DET
bam-9798	75	61	positive	positive	ADJ
bam-9798	75	62	efficacy	efficacy	NOUN
bam-9798	75	63	evaluation	evaluation	NOUN
bam-9798	75	64	of	of	ADP
bam-9798	75	65	ert	ert	NOUN
bam-9798	75	66	and	and	CCONJ
bam-9798	75	67	they	they	PRON
bam-9798	75	68	were	be	AUX
bam-9798	75	69	classified	classify	VERB
bam-9798	75	70	by	by	ADP
bam-9798	75	71	the	the	DET
bam-9798	75	72	self	self	NOUN
bam-9798	75	73	-	-	PUNCT
bam-9798	75	74	administered	administer	VERB
bam-9798	75	75	scale	scale	NOUN
bam-9798	75	76	as	as	ADP
bam-9798	75	77	responders	responder	NOUN
bam-9798	75	78	(	(	PUNCT
bam-9798	75	79	r	r	NOUN
bam-9798	75	80	)	)	PUNCT
bam-9798	75	81	or	or	CCONJ
bam-9798	75	82	nonresponders	nonresponder	NOUN
bam-9798	75	83	(	(	PUNCT
bam-9798	75	84	n	n	CCONJ
bam-9798	75	85	)	)	PUNCT
bam-9798	75	86	.	.	PUNCT
bam-9798	76	1	of	of	ADP
bam-9798	76	2	the	the	DET
bam-9798	76	3	58	58	NUM
bam-9798	76	4	lopd	lopd	NOUN
bam-9798	76	5	patients	patient	NOUN
bam-9798	76	6	recruited	recruit	VERB
bam-9798	76	7	(	(	PUNCT
bam-9798	76	8	figure	figure	NOUN
bam-9798	76	9	3	3	NUM
bam-9798	76	10	)	)	PUNCT
bam-9798	76	11	,	,	PUNCT
bam-9798	76	12	the	the	DET
bam-9798	76	13	majority	majority	NOUN
bam-9798	76	14	(	(	PUNCT
bam-9798	76	15	35	35	NUM
bam-9798	76	16	patients	patient	NOUN
bam-9798	76	17	)	)	PUNCT
bam-9798	76	18	,	,	PUNCT
bam-9798	76	19	self	self	NOUN
bam-9798	76	20	-	-	PUNCT
bam-9798	76	21	reported	report	VERB
bam-9798	76	22	a	a	DET
bam-9798	76	23	positive	positive	ADJ
bam-9798	76	24	improvement	improvement	NOUN
bam-9798	76	25	in	in	ADP
bam-9798	76	26	their	their	PRON
bam-9798	76	27	function	function	NOUN
bam-9798	76	28	,	,	PUNCT
bam-9798	76	29	11	11	NUM
bam-9798	76	30	had	have	VERB
bam-9798	76	31	a	a	DET
bam-9798	76	32	two	two	NUM
bam-9798	76	33	grades	grade	NOUN
bam-9798	76	34	gain	gain	NOUN
bam-9798	76	35	of	of	ADP
bam-9798	76	36	function	function	NOUN
bam-9798	76	37	and	and	CCONJ
bam-9798	76	38	24	24	NUM
bam-9798	76	39	performed	perform	VERB
bam-9798	76	40	the	the	DET
bam-9798	76	41	same	same	ADJ
bam-9798	76	42	function	function	NOUN
bam-9798	76	43	more	more	ADV
bam-9798	76	44	easily	easily	ADV
bam-9798	76	45	(	(	PUNCT
bam-9798	76	46	such	such	ADJ
bam-9798	76	47	as	as	ADP
bam-9798	76	48	walking	walking	NOUN
bam-9798	76	49	,	,	PUNCT
bam-9798	76	50	gowers	gower	NOUN
bam-9798	76	51	’	'	PUNCT
bam-9798	76	52	maneuver	maneuver	NOUN
bam-9798	76	53	,	,	PUNCT
bam-9798	76	54	climbing	climb	VERB
bam-9798	76	55	stairs	stair	NOUN
bam-9798	76	56	)	)	PUNCT
bam-9798	76	57	.	.	PUNCT
bam-9798	77	1	18	18	NUM
bam-9798	77	2	patients	patient	NOUN
bam-9798	77	3	reported	report	VERB
bam-9798	77	4	no	no	DET
bam-9798	77	5	variation	variation	NOUN
bam-9798	77	6	in	in	ADP
bam-9798	77	7	their	their	PRON
bam-9798	77	8	motor	motor	NOUN
bam-9798	77	9	functions	function	NOUN
bam-9798	77	10	while	while	SCONJ
bam-9798	77	11	4	4	NUM
bam-9798	77	12	reported	report	VERB
bam-9798	77	13	less	less	ADJ
bam-9798	77	14	ability	ability	NOUN
bam-9798	77	15	in	in	ADP
bam-9798	77	16	their	their	PRON
bam-9798	77	17	functions	function	NOUN
bam-9798	77	18	and	and	CCONJ
bam-9798	77	19	only	only	ADV
bam-9798	77	20	one	one	NUM
bam-9798	77	21	reported	report	VERB
bam-9798	77	22	loss	loss	NOUN
bam-9798	77	23	of	of	ADP
bam-9798	77	24	function(s	function(s	PROPN
bam-9798	77	25	)	)	PUNCT
bam-9798	77	26	.	.	PUNCT
bam-9798	78	1	we	we	PRON
bam-9798	78	2	therefore	therefore	ADV
bam-9798	78	3	divided	divide	VERB
bam-9798	78	4	our	our	PRON
bam-9798	78	5	series	series	NOUN
bam-9798	78	6	in	in	ADP
bam-9798	78	7	35	35	NUM
bam-9798	78	8	r	r	NOUN
bam-9798	78	9	=	=	NOUN
bam-9798	78	10	responders	responder	NOUN
bam-9798	78	11	including	include	VERB
bam-9798	78	12	in	in	ADP
bam-9798	78	13	this	this	DET
bam-9798	78	14	category	category	NOUN
bam-9798	78	15	patients	patient	NOUN
bam-9798	78	16	that	that	PRON
bam-9798	78	17	were	be	AUX
bam-9798	78	18	stable	stable	ADJ
bam-9798	78	19	while	while	SCONJ
bam-9798	78	20	23	23	NUM
bam-9798	78	21	were	be	AUX
bam-9798	78	22	classified	classify	VERB
bam-9798	78	23	in	in	ADP
bam-9798	78	24	the	the	DET
bam-9798	78	25	non	non	ADJ
bam-9798	78	26	-	-	NOUN
bam-9798	78	27	responder	responder	ADJ
bam-9798	78	28	=	=	SYM
bam-9798	78	29	n	n	PRON
bam-9798	78	30	category	category	NOUN
bam-9798	78	31	.	.	PUNCT
bam-9798	79	1	we	we	PRON
bam-9798	79	2	studied	study	VERB
bam-9798	79	3	in	in	ADP
bam-9798	79	4	responders	responder	NOUN
bam-9798	79	5	and	and	CCONJ
bam-9798	79	6	non	non	NOUN
bam-9798	79	7	-	-	NOUN
bam-9798	79	8	responders	responder	NOUN
bam-9798	79	9	average	average	ADJ
bam-9798	79	10	and	and	CCONJ
bam-9798	79	11	standard	standard	ADJ
bam-9798	79	12	deviation	deviation	NOUN
bam-9798	79	13	,	,	PUNCT
bam-9798	79	14	clinical	clinical	ADJ
bam-9798	79	15	efficacy	efficacy	NOUN
bam-9798	79	16	by	by	ADP
bam-9798	79	17	nonparametric	nonparametric	PROPN
bam-9798	79	18	mann	mann	PROPN
bam-9798	79	19	-	-	PUNCT
bam-9798	79	20	whitney	whitney	PROPN
bam-9798	79	21	test	test	NOUN
bam-9798	79	22	making	make	VERB
bam-9798	79	23	comparisons	comparison	NOUN
bam-9798	79	24	to	to	ADP
bam-9798	79	25	the	the	DET
bam-9798	79	26	following	following	ADJ
bam-9798	79	27	variables	variable	NOUN
bam-9798	79	28	:	:	PUNCT
bam-9798	79	29	age	age	NOUN
bam-9798	79	30	at	at	ADP
bam-9798	79	31	onset	onset	NOUN
bam-9798	79	32	of	of	ADP
bam-9798	79	33	ert	ert	PROPN
bam-9798	79	34	,	,	PUNCT
bam-9798	79	35	the	the	DET
bam-9798	79	36	initial	initial	ADJ
bam-9798	79	37	gardner	gardner	NOUN
bam-9798	79	38	-	-	PUNCT
bam-9798	79	39	medwin	medwin	PROPN
bam-9798	79	40	-	-	PUNCT
bam-9798	79	41	walton	walton	PROPN
bam-9798	79	42	grade	grade	NOUN
bam-9798	79	43	,	,	PUNCT
bam-9798	79	44	bmi	bmi	NOUN
bam-9798	79	45	,	,	PUNCT
bam-9798	79	46	duration	duration	NOUN
bam-9798	79	47	of	of	ADP
bam-9798	79	48	ert	ert	ADJ
bam-9798	79	49	treatment	treatment	NOUN
bam-9798	79	50	that	that	PRON
bam-9798	79	51	resulted	result	VERB
bam-9798	79	52	not	not	PART
bam-9798	79	53	significant	significant	ADJ
bam-9798	79	54	.	.	PUNCT
bam-9798	80	1	this	this	PRON
bam-9798	80	2	was	be	AUX
bam-9798	80	3	analyzed	analyze	VERB
bam-9798	80	4	for	for	ADP
bam-9798	80	5	each	each	DET
bam-9798	80	6	variable	variable	NOUN
bam-9798	80	7	but	but	CCONJ
bam-9798	80	8	the	the	DET
bam-9798	80	9	only	only	ADJ
bam-9798	80	10	significant	significant	ADJ
bam-9798	80	11	parameter	parameter	NOUN
bam-9798	80	12	was	be	AUX
bam-9798	80	13	a	a	DET
bam-9798	80	14	better	well	ADJ
bam-9798	80	15	performance	performance	NOUN
bam-9798	80	16	in	in	ADP
bam-9798	80	17	meter	meter	NOUN
bam-9798	80	18	length	length	NOUN
bam-9798	80	19	walked	walk	VERB
bam-9798	80	20	in	in	ADP
bam-9798	80	21	6mwt	6mwt	NUM
bam-9798	80	22	at	at	ADP
bam-9798	80	23	fig	fig	NOUN
bam-9798	80	24	2	2	NUM
bam-9798	80	25	.	.	PUNCT
bam-9798	80	26	patient	patient	ADJ
bam-9798	80	27	self	self	NOUN
bam-9798	80	28	-	-	PUNCT
bam-9798	80	29	administered	administer	VERB
bam-9798	80	30	questionnaire	questionnaire	NOUN
bam-9798	80	31	to	to	PART
bam-9798	80	32	evaluate	evaluate	VERB
bam-9798	80	33	ert	ert	NOUN
bam-9798	80	34	efficacy	efficacy	NOUN
bam-9798	80	35	fig	fig	NOUN
bam-9798	80	36	.	.	PUNCT
bam-9798	81	1	3.results	3.results	NUM
bam-9798	81	2	in	in	ADP
bam-9798	81	3	58	58	NUM
bam-9798	81	4	lopd	lopd	NOUN
bam-9798	81	5	of	of	ADP
bam-9798	81	6	ert	ert	PROPN
bam-9798	81	7	efficacy	efficacy	NOUN
bam-9798	81	8	evaluation	evaluation	NOUN
bam-9798	81	9	exercise	exercise	NOUN
bam-9798	81	10	and	and	CCONJ
bam-9798	81	11	nutrition	nutrition	NOUN
bam-9798	81	12	in	in	ADP
bam-9798	81	13	late	late	ADJ
bam-9798	81	14	onset	onset	ADJ
bam-9798	81	15	pompe	pompe	PROPN
bam-9798	81	16	disease	disease	PROPN
bam-9798	81	17	eur	eur	PROPN
bam-9798	81	18	j	j	PROPN
bam-9798	81	19	transl	transl	PROPN
bam-9798	81	20	myol	myol	ADV
bam-9798	81	21	31	31	NUM
bam-9798	81	22	(	(	PUNCT
bam-9798	81	23	2	2	NUM
bam-9798	81	24	):	):	PUNCT
bam-9798	81	25	9798	9798	NUM
bam-9798	81	26	,	,	PUNCT
bam-9798	81	27	2021	2021	NUM
bam-9798	81	28	doi	doi	NOUN
bam-9798	81	29	:	:	PUNCT
bam-9798	81	30	10.4081	10.4081	NUM
bam-9798	81	31	/	/	SYM
bam-9798	81	32	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	81	33	5	5	NUM
bam-9798	81	34	onset	onset	NOUN
bam-9798	81	35	before	before	ADP
bam-9798	81	36	ert	ert	X
bam-9798	81	37	i.e.	i.e.	X
bam-9798	81	38	344	344	NUM
bam-9798	81	39	meters	meter	NOUN
bam-9798	81	40	in	in	ADP
bam-9798	81	41	responders	responder	NOUN
bam-9798	81	42	versus	versus	ADP
bam-9798	81	43	238	238	NUM
bam-9798	81	44	meters	meter	NOUN
bam-9798	81	45	in	in	ADP
bam-9798	81	46	non	non	NOUN
bam-9798	81	47	-	-	NOUN
bam-9798	81	48	responders	responder	NOUN
bam-9798	81	49	(	(	PUNCT
bam-9798	81	50	p<0.035	p<0.035	NOUN
bam-9798	81	51	)	)	PUNCT
bam-9798	81	52	(	(	PUNCT
bam-9798	81	53	table	table	NOUN
bam-9798	81	54	1	1	NUM
bam-9798	81	55	)	)	PUNCT
bam-9798	81	56	.	.	PUNCT
bam-9798	82	1	by	by	ADP
bam-9798	82	2	the	the	DET
bam-9798	82	3	self	self	NOUN
bam-9798	82	4	-	-	PUNCT
bam-9798	82	5	evaluation	evaluation	NOUN
bam-9798	82	6	questionnaire	questionnaire	NOUN
bam-9798	82	7	the	the	DET
bam-9798	82	8	patients	patient	NOUN
bam-9798	82	9	that	that	PRON
bam-9798	82	10	gave	give	VERB
bam-9798	82	11	a	a	DET
bam-9798	82	12	positive	positive	ADJ
bam-9798	82	13	efficacy	efficacy	NOUN
bam-9798	82	14	evaluation	evaluation	NOUN
bam-9798	82	15	of	of	ADP
bam-9798	82	16	ert	ert	NOUN
bam-9798	82	17	were	be	AUX
bam-9798	82	18	35	35	NUM
bam-9798	82	19	cases	case	NOUN
bam-9798	82	20	,	,	PUNCT
bam-9798	82	21	while	while	SCONJ
bam-9798	82	22	18	18	NUM
bam-9798	82	23	reported	report	VERB
bam-9798	82	24	stable	stable	ADJ
bam-9798	82	25	conditions	condition	NOUN
bam-9798	82	26	,	,	PUNCT
bam-9798	82	27	they	they	PRON
bam-9798	82	28	were	be	AUX
bam-9798	82	29	classified	classify	VERB
bam-9798	82	30	by	by	ADP
bam-9798	82	31	the	the	DET
bam-9798	82	32	self	self	NOUN
bam-9798	82	33	-	-	PUNCT
bam-9798	82	34	administered	administer	VERB
bam-9798	82	35	scale	scale	NOUN
bam-9798	82	36	in	in	ADP
bam-9798	82	37	non	non	NOUN
bam-9798	82	38	-	-	NOUN
bam-9798	82	39	responders	responder	NOUN
bam-9798	82	40	(	(	PUNCT
bam-9798	82	41	n	n	CCONJ
bam-9798	82	42	)	)	PUNCT
bam-9798	82	43	,	,	PUNCT
bam-9798	82	44	the	the	DET
bam-9798	82	45	gender	gender	NOUN
bam-9798	82	46	in	in	ADP
bam-9798	82	47	these	these	DET
bam-9798	82	48	groups	group	NOUN
bam-9798	82	49	was	be	AUX
bam-9798	82	50	equally	equally	ADV
bam-9798	82	51	represented	represent	VERB
bam-9798	82	52	.	.	PUNCT
bam-9798	83	1	then	then	ADV
bam-9798	83	2	supportive	supportive	ADJ
bam-9798	83	3	therapies	therapy	NOUN
bam-9798	83	4	were	be	AUX
bam-9798	83	5	further	far	ADV
bam-9798	83	6	studied	study	VERB
bam-9798	83	7	by	by	ADP
bam-9798	83	8	the	the	DET
bam-9798	83	9	pearson	pearson	PROPN
bam-9798	83	10	’s	’s	PART
bam-9798	83	11	chi	chi	ADJ
bam-9798	83	12	-	-	PUNCT
bam-9798	83	13	squared	square	VERB
bam-9798	83	14	test	test	NOUN
bam-9798	83	15	that	that	PRON
bam-9798	83	16	showed	show	VERB
bam-9798	83	17	that	that	SCONJ
bam-9798	83	18	a	a	DET
bam-9798	83	19	clinical	clinical	ADJ
bam-9798	83	20	parameter	parameter	NOUN
bam-9798	83	21	significantly	significantly	ADV
bam-9798	83	22	associated	associate	VERB
bam-9798	83	23	with	with	ADP
bam-9798	83	24	a	a	DET
bam-9798	83	25	responder	responder	NOUN
bam-9798	83	26	category	category	NOUN
bam-9798	83	27	was	be	AUX
bam-9798	83	28	the	the	DET
bam-9798	83	29	use	use	NOUN
bam-9798	83	30	of	of	ADP
bam-9798	83	31	supportive	supportive	ADJ
bam-9798	83	32	therapies	therapy	NOUN
bam-9798	83	33	such	such	ADJ
bam-9798	83	34	as	as	ADP
bam-9798	83	35	regular	regular	ADJ
bam-9798	83	36	diet	diet	NOUN
bam-9798	83	37	or	or	CCONJ
bam-9798	83	38	exercise	exercise	NOUN
bam-9798	83	39	or	or	CCONJ
bam-9798	83	40	both	both	PRON
bam-9798	83	41	.	.	PUNCT
bam-9798	84	1	of	of	ADP
bam-9798	84	2	patients	patient	NOUN
bam-9798	84	3	following	follow	VERB
bam-9798	84	4	both	both	CCONJ
bam-9798	84	5	diet	diet	NOUN
bam-9798	84	6	and	and	CCONJ
bam-9798	84	7	exercise	exercise	VERB
bam-9798	84	8	47	47	NUM
bam-9798	84	9	%	%	NOUN
bam-9798	84	10	were	be	AUX
bam-9798	84	11	in	in	ADP
bam-9798	84	12	r	r	NOUN
bam-9798	84	13	category	category	NOUN
bam-9798	84	14	.	.	PUNCT
bam-9798	85	1	those	those	PRON
bam-9798	85	2	following	follow	VERB
bam-9798	85	3	only	only	ADV
bam-9798	85	4	either	either	CCONJ
bam-9798	85	5	regular	regular	ADJ
bam-9798	85	6	diet	diet	NOUN
bam-9798	85	7	or	or	CCONJ
bam-9798	85	8	exercise	exercise	NOUN
bam-9798	85	9	in	in	ADP
bam-9798	85	10	53	53	NUM
bam-9798	85	11	%	%	NOUN
bam-9798	85	12	resulted	result	VERB
bam-9798	85	13	in	in	ADP
bam-9798	85	14	the	the	DET
bam-9798	85	15	r	r	NOUN
bam-9798	85	16	category	category	NOUN
bam-9798	85	17	(	(	PUNCT
bam-9798	85	18	p	p	X
bam-9798	85	19	<	<	X
bam-9798	85	20	0.029	0.029	NUM
bam-9798	85	21	)	)	PUNCT
bam-9798	85	22	.	.	PUNCT
bam-9798	86	1	discussion	discussion	NOUN
bam-9798	86	2	ert	ert	NOUN
bam-9798	86	3	has	have	AUX
bam-9798	86	4	been	be	AUX
bam-9798	86	5	studied	study	VERB
bam-9798	86	6	in	in	ADP
bam-9798	86	7	numerous	numerous	ADJ
bam-9798	86	8	european	european	ADJ
bam-9798	86	9	series	series	NOUN
bam-9798	86	10	of	of	ADP
bam-9798	86	11	patients.5,15	patients.5,15	ADP
bam-9798	86	12	to	to	PART
bam-9798	86	13	allow	allow	VERB
bam-9798	86	14	to	to	PART
bam-9798	86	15	better	well	ADV
bam-9798	86	16	monitor	monitor	VERB
bam-9798	86	17	ert	ert	VERB
bam-9798	86	18	a	a	DET
bam-9798	86	19	choice	choice	NOUN
bam-9798	86	20	of	of	ADP
bam-9798	86	21	responder	responder	NOUN
bam-9798	86	22	patients	patient	NOUN
bam-9798	86	23	would	would	AUX
bam-9798	86	24	be	be	AUX
bam-9798	86	25	required	require	VERB
bam-9798	86	26	,	,	PUNCT
bam-9798	86	27	this	this	PRON
bam-9798	86	28	was	be	AUX
bam-9798	86	29	the	the	DET
bam-9798	86	30	main	main	ADJ
bam-9798	86	31	result	result	NOUN
bam-9798	86	32	in	in	ADP
bam-9798	86	33	our	our	PRON
bam-9798	86	34	study	study	NOUN
bam-9798	86	35	,	,	PUNCT
bam-9798	86	36	in	in	ADP
bam-9798	86	37	order	order	NOUN
bam-9798	86	38	to	to	PART
bam-9798	86	39	further	far	ADV
bam-9798	86	40	analyze	analyze	VERB
bam-9798	86	41	the	the	DET
bam-9798	86	42	effects	effect	NOUN
bam-9798	86	43	of	of	ADP
bam-9798	86	44	treatment	treatment	NOUN
bam-9798	86	45	and	and	CCONJ
bam-9798	86	46	prognostic	prognostic	ADJ
bam-9798	86	47	factors	factor	NOUN
bam-9798	86	48	,	,	PUNCT
bam-9798	86	49	it	it	PRON
bam-9798	86	50	is	be	AUX
bam-9798	86	51	important	important	ADJ
bam-9798	86	52	to	to	PART
bam-9798	86	53	collect	collect	VERB
bam-9798	86	54	information	information	NOUN
bam-9798	86	55	on	on	ADP
bam-9798	86	56	treatment	treatment	NOUN
bam-9798	86	57	(	(	PUNCT
bam-9798	86	58	has	have	AUX
bam-9798	86	59	the	the	DET
bam-9798	86	60	patient	patient	NOUN
bam-9798	86	61	regularly	regularly	ADV
bam-9798	86	62	received	receive	VERB
bam-9798	86	63	medication	medication	NOUN
bam-9798	86	64	for	for	ADP
bam-9798	86	65	pompe	pompe	PROPN
bam-9798	86	66	disease	disease	NOUN
bam-9798	86	67	,	,	PUNCT
bam-9798	86	68	and	and	CCONJ
bam-9798	86	69	if	if	SCONJ
bam-9798	86	70	so	so	ADV
bam-9798	86	71	,	,	PUNCT
bam-9798	86	72	which	which	DET
bam-9798	86	73	treatment	treatment	NOUN
bam-9798	86	74	and	and	CCONJ
bam-9798	86	75	since	since	SCONJ
bam-9798	86	76	/	/	SYM
bam-9798	86	77	until	until	ADP
bam-9798	86	78	when	when	SCONJ
bam-9798	86	79	)	)	PUNCT
bam-9798	86	80	as	as	ADV
bam-9798	86	81	well	well	ADV
bam-9798	86	82	as	as	ADP
bam-9798	86	83	the	the	DET
bam-9798	86	84	concomitant	concomitant	ADJ
bam-9798	86	85	follow	follow	NOUN
bam-9798	86	86	-	-	PUNCT
bam-9798	86	87	up	up	NOUN
bam-9798	86	88	for	for	ADP
bam-9798	86	89	regular	regular	ADJ
bam-9798	86	90	exercise	exercise	NOUN
bam-9798	86	91	and	and	CCONJ
bam-9798	86	92	nutrition	nutrition	NOUN
bam-9798	86	93	status	status	NOUN
bam-9798	86	94	(	(	PUNCT
bam-9798	86	95	including	include	VERB
bam-9798	86	96	daily	daily	ADJ
bam-9798	86	97	diet	diet	NOUN
bam-9798	86	98	and	and	CCONJ
bam-9798	86	99	type	type	NOUN
bam-9798	86	100	of	of	ADP
bam-9798	86	101	diet	diet	NOUN
bam-9798	86	102	)	)	PUNCT
bam-9798	86	103	that	that	PRON
bam-9798	86	104	might	might	AUX
bam-9798	86	105	result	result	VERB
bam-9798	86	106	in	in	ADP
bam-9798	86	107	a	a	DET
bam-9798	86	108	positive	positive	ADJ
bam-9798	86	109	recommendation	recommendation	NOUN
bam-9798	86	110	for	for	ADP
bam-9798	86	111	these	these	DET
bam-9798	86	112	supportive	supportive	ADJ
bam-9798	86	113	therapy	therapy	NOUN
bam-9798	86	114	in	in	ADP
bam-9798	86	115	patients	patient	NOUN
bam-9798	86	116	with	with	ADP
bam-9798	86	117	a	a	DET
bam-9798	86	118	confirmed	confirm	VERB
bam-9798	86	119	diagnosis	diagnosis	NOUN
bam-9798	86	120	.	.	PUNCT
bam-9798	87	1	similarly	similarly	ADV
bam-9798	87	2	,	,	PUNCT
bam-9798	87	3	the	the	DET
bam-9798	87	4	european	european	PROPN
bam-9798	87	5	pompe	pompe	PROPN
bam-9798	87	6	consortium	consortium	PROPN
bam-9798	87	7	recommends	recommend	VERB
bam-9798	87	8	initiating	initiate	VERB
bam-9798	87	9	ert	ert	NOUN
bam-9798	87	10	in	in	ADP
bam-9798	87	11	symptomatic	symptomatic	ADJ
bam-9798	87	12	patients	patient	NOUN
bam-9798	87	13	who	who	PRON
bam-9798	87	14	agree	agree	VERB
bam-9798	87	15	to	to	ADP
bam-9798	87	16	regular	regular	ADJ
bam-9798	87	17	treatment	treatment	NOUN
bam-9798	87	18	and	and	CCONJ
bam-9798	87	19	monitoring	monitoring	NOUN
bam-9798	87	20	,	,	PUNCT
bam-9798	87	21	have	have	VERB
bam-9798	87	22	residual	residual	ADJ
bam-9798	87	23	skeletal	skeletal	ADJ
bam-9798	87	24	and	and	CCONJ
bam-9798	87	25	respiratory	respiratory	ADJ
bam-9798	87	26	muscle	muscle	NOUN
bam-9798	87	27	function	function	NOUN
bam-9798	87	28	,	,	PUNCT
bam-9798	87	29	and	and	CCONJ
bam-9798	87	30	do	do	AUX
bam-9798	87	31	not	not	PART
bam-9798	87	32	have	have	VERB
bam-9798	87	33	another	another	DET
bam-9798	87	34	lifethreatening	lifethreatene	VERB
bam-9798	87	35	illness	illness	NOUN
bam-9798	87	36	in	in	ADP
bam-9798	87	37	an	an	DET
bam-9798	87	38	advanced	advanced	ADJ
bam-9798	87	39	stage.11	stage.11	NOUN
bam-9798	87	40	however	however	ADV
bam-9798	87	41	,	,	PUNCT
bam-9798	87	42	to	to	PART
bam-9798	87	43	better	well	ADV
bam-9798	87	44	identify	identify	VERB
bam-9798	87	45	the	the	DET
bam-9798	87	46	predictors	predictor	NOUN
bam-9798	87	47	of	of	ADP
bam-9798	87	48	the	the	DET
bam-9798	87	49	therapeutic	therapeutic	ADJ
bam-9798	87	50	response	response	NOUN
bam-9798	87	51	,	,	PUNCT
bam-9798	87	52	it	it	PRON
bam-9798	87	53	is	be	AUX
bam-9798	87	54	crucial	crucial	ADJ
bam-9798	87	55	to	to	PART
bam-9798	87	56	continue	continue	VERB
bam-9798	87	57	to	to	PART
bam-9798	87	58	collect	collect	VERB
bam-9798	87	59	data	datum	NOUN
bam-9798	87	60	on	on	ADP
bam-9798	87	61	cohorts	cohort	NOUN
bam-9798	87	62	of	of	ADP
bam-9798	87	63	patients	patient	NOUN
bam-9798	87	64	with	with	ADP
bam-9798	87	65	lopd	lopd	NOUN
bam-9798	87	66	.	.	PUNCT
bam-9798	88	1	in	in	ADP
bam-9798	88	2	lopd	lopd	NOUN
bam-9798	88	3	patients	patient	NOUN
bam-9798	88	4	receiving	receive	VERB
bam-9798	88	5	chronic	chronic	NOUN
bam-9798	88	6	care	care	VERB
bam-9798	88	7	a	a	DET
bam-9798	88	8	protein	protein	NOUN
bam-9798	88	9	rich	rich	ADJ
bam-9798	88	10	diet	diet	NOUN
bam-9798	88	11	or	or	CCONJ
bam-9798	88	12	exercise	exercise	NOUN
bam-9798	88	13	was	be	AUX
bam-9798	88	14	tried	try	VERB
bam-9798	88	15	by	by	ADP
bam-9798	88	16	slonim	slonim	PROPN
bam-9798	88	17	et	et	PROPN
bam-9798	88	18	al.12	al.12	PROPN
bam-9798	88	19	but	but	CCONJ
bam-9798	88	20	it	it	PRON
bam-9798	88	21	could	could	AUX
bam-9798	88	22	be	be	AUX
bam-9798	88	23	linked	link	VERB
bam-9798	88	24	to	to	ADP
bam-9798	88	25	limited	limited	ADJ
bam-9798	88	26	results	result	NOUN
bam-9798	88	27	because	because	SCONJ
bam-9798	88	28	of	of	ADP
bam-9798	88	29	the	the	DET
bam-9798	88	30	difficulty	difficulty	NOUN
bam-9798	88	31	of	of	ADP
bam-9798	88	32	guaranteeing	guarantee	VERB
bam-9798	88	33	compliance	compliance	NOUN
bam-9798	88	34	to	to	ADP
bam-9798	88	35	high	high	ADJ
bam-9798	88	36	-	-	PUNCT
bam-9798	88	37	protein	protein	NOUN
bam-9798	88	38	diets	diet	NOUN
bam-9798	88	39	,	,	PUNCT
bam-9798	88	40	as	as	ADP
bam-9798	88	41	a	a	DET
bam-9798	88	42	consequence	consequence	NOUN
bam-9798	88	43	of	of	ADP
bam-9798	88	44	the	the	DET
bam-9798	88	45	lower	low	ADJ
bam-9798	88	46	palatability	palatability	NOUN
bam-9798	88	47	of	of	ADP
bam-9798	88	48	many	many	ADJ
bam-9798	88	49	high	high	ADJ
bam-9798	88	50	-	-	PUNCT
bam-9798	88	51	protein	protein	NOUN
bam-9798	88	52	foods	food	NOUN
bam-9798	88	53	compared	compare	VERB
bam-9798	88	54	to	to	ADP
bam-9798	88	55	those	those	PRON
bam-9798	88	56	with	with	ADP
bam-9798	88	57	high	high	ADJ
bam-9798	88	58	carbohydrate	carbohydrate	NOUN
bam-9798	88	59	content	content	NOUN
bam-9798	88	60	,	,	PUNCT
bam-9798	88	61	or	or	CCONJ
bam-9798	88	62	of	of	ADP
bam-9798	88	63	the	the	DET
bam-9798	88	64	higher	high	ADJ
bam-9798	88	65	satiety	satiety	NOUN
bam-9798	88	66	power	power	NOUN
bam-9798	88	67	of	of	ADP
bam-9798	88	68	proteins	protein	NOUN
bam-9798	88	69	,	,	PUNCT
bam-9798	88	70	which	which	PRON
bam-9798	88	71	may	may	AUX
bam-9798	88	72	lead	lead	VERB
bam-9798	88	73	to	to	ADP
bam-9798	88	74	a	a	DET
bam-9798	88	75	reduction	reduction	NOUN
bam-9798	88	76	in	in	ADP
bam-9798	88	77	food	food	NOUN
bam-9798	88	78	.	.	PUNCT
bam-9798	89	1	the	the	DET
bam-9798	89	2	slonim	slonim	PROPN
bam-9798	89	3	study	study	NOUN
bam-9798	89	4	published	publish	VERB
bam-9798	89	5	in	in	ADP
bam-9798	89	6	the	the	DET
bam-9798	89	7	pre	pre	ADJ
bam-9798	89	8	-	-	ADJ
bam-9798	89	9	ert	ert	ADJ
bam-9798	89	10	era	era	NOUN
bam-9798	89	11	,	,	PUNCT
bam-9798	89	12	dealing	deal	VERB
bam-9798	89	13	with	with	ADP
bam-9798	89	14	lopd	lopd	NOUN
bam-9798	89	15	patients	patient	NOUN
bam-9798	89	16	on	on	ADP
bam-9798	89	17	high	high	ADJ
bam-9798	89	18	-	-	PUNCT
bam-9798	89	19	protein	protein	NOUN
bam-9798	89	20	diets	diet	NOUN
bam-9798	89	21	,	,	PUNCT
bam-9798	89	22	reported	report	VERB
bam-9798	89	23	that	that	SCONJ
bam-9798	89	24	only	only	ADV
bam-9798	89	25	25	25	NUM
bam-9798	89	26	%	%	NOUN
bam-9798	89	27	of	of	ADP
bam-9798	89	28	patients	patient	NOUN
bam-9798	89	29	showed	show	VERB
bam-9798	89	30	improvement	improvement	NOUN
bam-9798	89	31	in	in	ADP
bam-9798	89	32	muscle	muscle	NOUN
bam-9798	89	33	or	or	CCONJ
bam-9798	89	34	respiratory	respiratory	ADJ
bam-9798	89	35	function	function	NOUN
bam-9798	89	36	.	.	PUNCT
bam-9798	90	1	there	there	PRON
bam-9798	90	2	is	be	VERB
bam-9798	90	3	only	only	ADV
bam-9798	90	4	one	one	NUM
bam-9798	90	5	study	study	NOUN
bam-9798	90	6	on	on	ADP
bam-9798	90	7	nutritional	nutritional	ADJ
bam-9798	90	8	interventions	intervention	NOUN
bam-9798	90	9	in	in	ADP
bam-9798	90	10	lopd	lopd	NOUN
bam-9798	90	11	patients	patient	NOUN
bam-9798	90	12	receiving	receive	VERB
bam-9798	90	13	chronic	chronic	ADJ
bam-9798	90	14	ert.14	ert.14	NOUN
bam-9798	90	15	the	the	DET
bam-9798	90	16	current	current	ADJ
bam-9798	90	17	standard	standard	NOUN
bam-9798	90	18	of	of	ADP
bam-9798	90	19	care	care	NOUN
bam-9798	90	20	for	for	ADP
bam-9798	90	21	pompe	pompe	PROPN
bam-9798	90	22	table	table	NOUN
bam-9798	90	23	1	1	NUM
bam-9798	90	24	.	.	PUNCT
bam-9798	90	25	parameters	parameter	NOUN
bam-9798	90	26	of	of	ADP
bam-9798	90	27	clinical	clinical	ADJ
bam-9798	90	28	efficacy	efficacy	NOUN
bam-9798	90	29	in	in	ADP
bam-9798	90	30	non	non	NOUN
bam-9798	90	31	-	-	NOUN
bam-9798	90	32	responders	responder	NOUN
bam-9798	90	33	(	(	PUNCT
bam-9798	90	34	n	n	CCONJ
bam-9798	90	35	)	)	PUNCT
bam-9798	90	36	and	and	CCONJ
bam-9798	90	37	responders	responder	NOUN
bam-9798	90	38	(	(	PUNCT
bam-9798	90	39	r	r	NOUN
bam-9798	90	40	)	)	PUNCT
bam-9798	90	41	patients	patient	NOUN
bam-9798	90	42	average	average	ADJ
bam-9798	90	43	patient	patient	ADJ
bam-9798	90	44	number	number	NOUN
bam-9798	90	45	sd	sd	ADP
bam-9798	90	46	p	p	PROPN
bam-9798	90	47	mannwhitney	mannwhitney	NOUN
bam-9798	90	48	n	n	CCONJ
bam-9798	90	49	r	r	NOUN
bam-9798	90	50	n	n	ADP
bam-9798	90	51	r	r	NOUN
bam-9798	90	52	n	n	CCONJ
bam-9798	90	53	r	r	NOUN
bam-9798	90	54	age	age	NOUN
bam-9798	90	55	(	(	PUNCT
bam-9798	90	56	yrs	yr	NOUN
bam-9798	90	57	)	)	PUNCT
bam-9798	90	58	46.04	46.04	NUM
bam-9798	90	59	45.11	45.11	NUM
bam-9798	90	60	25	25	NUM
bam-9798	90	61	36	36	NUM
bam-9798	90	62	10.81	10.81	NUM
bam-9798	90	63	13.56	13.56	NUM
bam-9798	90	64	n.s	n.s	PROPN
bam-9798	90	65	.	.	PROPN
bam-9798	90	66	disease	disease	PROPN
bam-9798	90	67	duration	duration	NOUN
bam-9798	90	68	(	(	PUNCT
bam-9798	90	69	yrs	yr	NOUN
bam-9798	90	70	)	)	PUNCT
bam-9798	90	71	at	at	ADP
bam-9798	90	72	t0	t0	PROPN
bam-9798	90	73	17.20	17.20	NUM
bam-9798	90	74	14.42	14.42	NUM
bam-9798	90	75	25	25	NUM
bam-9798	90	76	36	36	NUM
bam-9798	90	77	9.57	9.57	NUM
bam-9798	90	78	9.10	9.10	NUM
bam-9798	90	79	n.s	n.s	PROPN
bam-9798	90	80	.	.	PROPN
bam-9798	90	81	bmi	bmi	PROPN
bam-9798	90	82	at	at	ADP
bam-9798	90	83	t0	t0	PROPN
bam-9798	90	84	25.11	25.11	NUM
bam-9798	90	85	22.70	22.70	NUM
bam-9798	90	86	13	13	NUM
bam-9798	90	87	22	22	NUM
bam-9798	90	88	5.97	5.97	NUM
bam-9798	90	89	5.37	5.37	NUM
bam-9798	90	90	n.s	n.s	PROPN
bam-9798	90	91	.	.	PROPN
bam-9798	90	92	gmw	gmw	PROPN
bam-9798	90	93	at	at	ADP
bam-9798	90	94	t0	t0	PROPN
bam-9798	90	95	3.91	3.91	NUM
bam-9798	90	96	3.22	3.22	NUM
bam-9798	90	97	22	22	NUM
bam-9798	90	98	23	23	NUM
bam-9798	90	99	2.47	2.47	NUM
bam-9798	90	100	1.98	1.98	NUM
bam-9798	90	101	n.s	n.s	PROPN
bam-9798	90	102	.	.	PROPN
bam-9798	90	103	6	6	NUM
bam-9798	90	104	mwt	mwt	VERB
bam-9798	90	105	at	at	ADP
bam-9798	90	106	t0	t0	PROPN
bam-9798	90	107	238.27	238.27	NUM
bam-9798	90	108	344.40	344.40	NUM
bam-9798	90	109	15	15	NUM
bam-9798	90	110	25	25	NUM
bam-9798	90	111	159.40	159.40	NUM
bam-9798	90	112	112.10	112.10	NUM
bam-9798	90	113	0.035	0.035	NUM
bam-9798	90	114	fvc	fvc	NOUN
bam-9798	90	115	at	at	ADP
bam-9798	90	116	t0	t0	PROPN
bam-9798	90	117	60.36	60.36	NUM
bam-9798	90	118	67.80	67.80	NUM
bam-9798	90	119	23	23	NUM
bam-9798	90	120	33	33	NUM
bam-9798	90	121	28.30	28.30	NUM
bam-9798	90	122	19.83	19.83	NUM
bam-9798	90	123	n.s	n.s	PROPN
bam-9798	90	124	.	.	PROPN
bam-9798	90	125	gender	gender	PROPN
bam-9798	90	126	patient	patient	ADJ
bam-9798	90	127	number	number	NOUN
bam-9798	90	128	(	(	PUNCT
bam-9798	90	129	%	%	INTJ
bam-9798	90	130	)	)	PUNCT
bam-9798	90	131	pearson	pearson	PROPN
bam-9798	90	132	chi	chi	PROPN
bam-9798	90	133	square	square	PROPN
bam-9798	90	134	n	n	CCONJ
bam-9798	90	135	r	r	NOUN
bam-9798	90	136	m	m	VERB
bam-9798	90	137	13	13	NUM
bam-9798	90	138	(	(	PUNCT
bam-9798	90	139	52	52	NUM
bam-9798	90	140	%	%	NOUN
bam-9798	90	141	)	)	PUNCT
bam-9798	90	142	12	12	NUM
bam-9798	90	143	(	(	PUNCT
bam-9798	90	144	34	34	NUM
bam-9798	90	145	%	%	NOUN
bam-9798	90	146	)	)	PUNCT
bam-9798	91	1	n.s	n.s	PROPN
bam-9798	91	2	.	.	PROPN
bam-9798	91	3	f	f	PROPN
bam-9798	91	4	12	12	NUM
bam-9798	91	5	(	(	PUNCT
bam-9798	91	6	48	48	NUM
bam-9798	91	7	%	%	NOUN
bam-9798	91	8	)	)	PUNCT
bam-9798	91	9	23	23	NUM
bam-9798	91	10	(	(	PUNCT
bam-9798	91	11	66	66	NUM
bam-9798	91	12	%	%	NOUN
bam-9798	91	13	)	)	PUNCT
bam-9798	92	1	n.s	n.s	PROPN
bam-9798	92	2	.	.	PROPN
bam-9798	92	3	supportive	supportive	ADJ
bam-9798	92	4	therapies	therapy	NOUN
bam-9798	92	5	patient	patient	ADJ
bam-9798	92	6	number	number	NOUN
bam-9798	92	7	(	(	PUNCT
bam-9798	92	8	%	%	INTJ
bam-9798	92	9	)	)	PUNCT
bam-9798	92	10	pearson	pearson	PROPN
bam-9798	92	11	chi	chi	PROPN
bam-9798	92	12	square	square	PROPN
bam-9798	92	13	n	n	CCONJ
bam-9798	92	14	r	r	NOUN
bam-9798	92	15	diet	diet	NOUN
bam-9798	92	16	and	and	CCONJ
bam-9798	92	17	physical	physical	ADJ
bam-9798	92	18	activities	activity	NOUN
bam-9798	92	19	5	5	NUM
bam-9798	92	20	(	(	PUNCT
bam-9798	92	21	20	20	NUM
bam-9798	92	22	%	%	NOUN
bam-9798	92	23	)	)	PUNCT
bam-9798	92	24	17	17	NUM
bam-9798	92	25	(	(	PUNCT
bam-9798	92	26	47	47	NUM
bam-9798	92	27	%	%	NOUN
bam-9798	92	28	)	)	PUNCT
bam-9798	92	29	0.029	0.029	NUM
bam-9798	92	30	only	only	ADV
bam-9798	92	31	diet	diet	NOUN
bam-9798	92	32	,	,	PUNCT
bam-9798	92	33	only	only	ADV
bam-9798	92	34	physical	physical	ADJ
bam-9798	92	35	activities	activity	NOUN
bam-9798	92	36	,	,	PUNCT
bam-9798	92	37	none	none	NOUN
bam-9798	92	38	20	20	NUM
bam-9798	92	39	(	(	PUNCT
bam-9798	92	40	80	80	NUM
bam-9798	92	41	%	%	NOUN
bam-9798	92	42	)	)	PUNCT
bam-9798	92	43	19	19	NUM
bam-9798	92	44	(	(	PUNCT
bam-9798	92	45	53	53	NUM
bam-9798	92	46	%	%	NOUN
bam-9798	92	47	)	)	PUNCT
bam-9798	92	48	sd	sd	NOUN
bam-9798	92	49	,	,	PUNCT
bam-9798	92	50	standard	standard	ADJ
bam-9798	92	51	deviation	deviation	NOUN
bam-9798	92	52	;	;	PUNCT
bam-9798	92	53	p	p	PROPN
bam-9798	92	54	mann	mann	PROPN
bam-9798	92	55	-	-	PUNCT
bam-9798	92	56	whitney	whitney	PROPN
bam-9798	92	57	and	and	CCONJ
bam-9798	92	58	pearson	pearson	PROPN
bam-9798	92	59	chi	chi	PROPN
bam-9798	92	60	square	square	PROPN
bam-9798	92	61	:	:	PUNCT
bam-9798	93	1	n.s	n.s	PROPN
bam-9798	93	2	.	.	PROPN
bam-9798	93	3	,	,	PUNCT
bam-9798	93	4	non	non	ADJ
bam-9798	93	5	-	-	ADJ
bam-9798	93	6	significant	significant	ADJ
bam-9798	93	7	exercise	exercise	NOUN
bam-9798	93	8	and	and	CCONJ
bam-9798	93	9	nutrition	nutrition	NOUN
bam-9798	93	10	in	in	ADP
bam-9798	93	11	late	late	ADJ
bam-9798	93	12	onset	onset	ADJ
bam-9798	93	13	pompe	pompe	PROPN
bam-9798	93	14	disease	disease	PROPN
bam-9798	93	15	eur	eur	PROPN
bam-9798	93	16	j	j	PROPN
bam-9798	93	17	transl	transl	PROPN
bam-9798	93	18	myol	myol	ADV
bam-9798	93	19	31	31	NUM
bam-9798	93	20	(	(	PUNCT
bam-9798	93	21	2	2	NUM
bam-9798	93	22	):	):	PUNCT
bam-9798	93	23	9798	9798	NUM
bam-9798	93	24	,	,	PUNCT
bam-9798	93	25	2021	2021	NUM
bam-9798	93	26	doi	doi	NOUN
bam-9798	93	27	:	:	PUNCT
bam-9798	93	28	10.4081	10.4081	NUM
bam-9798	93	29	/	/	SYM
bam-9798	93	30	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	93	31	6	6	NUM
bam-9798	93	32	disease	disease	NOUN
bam-9798	93	33	is	be	AUX
bam-9798	93	34	the	the	DET
bam-9798	93	35	administration	administration	NOUN
bam-9798	93	36	of	of	ADP
bam-9798	93	37	enzyme	enzyme	NOUN
bam-9798	93	38	replacement	replacement	NOUN
bam-9798	93	39	therapy	therapy	NOUN
bam-9798	93	40	(	(	PUNCT
bam-9798	93	41	ert),16	ert),16	PROPN
bam-9798	93	42	while	while	SCONJ
bam-9798	93	43	exercise	exercise	NOUN
bam-9798	93	44	and	and	CCONJ
bam-9798	93	45	nutrition	nutrition	NOUN
bam-9798	93	46	should	should	AUX
bam-9798	93	47	be	be	AUX
bam-9798	93	48	considered	consider	VERB
bam-9798	93	49	as	as	ADP
bam-9798	93	50	complementary	complementary	ADJ
bam-9798	93	51	strategies	strategy	NOUN
bam-9798	93	52	rather	rather	ADV
bam-9798	93	53	than	than	ADP
bam-9798	93	54	“	"	PUNCT
bam-9798	93	55	treatments	treatment	NOUN
bam-9798	93	56	”	"	PUNCT
bam-9798	93	57	per	per	ADP
bam-9798	93	58	se	se	X
bam-9798	93	59	.	.	PUNCT
bam-9798	94	1	nutritional	nutritional	ADJ
bam-9798	94	2	assessment	assessment	NOUN
bam-9798	94	3	is	be	AUX
bam-9798	94	4	important	important	ADJ
bam-9798	94	5	in	in	ADP
bam-9798	94	6	patients	patient	NOUN
bam-9798	94	7	with	with	ADP
bam-9798	94	8	motor	motor	NOUN
bam-9798	94	9	disability	disability	NOUN
bam-9798	94	10	because	because	SCONJ
bam-9798	94	11	the	the	DET
bam-9798	94	12	relative	relative	ADJ
bam-9798	94	13	lack	lack	NOUN
bam-9798	94	14	of	of	ADP
bam-9798	94	15	exercise	exercise	NOUN
bam-9798	94	16	limits	limit	VERB
bam-9798	94	17	energy	energy	NOUN
bam-9798	94	18	expenditure	expenditure	NOUN
bam-9798	94	19	and	and	CCONJ
bam-9798	94	20	thus	thus	ADV
bam-9798	94	21	the	the	DET
bam-9798	94	22	total	total	ADJ
bam-9798	94	23	amount	amount	NOUN
bam-9798	94	24	of	of	ADP
bam-9798	94	25	energy	energy	NOUN
bam-9798	94	26	must	must	AUX
bam-9798	94	27	be	be	AUX
bam-9798	94	28	reduced	reduce	VERB
bam-9798	94	29	to	to	PART
bam-9798	94	30	avoid	avoid	VERB
bam-9798	94	31	obesity	obesity	NOUN
bam-9798	94	32	.	.	PUNCT
bam-9798	95	1	a	a	DET
bam-9798	95	2	lower	low	ADJ
bam-9798	95	3	total	total	ADJ
bam-9798	95	4	energy	energy	NOUN
bam-9798	95	5	intake	intake	NOUN
bam-9798	95	6	often	often	ADV
bam-9798	95	7	leads	lead	VERB
bam-9798	95	8	to	to	ADP
bam-9798	95	9	lower	low	ADJ
bam-9798	95	10	protein	protein	NOUN
bam-9798	95	11	and	and	CCONJ
bam-9798	95	12	micronutrient	micronutrient	NOUN
bam-9798	95	13	intake	intake	NOUN
bam-9798	95	14	.	.	PUNCT
bam-9798	96	1	consequently	consequently	ADV
bam-9798	96	2	,	,	PUNCT
bam-9798	96	3	ensuring	ensure	VERB
bam-9798	96	4	that	that	SCONJ
bam-9798	96	5	lopd	lopd	NOUN
bam-9798	96	6	patients	patient	NOUN
bam-9798	96	7	are	be	AUX
bam-9798	96	8	tested	test	VERB
bam-9798	96	9	for	for	ADP
bam-9798	96	10	and	and	CCONJ
bam-9798	96	11	replaced	replace	VERB
bam-9798	96	12	for	for	ADP
bam-9798	96	13	deficiencies	deficiency	NOUN
bam-9798	96	14	(	(	PUNCT
bam-9798	96	15	protein	protein	NOUN
bam-9798	96	16	,	,	PUNCT
bam-9798	96	17	vitamin	vitamin	NOUN
bam-9798	96	18	d	d	PROPN
bam-9798	96	19	,	,	PUNCT
bam-9798	96	20	etc	etc	X
bam-9798	96	21	.	.	X
bam-9798	96	22	)	)	PUNCT
bam-9798	96	23	is	be	AUX
bam-9798	96	24	an	an	DET
bam-9798	96	25	important	important	ADJ
bam-9798	96	26	aspect	aspect	NOUN
bam-9798	96	27	of	of	ADP
bam-9798	96	28	care	care	NOUN
bam-9798	96	29	.	.	PUNCT
bam-9798	97	1	furthermore	furthermore	ADV
bam-9798	97	2	,	,	PUNCT
bam-9798	97	3	given	give	VERB
bam-9798	97	4	the	the	DET
bam-9798	97	5	role	role	NOUN
bam-9798	97	6	of	of	ADP
bam-9798	97	7	autophagy	autophagy	NOUN
bam-9798	97	8	in	in	ADP
bam-9798	97	9	the	the	DET
bam-9798	97	10	pathophysiology	pathophysiology	NOUN
bam-9798	97	11	of	of	ADP
bam-9798	97	12	lopd	lopd	NOUN
bam-9798	97	13	,	,	PUNCT
bam-9798	97	14	and	and	CCONJ
bam-9798	97	15	the	the	DET
bam-9798	97	16	fact	fact	NOUN
bam-9798	97	17	that	that	SCONJ
bam-9798	97	18	exercise	exercise	NOUN
bam-9798	97	19	induces	induce	VERB
bam-9798	97	20	autophagy,17	autophagy,17	NOUN
bam-9798	97	21	it	it	PRON
bam-9798	97	22	is	be	AUX
bam-9798	97	23	important	important	ADJ
bam-9798	97	24	that	that	SCONJ
bam-9798	97	25	strategies	strategy	NOUN
bam-9798	97	26	such	such	ADJ
bam-9798	97	27	as	as	ADP
bam-9798	97	28	diet	diet	NOUN
bam-9798	97	29	and	and	CCONJ
bam-9798	97	30	exercise	exercise	NOUN
bam-9798	97	31	are	be	AUX
bam-9798	97	32	used	use	VERB
bam-9798	97	33	in	in	ADP
bam-9798	97	34	combination	combination	NOUN
bam-9798	97	35	to	to	PART
bam-9798	97	36	ert	ert	VERB
bam-9798	97	37	.	.	PUNCT
bam-9798	98	1	in	in	ADP
bam-9798	98	2	conclusion	conclusion	NOUN
bam-9798	98	3	,	,	PUNCT
bam-9798	98	4	the	the	DET
bam-9798	98	5	available	available	ADJ
bam-9798	98	6	data	datum	NOUN
bam-9798	98	7	show	show	VERB
bam-9798	98	8	that	that	SCONJ
bam-9798	98	9	pre	pre	ADJ
bam-9798	98	10	-	-	ADJ
bam-9798	98	11	ert	ert	ADJ
bam-9798	98	12	performance	performance	NOUN
bam-9798	98	13	during	during	ADP
bam-9798	98	14	6mwt	6mwt	PROPN
bam-9798	98	15	is	be	AUX
bam-9798	98	16	a	a	DET
bam-9798	98	17	significant	significant	ADJ
bam-9798	98	18	factor	factor	NOUN
bam-9798	98	19	associated	associate	VERB
bam-9798	98	20	with	with	ADP
bam-9798	98	21	responder	responder	NOUN
bam-9798	98	22	category	category	NOUN
bam-9798	98	23	.	.	PUNCT
bam-9798	99	1	in	in	ADP
bam-9798	99	2	lopd	lopd	NOUN
bam-9798	99	3	patients	patient	NOUN
bam-9798	99	4	there	there	PRON
bam-9798	99	5	was	be	VERB
bam-9798	99	6	non	non	ADJ
bam-9798	99	7	-	-	ADJ
bam-9798	99	8	significant	significant	ADJ
bam-9798	99	9	improvement	improvement	NOUN
bam-9798	99	10	of	of	ADP
bam-9798	99	11	muscle	muscle	NOUN
bam-9798	99	12	strength,18	strength,18	NOUN
bam-9798	99	13	while	while	SCONJ
bam-9798	99	14	respiratory	respiratory	ADJ
bam-9798	99	15	status	status	NOUN
bam-9798	99	16	was	be	AUX
bam-9798	99	17	maintained.19	maintained.19	ADJ
bam-9798	99	18	more	more	ADV
bam-9798	99	19	prospective	prospective	ADJ
bam-9798	99	20	data	datum	NOUN
bam-9798	99	21	would	would	AUX
bam-9798	99	22	be	be	AUX
bam-9798	99	23	needed	need	VERB
bam-9798	99	24	to	to	PART
bam-9798	99	25	prove	prove	VERB
bam-9798	99	26	the	the	DET
bam-9798	99	27	effect	effect	NOUN
bam-9798	99	28	of	of	ADP
bam-9798	99	29	supportive	supportive	ADJ
bam-9798	99	30	therapies	therapy	NOUN
bam-9798	99	31	,	,	PUNCT
bam-9798	99	32	but	but	CCONJ
bam-9798	99	33	the	the	DET
bam-9798	99	34	present	present	ADJ
bam-9798	99	35	results	result	NOUN
bam-9798	99	36	show	show	VERB
bam-9798	99	37	the	the	DET
bam-9798	99	38	importance	importance	NOUN
bam-9798	99	39	of	of	ADP
bam-9798	99	40	a	a	DET
bam-9798	99	41	dietary	dietary	ADJ
bam-9798	99	42	and	and	CCONJ
bam-9798	99	43	exercise	exercise	NOUN
bam-9798	99	44	protocol	protocol	NOUN
bam-9798	99	45	concomitant	concomitant	ADJ
bam-9798	99	46	to	to	PART
bam-9798	99	47	ert	ert	VERB
bam-9798	99	48	.	.	PUNCT
bam-9798	100	1	furthermore	furthermore	ADV
bam-9798	100	2	we	we	PRON
bam-9798	100	3	propose	propose	VERB
bam-9798	100	4	that	that	SCONJ
bam-9798	100	5	in	in	ADP
bam-9798	100	6	future	future	NOUN
bam-9798	100	7	the	the	DET
bam-9798	100	8	use	use	NOUN
bam-9798	100	9	of	of	ADP
bam-9798	100	10	a	a	DET
bam-9798	100	11	mobile	mobile	ADJ
bam-9798	100	12	app	app	NOUN
bam-9798	100	13	may	may	AUX
bam-9798	100	14	implement	implement	VERB
bam-9798	100	15	controls	control	NOUN
bam-9798	100	16	on	on	ADP
bam-9798	100	17	such	such	ADJ
bam-9798	100	18	benefits	benefit	NOUN
bam-9798	100	19	for	for	ADP
bam-9798	100	20	patients.20	patients.20	PROPN
bam-9798	100	21	list	list	NOUN
bam-9798	100	22	of	of	ADP
bam-9798	100	23	acronyms	acronym	NOUN
bam-9798	100	24	ert	ert	VERB
bam-9798	100	25	enzyme	enzyme	NOUN
bam-9798	100	26	replacement	replacement	NOUN
bam-9798	100	27	therapy	therapy	NOUN
bam-9798	100	28	epoc	epoc	PROPN
bam-9798	100	29	european	european	PROPN
bam-9798	100	30	pompe	pompe	PROPN
bam-9798	100	31	consortium	consortium	PROPN
bam-9798	100	32	enmc	enmc	VERB
bam-9798	100	33	european	european	ADJ
bam-9798	100	34	neuromuscular	neuromuscular	ADJ
bam-9798	100	35	center	center	NOUN
bam-9798	100	36	lopd	lopd	NOUN
bam-9798	100	37	late	late	ADJ
bam-9798	100	38	onset	onset	VERB
bam-9798	100	39	pompe	pompe	PROPN
bam-9798	100	40	disease	disease	PROPN
bam-9798	100	41	bmi	bmi	PROPN
bam-9798	100	42	body	body	PROPN
bam-9798	100	43	mass	mass	PROPN
bam-9798	100	44	index	index	NOUN
bam-9798	100	45	6mwt	6mwt	NUM
bam-9798	100	46	six	six	NUM
bam-9798	100	47	minute	minute	NOUN
bam-9798	100	48	walk	walk	NOUN
bam-9798	100	49	test	test	NOUN
bam-9798	100	50	fvc	fvc	PROPN
bam-9798	100	51	forced	force	VERB
bam-9798	100	52	vital	vital	ADJ
bam-9798	100	53	capacity	capacity	NOUN
bam-9798	100	54	gmw	gmw	NOUN
bam-9798	100	55	gardner	gardner	NOUN
bam-9798	100	56	-	-	PUNCT
bam-9798	100	57	medwin	medwin	PROPN
bam-9798	100	58	-	-	PUNCT
bam-9798	100	59	walton	walton	PROPN
bam-9798	100	60	scale	scale	NOUN
bam-9798	100	61	gsgc	gsgc	PROPN
bam-9798	100	62	gait	gait	NOUN
bam-9798	100	63	,	,	PUNCT
bam-9798	100	64	stairs	stair	NOUN
bam-9798	100	65	,	,	PUNCT
bam-9798	100	66	gowers	gower	NOUN
bam-9798	100	67	,	,	PUNCT
bam-9798	100	68	chair	chair	NOUN
bam-9798	100	69	scale	scale	NOUN
bam-9798	100	70	r	r	NOUN
bam-9798	100	71	responder	responder	NOUN
bam-9798	100	72	n	n	CCONJ
bam-9798	100	73	non	non	ADJ
bam-9798	100	74	-	-	ADJ
bam-9798	100	75	responder	responder	ADJ
bam-9798	100	76	author	author	NOUN
bam-9798	100	77	contributions	contribution	NOUN
bam-9798	100	78	this	this	PRON
bam-9798	100	79	is	be	AUX
bam-9798	100	80	a	a	DET
bam-9798	100	81	one	one	NUM
bam-9798	100	82	-	-	PUNCT
bam-9798	100	83	author	author	NOUN
bam-9798	100	84	paper	paper	NOUN
bam-9798	100	85	.	.	PUNCT
bam-9798	101	1	acknowledgments	acknowledgment	NOUN
bam-9798	101	2	funding	fund	VERB
bam-9798	101	3	this	this	DET
bam-9798	101	4	workshop	workshop	NOUN
bam-9798	101	5	was	be	AUX
bam-9798	101	6	made	make	VERB
bam-9798	101	7	possible	possible	ADJ
bam-9798	101	8	with	with	ADP
bam-9798	101	9	the	the	DET
bam-9798	101	10	financial	financial	ADJ
bam-9798	101	11	support	support	NOUN
bam-9798	101	12	of	of	ADP
bam-9798	101	13	the	the	DET
bam-9798	101	14	european	european	ADJ
bam-9798	101	15	neuromuscular	neuromuscular	ADJ
bam-9798	101	16	centre	centre	NOUN
bam-9798	101	17	(	(	PUNCT
bam-9798	101	18	enmc	enmc	PROPN
bam-9798	101	19	)	)	PUNCT
bam-9798	101	20	and	and	CCONJ
bam-9798	101	21	its	its	PRON
bam-9798	101	22	main	main	ADJ
bam-9798	101	23	sponsors	sponsor	NOUN
bam-9798	101	24	:	:	PUNCT
bam-9798	101	25	association	association	NOUN
bam-9798	101	26	française	française	PROPN
bam-9798	101	27	contre	contre	PROPN
bam-9798	101	28	les	les	X
bam-9798	101	29	myopathies	myopathy	NOUN
bam-9798	101	30	(	(	PUNCT
bam-9798	101	31	france	france	PROPN
bam-9798	101	32	)	)	PUNCT
bam-9798	101	33	,	,	PUNCT
bam-9798	101	34	deutsche	deutsche	PROPN
bam-9798	101	35	gesellschaft	gesellschaft	PROPN
bam-9798	101	36	für	für	PROPN
bam-9798	101	37	muskelkranke	muskelkranke	PROPN
bam-9798	101	38	(	(	PUNCT
bam-9798	101	39	germany	germany	PROPN
bam-9798	101	40	)	)	PUNCT
bam-9798	101	41	,	,	PUNCT
bam-9798	101	42	telethon	telethon	PROPN
bam-9798	101	43	foundation	foundation	NOUN
bam-9798	101	44	(	(	PUNCT
bam-9798	101	45	italy	italy	PROPN
bam-9798	101	46	)	)	PUNCT
bam-9798	101	47	,	,	PUNCT
bam-9798	101	48	schweizerische	schweizerische	PROPN
bam-9798	101	49	stiftung	stiftung	PROPN
bam-9798	101	50	für	für	PROPN
bam-9798	101	51	die	die	VERB
bam-9798	101	52	erforschung	erforschung	PROPN
bam-9798	101	53	der	der	NOUN
bam-9798	101	54	muskelkrankheiten	muskelkrankheiten	VERB
bam-9798	101	55	(	(	PUNCT
bam-9798	101	56	switzeland	switzeland	NOUN
bam-9798	101	57	)	)	PUNCT
bam-9798	101	58	muscular	muscular	ADJ
bam-9798	101	59	dystrophy	dystrophy	NOUN
bam-9798	101	60	campaign	campaign	NOUN
bam-9798	101	61	(	(	PUNCT
bam-9798	101	62	uk	uk	PROPN
bam-9798	101	63	)	)	PUNCT
bam-9798	101	64	.	.	PUNCT
bam-9798	102	1	conflict	conflict	NOUN
bam-9798	102	2	of	of	ADP
bam-9798	102	3	interest	interest	NOUN
bam-9798	102	4	the	the	DET
bam-9798	102	5	author	author	NOUN
bam-9798	102	6	declares	declare	VERB
bam-9798	102	7	no	no	DET
bam-9798	102	8	financial	financial	ADJ
bam-9798	102	9	,	,	PUNCT
bam-9798	102	10	personal	personal	ADJ
bam-9798	102	11	,	,	PUNCT
bam-9798	102	12	or	or	CCONJ
bam-9798	102	13	other	other	ADJ
bam-9798	102	14	conflicts	conflict	NOUN
bam-9798	102	15	of	of	ADP
bam-9798	102	16	interest	interest	NOUN
bam-9798	102	17	.	.	PUNCT
bam-9798	103	1	ethical	ethical	ADJ
bam-9798	103	2	publication	publication	NOUN
bam-9798	103	3	statement	statement	NOUN
bam-9798	103	4	we	we	PRON
bam-9798	103	5	confirm	confirm	VERB
bam-9798	103	6	that	that	SCONJ
bam-9798	103	7	we	we	PRON
bam-9798	103	8	have	have	AUX
bam-9798	103	9	read	read	VERB
bam-9798	103	10	the	the	DET
bam-9798	103	11	journal	journal	NOUN
bam-9798	103	12	’s	’s	PART
bam-9798	103	13	position	position	NOUN
bam-9798	103	14	on	on	ADP
bam-9798	103	15	issues	issue	NOUN
bam-9798	103	16	involved	involve	VERB
bam-9798	103	17	in	in	ADP
bam-9798	103	18	ethical	ethical	ADJ
bam-9798	103	19	publication	publication	NOUN
bam-9798	103	20	and	and	CCONJ
bam-9798	103	21	affirm	affirm	NOUN
bam-9798	103	22	that	that	SCONJ
bam-9798	103	23	this	this	DET
bam-9798	103	24	report	report	NOUN
bam-9798	103	25	is	be	AUX
bam-9798	103	26	consistent	consistent	ADJ
bam-9798	103	27	with	with	ADP
bam-9798	103	28	those	those	DET
bam-9798	103	29	guidelines	guideline	NOUN
bam-9798	103	30	.	.	PUNCT
bam-9798	104	1	corresponding	correspond	VERB
bam-9798	104	2	author	author	PROPN
bam-9798	104	3	corrado	corrado	PROPN
bam-9798	104	4	angelini	angelini	PROPN
bam-9798	104	5	,	,	PUNCT
bam-9798	104	6	neuromuscular	neuromuscular	ADJ
bam-9798	104	7	laboratory	laboratory	NOUN
bam-9798	104	8	,	,	PUNCT
bam-9798	104	9	department	department	NOUN
bam-9798	104	10	of	of	ADP
bam-9798	104	11	neurosciences	neuroscience	NOUN
bam-9798	104	12	,	,	PUNCT
bam-9798	104	13	university	university	NOUN
bam-9798	104	14	of	of	ADP
bam-9798	104	15	padova	padova	PROPN
bam-9798	104	16	,	,	PUNCT
bam-9798	104	17	padova	padova	PROPN
bam-9798	104	18	,	,	PUNCT
bam-9798	104	19	italy	italy	PROPN
bam-9798	104	20	orcid	orcid	PROPN
bam-9798	105	1	i	i	PRON
bam-9798	105	2	d	d	NOUN
bam-9798	105	3	:	:	PUNCT
bam-9798	105	4	0000	0000	NUM
bam-9798	105	5	-	-	PUNCT
bam-9798	105	6	0002	0002	NUM
bam-9798	105	7	-	-	PUNCT
bam-9798	105	8	9554	9554	NUM
bam-9798	105	9	-	-	PUNCT
bam-9798	105	10	8794	8794	NUM
bam-9798	105	11	e	e	NOUN
bam-9798	105	12	-	-	NOUN
bam-9798	105	13	mail	mail	NOUN
bam-9798	105	14	:	:	PUNCT
bam-9798	105	15	corrado.angelini@unipd.it	corrado.angelini@unipd.it	NUM
bam-9798	105	16	references	reference	NOUN
bam-9798	105	17	1	1	NUM
bam-9798	105	18	.	.	PUNCT
bam-9798	106	1	van	van	PROPN
bam-9798	106	2	den	den	PROPN
bam-9798	106	3	hout	hout	PROPN
bam-9798	106	4	jm	jm	PROPN
bam-9798	106	5	,	,	PUNCT
bam-9798	106	6	kamphoven	kamphoven	PROPN
bam-9798	106	7	jh	jh	PROPN
bam-9798	106	8	,	,	PUNCT
bam-9798	106	9	winkel	winkel	PROPN
bam-9798	106	10	lp	lp	PROPN
bam-9798	106	11	,	,	PUNCT
bam-9798	106	12	arts	arts	PROPN
bam-9798	106	13	wf	wf	PROPN
bam-9798	106	14	,	,	PUNCT
bam-9798	106	15	de	de	PROPN
bam-9798	106	16	klerk	klerk	PROPN
bam-9798	106	17	jb	jb	PROPN
bam-9798	106	18	,	,	PUNCT
bam-9798	106	19	loonen	loonen	PROPN
bam-9798	106	20	mc	mc	PROPN
bam-9798	106	21	,	,	PUNCT
bam-9798	106	22	vulto	vulto	PROPN
bam-9798	106	23	ag	ag	PROPN
bam-9798	106	24	,	,	PUNCT
bam-9798	106	25	cromme	cromme	NOUN
bam-9798	106	26	-	-	PUNCT
bam-9798	106	27	dijkhuis	dijkhuis	NOUN
bam-9798	106	28	a	a	NOUN
bam-9798	106	29	,	,	PUNCT
bam-9798	106	30	weisglas	weisglas	PROPN
bam-9798	106	31	-	-	PUNCT
bam-9798	106	32	kuperus	kuperus	NOUN
bam-9798	106	33	n	n	CCONJ
bam-9798	106	34	,	,	PUNCT
bam-9798	106	35	hop	hop	PROPN
bam-9798	106	36	w	w	PROPN
bam-9798	106	37	,	,	PUNCT
bam-9798	106	38	van	van	PROPN
bam-9798	106	39	hirtum	hirtum	PROPN
bam-9798	106	40	h	h	PROPN
bam-9798	106	41	,	,	PUNCT
bam-9798	106	42	van	van	PROPN
bam-9798	106	43	diggelen	diggelen	VERB
bam-9798	106	44	op	op	NOUN
bam-9798	106	45	,	,	PUNCT
bam-9798	106	46	boer	boer	PROPN
bam-9798	106	47	m	m	PROPN
bam-9798	106	48	,	,	PUNCT
bam-9798	106	49	kroos	kroos	PROPN
bam-9798	106	50	ma	ma	PROPN
bam-9798	106	51	,	,	PUNCT
bam-9798	106	52	van	van	PROPN
bam-9798	106	53	doorn	doorn	PROPN
bam-9798	106	54	pa	pa	PROPN
bam-9798	106	55	,	,	PUNCT
bam-9798	106	56	van	van	PROPN
bam-9798	106	57	der	der	PROPN
bam-9798	106	58	voort	voort	PROPN
bam-9798	106	59	e	e	PROPN
bam-9798	106	60	,	,	PUNCT
bam-9798	106	61	sibbles	sibble	NOUN
bam-9798	106	62	b	b	NUM
bam-9798	106	63	,	,	PUNCT
bam-9798	106	64	van	van	PROPN
bam-9798	106	65	corven	corven	NOUN
bam-9798	106	66	ej	ej	PROPN
bam-9798	106	67	,	,	PUNCT
bam-9798	106	68	brakenhoff	brakenhoff	PROPN
bam-9798	106	69	jp	jp	PROPN
bam-9798	106	70	,	,	PUNCT
bam-9798	106	71	van	van	PROPN
bam-9798	106	72	hove	hove	PROPN
bam-9798	106	73	j	j	PROPN
bam-9798	106	74	,	,	PUNCT
bam-9798	106	75	smeitink	smeitink	PROPN
bam-9798	106	76	ja	ja	PROPN
bam-9798	106	77	,	,	PUNCT
bam-9798	106	78	de	de	PROPN
bam-9798	106	79	jong	jong	PROPN
bam-9798	106	80	g	g	PROPN
bam-9798	106	81	,	,	PUNCT
bam-9798	106	82	reuser	reuser	PROPN
bam-9798	106	83	aj	aj	PROPN
bam-9798	106	84	,	,	PUNCT
bam-9798	106	85	van	van	PROPN
bam-9798	106	86	der	der	PROPN
bam-9798	106	87	ploeg	ploeg	PROPN
bam-9798	106	88	at	at	ADP
bam-9798	106	89	.	.	PUNCT
bam-9798	107	1	long	long	ADJ
bam-9798	107	2	-	-	PUNCT
bam-9798	107	3	term	term	NOUN
bam-9798	107	4	intravenous	intravenous	ADJ
bam-9798	107	5	treatment	treatment	NOUN
bam-9798	107	6	of	of	ADP
bam-9798	107	7	pompe	pompe	PROPN
bam-9798	107	8	disease	disease	NOUN
bam-9798	107	9	with	with	ADP
bam-9798	107	10	recombinant	recombinant	ADJ
bam-9798	107	11	human	human	ADJ
bam-9798	107	12	alpha	alpha	NOUN
bam-9798	107	13	-	-	PUNCT
bam-9798	107	14	glucosidase	glucosidase	NOUN
bam-9798	107	15	from	from	ADP
bam-9798	107	16	milk	milk	NOUN
bam-9798	107	17	.	.	PUNCT
bam-9798	108	1	pediatrics	pediatric	NOUN
bam-9798	108	2	.	.	PUNCT
bam-9798	109	1	2004	2004	NUM
bam-9798	109	2	may;113(5):e448	may;113(5):e448	NUM
bam-9798	109	3	-	-	SYM
bam-9798	109	4	57	57	NUM
bam-9798	109	5	.	.	PUNCT
bam-9798	110	1	doi	doi	NOUN
bam-9798	110	2	:	:	PUNCT
bam-9798	110	3	10.1542	10.1542	NUM
bam-9798	110	4	/	/	SYM
bam-9798	110	5	peds.113.5.e448	peds.113.5.e448	X
bam-9798	110	6	.	.	PUNCT
bam-9798	111	1	2	2	X
bam-9798	111	2	.	.	X
bam-9798	111	3	kishnani	kishnani	PROPN
bam-9798	111	4	ps	ps	PROPN
bam-9798	111	5	,	,	PUNCT
bam-9798	111	6	corzo	corzo	NOUN
bam-9798	111	7	d	d	PROPN
bam-9798	111	8	,	,	PUNCT
bam-9798	111	9	nicolino	nicolino	PROPN
bam-9798	111	10	m	m	PROPN
bam-9798	111	11	,	,	PUNCT
bam-9798	111	12	byrne	byrne	PROPN
bam-9798	111	13	b	b	PROPN
bam-9798	111	14	,	,	PUNCT
bam-9798	111	15	mandel	mandel	PROPN
bam-9798	111	16	h	h	PROPN
bam-9798	111	17	,	,	PUNCT
bam-9798	111	18	hwu	hwu	PROPN
bam-9798	111	19	wl	wl	PROPN
bam-9798	111	20	,	,	PUNCT
bam-9798	111	21	leslie	leslie	PROPN
bam-9798	111	22	n	n	PROPN
bam-9798	111	23	,	,	PUNCT
bam-9798	111	24	levine	levine	PROPN
bam-9798	111	25	j	j	PROPN
bam-9798	111	26	,	,	PUNCT
bam-9798	111	27	spencer	spencer	PROPN
bam-9798	111	28	c	c	PROPN
bam-9798	111	29	,	,	PUNCT
bam-9798	111	30	mcdonald	mcdonald	PROPN
bam-9798	111	31	m	m	PROPN
bam-9798	111	32	,	,	PUNCT
bam-9798	111	33	li	li	PROPN
bam-9798	111	34	j	j	PROPN
bam-9798	111	35	,	,	PUNCT
bam-9798	111	36	dumontier	dumontier	PROPN
bam-9798	111	37	j	j	PROPN
bam-9798	111	38	,	,	PUNCT
bam-9798	111	39	halberthal	halberthal	PROPN
bam-9798	111	40	m	m	PROPN
bam-9798	111	41	,	,	PUNCT
bam-9798	111	42	chien	chien	PROPN
bam-9798	111	43	yh	yh	PROPN
bam-9798	111	44	,	,	PUNCT
bam-9798	111	45	hopkin	hopkin	PROPN
bam-9798	111	46	r	r	PROPN
bam-9798	111	47	,	,	PUNCT
bam-9798	111	48	vijayaraghavan	vijayaraghavan	NOUN
bam-9798	111	49	s	s	NOUN
bam-9798	111	50	,	,	PUNCT
bam-9798	111	51	gruskin	gruskin	X
bam-9798	111	52	d	d	NOUN
bam-9798	111	53	,	,	PUNCT
bam-9798	111	54	bartholomew	bartholomew	PROPN
bam-9798	111	55	d	d	PROPN
bam-9798	111	56	,	,	PUNCT
bam-9798	111	57	van	van	PROPN
bam-9798	111	58	der	der	PROPN
bam-9798	111	59	ploeg	ploeg	PROPN
bam-9798	111	60	a	a	PROPN
bam-9798	111	61	,	,	PUNCT
bam-9798	111	62	clancy	clancy	NOUN
bam-9798	111	63	jp	jp	NOUN
bam-9798	111	64	,	,	PUNCT
bam-9798	111	65	parini	parini	PROPN
bam-9798	111	66	r	r	NOUN
bam-9798	111	67	,	,	PUNCT
bam-9798	111	68	morin	morin	NOUN
bam-9798	111	69	g	g	PROPN
bam-9798	111	70	,	,	PUNCT
bam-9798	111	71	beck	beck	PROPN
bam-9798	111	72	m	m	PROPN
bam-9798	111	73	,	,	PUNCT
bam-9798	111	74	de	de	PROPN
bam-9798	111	75	la	la	PROPN
bam-9798	111	76	gastine	gastine	PROPN
bam-9798	111	77	gs	gs	PROPN
bam-9798	111	78	,	,	PUNCT
bam-9798	111	79	jokic	jokic	PROPN
bam-9798	111	80	m	m	PROPN
bam-9798	111	81	,	,	PUNCT
bam-9798	111	82	thurberg	thurberg	PROPN
bam-9798	111	83	b	b	NUM
bam-9798	111	84	,	,	PUNCT
bam-9798	111	85	richards	richards	PROPN
bam-9798	111	86	s	s	PROPN
bam-9798	111	87	,	,	PUNCT
bam-9798	111	88	bali	bali	PROPN
bam-9798	111	89	d	d	PROPN
bam-9798	111	90	,	,	PUNCT
bam-9798	111	91	davison	davison	PROPN
bam-9798	111	92	m	m	PROPN
bam-9798	111	93	,	,	PUNCT
bam-9798	111	94	worden	worden	PROPN
bam-9798	111	95	ma	ma	PROPN
bam-9798	111	96	,	,	PUNCT
bam-9798	111	97	chen	chen	PROPN
bam-9798	111	98	yt	yt	PROPN
bam-9798	111	99	,	,	PUNCT
bam-9798	111	100	wraith	wraith	PROPN
bam-9798	111	101	je	je	PROPN
bam-9798	111	102	.	.	PROPN
bam-9798	111	103	recombinant	recombinant	ADJ
bam-9798	111	104	human	human	ADJ
bam-9798	111	105	acid	acid	NOUN
bam-9798	112	1	[	[	X
bam-9798	112	2	alpha]-glucosidase	alpha]-glucosidase	PROPN
bam-9798	112	3	:	:	PUNCT
bam-9798	112	4	major	major	ADJ
bam-9798	112	5	clinical	clinical	ADJ
bam-9798	112	6	benefits	benefit	NOUN
bam-9798	112	7	in	in	ADP
bam-9798	112	8	infantile	infantile	ADJ
bam-9798	112	9	-	-	PUNCT
bam-9798	112	10	onset	onset	NOUN
bam-9798	112	11	pompe	pompe	PROPN
bam-9798	112	12	disease	disease	NOUN
bam-9798	112	13	.	.	PUNCT
bam-9798	113	1	neurology	neurology	NOUN
bam-9798	113	2	.	.	PUNCT
bam-9798	114	1	2007	2007	NUM
bam-9798	114	2	jan	jan	PROPN
bam-9798	114	3	9;68(2):99	9;68(2):99	PROPN
bam-9798	114	4	-	-	PUNCT
bam-9798	114	5	109	109	NUM
bam-9798	114	6	.	.	PUNCT
bam-9798	115	1	doi	doi	NOUN
bam-9798	115	2	:	:	PUNCT
bam-9798	115	3	10.1212/01.wnl.0000251268.41188.04	10.1212/01.wnl.0000251268.41188.04	NUM
bam-9798	115	4	.	.	PUNCT
bam-9798	116	1	epub	epub	PROPN
bam-9798	116	2	2006	2006	NUM
bam-9798	116	3	dec	dec	PROPN
bam-9798	116	4	6	6	NUM
bam-9798	116	5	.	.	PUNCT
bam-9798	116	6	erratum	erratum	PROPN
bam-9798	116	7	in	in	ADP
bam-9798	116	8	:	:	PUNCT
bam-9798	116	9	neurology	neurology	NOUN
bam-9798	116	10	.	.	PUNCT
bam-9798	117	1	2008	2008	NUM
bam-9798	117	2	nov	nov	NOUN
bam-9798	117	3	18;71(21):1748	18;71(21):1748	NUM
bam-9798	117	4	.	.	NOUN
bam-9798	118	1	3	3	NUM
bam-9798	118	2	.	.	X
bam-9798	118	3	de	de	PROPN
bam-9798	118	4	vries	vries	PROPN
bam-9798	118	5	jm	jm	PROPN
bam-9798	118	6	,	,	PUNCT
bam-9798	118	7	van	van	PROPN
bam-9798	118	8	der	der	PROPN
bam-9798	118	9	beek	beek	PROPN
bam-9798	119	1	na	na	PROPN
bam-9798	119	2	,	,	PUNCT
bam-9798	119	3	hop	hop	PROPN
bam-9798	119	4	wc	wc	PROPN
bam-9798	119	5	,	,	PUNCT
bam-9798	119	6	karstens	karstens	PROPN
bam-9798	119	7	fp	fp	PROPN
bam-9798	119	8	,	,	PUNCT
bam-9798	119	9	wokke	wokke	PROPN
bam-9798	119	10	jh	jh	PROPN
bam-9798	119	11	,	,	PUNCT
bam-9798	119	12	de	de	PROPN
bam-9798	119	13	visser	visser	PROPN
bam-9798	119	14	m	m	PROPN
bam-9798	119	15	,	,	PUNCT
bam-9798	119	16	van	van	PROPN
bam-9798	119	17	engelen	engelen	PROPN
bam-9798	119	18	bg	bg	PROPN
bam-9798	119	19	,	,	PUNCT
bam-9798	119	20	kuks	kuks	PROPN
bam-9798	119	21	jb	jb	PROPN
bam-9798	119	22	,	,	PUNCT
bam-9798	119	23	van	van	PROPN
bam-9798	119	24	der	der	PROPN
bam-9798	119	25	kooi	kooi	PROPN
bam-9798	119	26	aj	aj	PROPN
bam-9798	119	27	,	,	PUNCT
bam-9798	119	28	notermans	notermans	PROPN
bam-9798	119	29	nc	nc	PROPN
bam-9798	119	30	,	,	PUNCT
bam-9798	119	31	faber	faber	PROPN
bam-9798	119	32	cg	cg	PROPN
bam-9798	119	33	,	,	PUNCT
bam-9798	119	34	verschuuren	verschuuren	PROPN
bam-9798	119	35	jj	jj	PROPN
bam-9798	119	36	,	,	PUNCT
bam-9798	119	37	kruijshaar	kruijshaar	VERB
bam-9798	119	38	me	i	PRON
bam-9798	119	39	,	,	PUNCT
bam-9798	119	40	reuser	reuser	PROPN
bam-9798	119	41	aj	aj	PROPN
bam-9798	119	42	,	,	PUNCT
bam-9798	119	43	van	van	PROPN
bam-9798	119	44	doorn	doorn	PROPN
bam-9798	119	45	pa	pa	PROPN
bam-9798	119	46	,	,	PUNCT
bam-9798	119	47	van	van	PROPN
bam-9798	119	48	der	der	PROPN
bam-9798	119	49	ploeg	ploeg	NOUN
bam-9798	119	50	at	at	ADP
bam-9798	119	51	.	.	PUNCT
bam-9798	120	1	effect	effect	NOUN
bam-9798	120	2	of	of	ADP
bam-9798	120	3	enzyme	enzyme	NOUN
bam-9798	120	4	therapy	therapy	NOUN
bam-9798	120	5	and	and	CCONJ
bam-9798	120	6	prognostic	prognostic	ADJ
bam-9798	120	7	factors	factor	NOUN
bam-9798	120	8	in	in	ADP
bam-9798	120	9	69	69	NUM
bam-9798	120	10	adults	adult	NOUN
bam-9798	120	11	with	with	ADP
bam-9798	120	12	pompe	pompe	PROPN
bam-9798	120	13	disease	disease	PROPN
bam-9798	120	14	:	:	PUNCT
bam-9798	120	15	an	an	DET
bam-9798	120	16	open	open	ADJ
bam-9798	120	17	-	-	PUNCT
bam-9798	120	18	label	label	NOUN
bam-9798	120	19	single	single	ADJ
bam-9798	120	20	-	-	PUNCT
bam-9798	120	21	center	center	NOUN
bam-9798	120	22	study	study	NOUN
bam-9798	120	23	.	.	PUNCT
bam-9798	121	1	orphanet	orphanet	PROPN
bam-9798	121	2	j	j	PROPN
bam-9798	121	3	rare	rare	ADJ
bam-9798	121	4	dis	dis	PROPN
bam-9798	121	5	.	.	PUNCT
bam-9798	122	1	2012	2012	NUM
bam-9798	122	2	sep	sep	PROPN
bam-9798	122	3	26;7:73	26;7:73	NUM
bam-9798	122	4	.	.	PUNCT
bam-9798	123	1	doi	doi	NOUN
bam-9798	123	2	:	:	PUNCT
bam-9798	123	3	10.1186/1750	10.1186/1750	NUM
bam-9798	123	4	-	-	SYM
bam-9798	123	5	1172	1172	NUM
bam-9798	123	6	-	-	PUNCT
bam-9798	123	7	7	7	NUM
bam-9798	123	8	-	-	SYM
bam-9798	123	9	73	73	NUM
bam-9798	123	10	.	.	PUNCT
bam-9798	124	1	4	4	X
bam-9798	124	2	.	.	X
bam-9798	124	3	güngör	güngör	PROPN
bam-9798	124	4	d	d	PROPN
bam-9798	124	5	,	,	PUNCT
bam-9798	124	6	kruijshaar	kruijshaar	VERB
bam-9798	124	7	me	i	PRON
bam-9798	124	8	,	,	PUNCT
bam-9798	124	9	plug	plug	VERB
bam-9798	124	10	i	i	PRON
bam-9798	124	11	,	,	PUNCT
bam-9798	124	12	d'agostino	d'agostino	PROPN
bam-9798	124	13	rb	rb	PROPN
bam-9798	124	14	,	,	PUNCT
bam-9798	124	15	hagemans	hageman	NOUN
bam-9798	124	16	ml	ml	NOUN
bam-9798	124	17	,	,	PUNCT
bam-9798	124	18	van	van	PROPN
bam-9798	124	19	doorn	doorn	PROPN
bam-9798	124	20	pa	pa	PROPN
bam-9798	124	21	,	,	PUNCT
bam-9798	124	22	reuser	reuser	PROPN
bam-9798	124	23	aj	aj	PROPN
bam-9798	124	24	,	,	PUNCT
bam-9798	124	25	van	van	PROPN
bam-9798	124	26	der	der	PROPN
bam-9798	124	27	ploeg	ploeg	PROPN
bam-9798	124	28	at	at	ADP
bam-9798	124	29	.	.	PUNCT
bam-9798	125	1	impact	impact	NOUN
bam-9798	125	2	of	of	ADP
bam-9798	125	3	enzyme	enzyme	NOUN
bam-9798	125	4	replacement	replacement	NOUN
bam-9798	125	5	therapy	therapy	NOUN
bam-9798	125	6	on	on	ADP
bam-9798	125	7	survival	survival	NOUN
bam-9798	125	8	in	in	ADP
bam-9798	125	9	adults	adult	NOUN
bam-9798	125	10	with	with	ADP
bam-9798	125	11	pompe	pompe	PROPN
bam-9798	125	12	disease	disease	PROPN
bam-9798	125	13	:	:	PUNCT
bam-9798	125	14	results	result	VERB
bam-9798	125	15	from	from	ADP
bam-9798	125	16	a	a	DET
bam-9798	125	17	prospective	prospective	ADJ
bam-9798	125	18	international	international	ADJ
bam-9798	125	19	observational	observational	ADJ
bam-9798	125	20	study	study	NOUN
bam-9798	125	21	.	.	PUNCT
bam-9798	126	1	orphanet	orphanet	PROPN
bam-9798	126	2	j	j	PROPN
bam-9798	126	3	rare	rare	ADJ
bam-9798	126	4	dis	dis	PROPN
bam-9798	126	5	.	.	PUNCT
bam-9798	127	1	2013	2013	NUM
bam-9798	127	2	mar	mar	PROPN
bam-9798	127	3	27;8:49	27;8:49	NUM
bam-9798	127	4	.	.	PUNCT
bam-9798	127	5	doi	doi	NOUN
bam-9798	127	6	:	:	PUNCT
bam-9798	127	7	10.1186/1750	10.1186/1750	NUM
bam-9798	127	8	-	-	SYM
bam-9798	127	9	1172	1172	NUM
bam-9798	127	10	-	-	PUNCT
bam-9798	127	11	8	8	NUM
bam-9798	127	12	-	-	NUM
bam-9798	127	13	49	49	NUM
bam-9798	127	14	.	.	PUNCT
bam-9798	128	1	5	5	NUM
bam-9798	128	2	.	.	X
bam-9798	128	3	toscano	toscano	PROPN
bam-9798	128	4	a	a	PRON
bam-9798	128	5	,	,	PUNCT
bam-9798	128	6	schoser	schoser	NOUN
bam-9798	128	7	b.	b.	PROPN
bam-9798	128	8	enzyme	enzyme	NOUN
bam-9798	128	9	replacement	replacement	NOUN
bam-9798	128	10	therapy	therapy	NOUN
bam-9798	128	11	in	in	ADP
bam-9798	128	12	late	late	ADJ
bam-9798	128	13	-	-	PUNCT
bam-9798	128	14	onset	onset	NOUN
bam-9798	128	15	pompe	pompe	PROPN
bam-9798	128	16	disease	disease	NOUN
bam-9798	128	17	:	:	PUNCT
bam-9798	128	18	a	a	DET
bam-9798	128	19	systematic	systematic	ADJ
bam-9798	128	20	literature	literature	NOUN
bam-9798	128	21	review	review	NOUN
bam-9798	128	22	.	.	PUNCT
bam-9798	129	1	j	j	PROPN
bam-9798	129	2	neurol	neurol	PROPN
bam-9798	129	3	.	.	PUNCT
bam-9798	130	1	2013	2013	NUM
bam-9798	130	2	apr;260(4):951	apr;260(4):951	NOUN
bam-9798	130	3	-	-	PUNCT
bam-9798	130	4	9	9	NUM
bam-9798	130	5	.	.	PUNCT
bam-9798	131	1	mailto:corrado.angelini@unipd.it	mailto:corrado.angelini@unipd.it	ADJ
bam-9798	131	2	exercise	exercise	NOUN
bam-9798	131	3	and	and	CCONJ
bam-9798	131	4	nutrition	nutrition	NOUN
bam-9798	131	5	in	in	ADP
bam-9798	131	6	late	late	ADJ
bam-9798	131	7	onset	onset	ADJ
bam-9798	131	8	pompe	pompe	PROPN
bam-9798	131	9	disease	disease	PROPN
bam-9798	131	10	eur	eur	PROPN
bam-9798	131	11	j	j	PROPN
bam-9798	131	12	transl	transl	PROPN
bam-9798	131	13	myol	myol	ADV
bam-9798	131	14	31	31	NUM
bam-9798	131	15	(	(	PUNCT
bam-9798	131	16	2	2	NUM
bam-9798	131	17	):	):	PUNCT
bam-9798	131	18	9798	9798	NUM
bam-9798	131	19	,	,	PUNCT
bam-9798	131	20	2021	2021	NUM
bam-9798	131	21	doi	doi	NOUN
bam-9798	131	22	:	:	PUNCT
bam-9798	131	23	10.4081	10.4081	NUM
bam-9798	131	24	/	/	SYM
bam-9798	131	25	ejtm.2021.9798	ejtm.2021.9798	ADJ
bam-9798	131	26	7	7	NUM
bam-9798	131	27	doi	doi	NOUN
bam-9798	131	28	:	:	PUNCT
bam-9798	131	29	10.1007	10.1007	NUM
bam-9798	131	30	/	/	SYM
bam-9798	131	31	s00415	s00415	NOUN
bam-9798	131	32	-	-	PUNCT
bam-9798	131	33	012	012	NUM
bam-9798	131	34	-	-	PUNCT
bam-9798	131	35	6636	6636	NUM
bam-9798	131	36	-	-	PUNCT
bam-9798	131	37	x.	x.	NOUN
bam-9798	131	38	epub	epub	PROPN
bam-9798	131	39	2012	2012	NUM
bam-9798	131	40	aug	aug	PROPN
bam-9798	131	41	28	28	NUM
bam-9798	131	42	.	.	PUNCT
bam-9798	132	1	6	6	NUM
bam-9798	132	2	.	.	PUNCT
bam-9798	132	3	barba	barba	NOUN
bam-9798	132	4	-	-	PUNCT
bam-9798	132	5	romero	romero	PROPN
bam-9798	132	6	ma	ma	PROPN
bam-9798	132	7	,	,	PUNCT
bam-9798	132	8	barrot	barrot	PROPN
bam-9798	132	9	e	e	PROPN
bam-9798	132	10	,	,	PUNCT
bam-9798	132	11	bautista	bautista	PROPN
bam-9798	132	12	-	-	PUNCT
bam-9798	132	13	lorite	lorite	PROPN
bam-9798	132	14	j	j	PROPN
bam-9798	132	15	,	,	PUNCT
bam-9798	132	16	gutierrez	gutierrez	PROPN
bam-9798	132	17	-	-	PUNCT
bam-9798	132	18	rivas	rivas	PROPN
bam-9798	132	19	e	e	PROPN
bam-9798	132	20	,	,	PUNCT
bam-9798	132	21	illa	illa	VERB
bam-9798	132	22	i	i	PROPN
bam-9798	132	23	,	,	PUNCT
bam-9798	132	24	jimenez	jimenez	PROPN
bam-9798	132	25	lm	lm	PROPN
bam-9798	132	26	,	,	PUNCT
bam-9798	132	27	ley	ley	NOUN
bam-9798	132	28	-	-	PUNCT
bam-9798	132	29	martos	martos	NOUN
bam-9798	132	30	m	m	NOUN
bam-9798	132	31	,	,	PUNCT
bam-9798	132	32	lopez	lopez	PROPN
bam-9798	132	33	de	de	ADP
bam-9798	132	34	munain	munain	PROPN
bam-9798	132	35	a	a	PROPN
bam-9798	132	36	,	,	PUNCT
bam-9798	132	37	pardo	pardo	PROPN
bam-9798	132	38	j	j	PROPN
bam-9798	132	39	,	,	PUNCT
bam-9798	132	40	pascual	pascual	ADJ
bam-9798	132	41	-	-	ADJ
bam-9798	132	42	pascual	pascual	ADJ
bam-9798	132	43	si	si	X
bam-9798	132	44	,	,	PUNCT
bam-9798	132	45	perez	perez	PROPN
bam-9798	132	46	-	-	PUNCT
bam-9798	132	47	lopez	lopez	PROPN
bam-9798	132	48	j	j	PROPN
bam-9798	132	49	,	,	PUNCT
bam-9798	132	50	solera	solera	PROPN
bam-9798	132	51	j	j	PROPN
bam-9798	132	52	,	,	PUNCT
bam-9798	132	53	vilchez	vilchez	PROPN
bam-9798	132	54	-	-	PUNCT
bam-9798	132	55	padilla	padilla	PROPN
bam-9798	132	56	jj	jj	PROPN
bam-9798	132	57	.	.	PROPN
bam-9798	132	58	clinical	clinical	ADJ
bam-9798	132	59	guidelines	guideline	NOUN
bam-9798	132	60	for	for	ADP
bam-9798	132	61	late	late	ADJ
bam-9798	132	62	-	-	PUNCT
bam-9798	132	63	onset	onset	NOUN
bam-9798	132	64	pompe	pompe	PROPN
bam-9798	132	65	disease	disease	NOUN
bam-9798	132	66	.	.	PUNCT
bam-9798	133	1	rev	rev	PROPN
bam-9798	133	2	neurol	neurol	PROPN
bam-9798	133	3	.	.	PUNCT
bam-9798	134	1	2012	2012	NUM
bam-9798	134	2	apr	apr	NOUN
bam-9798	134	3	16;54(8):497	16;54(8):497	NUM
bam-9798	134	4	-	-	SYM
bam-9798	134	5	507	507	NUM
bam-9798	134	6	.	.	PUNCT
bam-9798	135	1	english	english	PROPN
bam-9798	135	2	,	,	PUNCT
bam-9798	135	3	spanish	spanish	ADJ
bam-9798	135	4	.	.	PUNCT
bam-9798	136	1	7	7	X
bam-9798	136	2	.	.	NOUN
bam-9798	136	3	cupler	cupler	PROPN
bam-9798	136	4	ej	ej	PROPN
bam-9798	136	5	,	,	PUNCT
bam-9798	136	6	berger	berger	PROPN
bam-9798	136	7	ki	ki	PROPN
bam-9798	136	8	,	,	PUNCT
bam-9798	136	9	leshner	leshner	PROPN
bam-9798	136	10	rt	rt	PROPN
bam-9798	136	11	,	,	PUNCT
bam-9798	136	12	wolfe	wolfe	PROPN
bam-9798	136	13	gi	gi	PROPN
bam-9798	136	14	,	,	PUNCT
bam-9798	136	15	han	han	PROPN
bam-9798	136	16	jj	jj	PROPN
bam-9798	136	17	,	,	PUNCT
bam-9798	136	18	barohn	barohn	PROPN
bam-9798	136	19	rj	rj	PROPN
bam-9798	136	20	,	,	PUNCT
bam-9798	136	21	kissel	kissel	PROPN
bam-9798	136	22	jt	jt	PROPN
bam-9798	136	23	;	;	PUNCT
bam-9798	136	24	aanem	aanem	PROPN
bam-9798	136	25	consensus	consensus	PROPN
bam-9798	136	26	committee	committee	PROPN
bam-9798	136	27	on	on	ADP
bam-9798	136	28	late	late	ADJ
bam-9798	136	29	-	-	PUNCT
bam-9798	136	30	onset	onset	NOUN
bam-9798	136	31	pompe	pompe	PROPN
bam-9798	136	32	disease	disease	NOUN
bam-9798	136	33	.	.	PUNCT
bam-9798	137	1	consensus	consensus	NOUN
bam-9798	137	2	treatment	treatment	NOUN
bam-9798	137	3	recommendations	recommendation	NOUN
bam-9798	137	4	for	for	ADP
bam-9798	137	5	lateonset	lateonset	NOUN
bam-9798	137	6	pompe	pompe	PROPN
bam-9798	137	7	disease	disease	PROPN
bam-9798	137	8	.	.	PUNCT
bam-9798	138	1	muscle	muscle	NOUN
bam-9798	138	2	nerve	nerve	NOUN
bam-9798	138	3	.	.	PUNCT
bam-9798	139	1	2012	2012	NUM
bam-9798	139	2	mar;45(3):319	mar;45(3):319	PROPN
bam-9798	139	3	-	-	PUNCT
bam-9798	139	4	33	33	NUM
bam-9798	139	5	.	.	PUNCT
bam-9798	140	1	doi	doi	NOUN
bam-9798	140	2	:	:	PUNCT
bam-9798	140	3	10.1002	10.1002	NUM
bam-9798	140	4	/	/	SYM
bam-9798	140	5	mus.22329	mus.22329	PROPN
bam-9798	140	6	.	.	PUNCT
bam-9798	141	1	epub	epub	PROPN
bam-9798	141	2	2011	2011	NUM
bam-9798	141	3	dec	dec	PROPN
bam-9798	141	4	15	15	NUM
bam-9798	141	5	.	.	NOUN
bam-9798	141	6	8	8	NUM
bam-9798	141	7	.	.	NOUN
bam-9798	141	8	hundsberger	hundsberger	PROPN
bam-9798	141	9	t	t	PROPN
bam-9798	141	10	,	,	PUNCT
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bam-9798	141	12	m	m	PROPN
bam-9798	141	13	,	,	PUNCT
bam-9798	141	14	kern	kern	PROPN
bam-9798	141	15	l	l	PROPN
bam-9798	141	16	,	,	PUNCT
bam-9798	141	17	rösler	rösler	NOUN
bam-9798	141	18	km	km	PROPN
bam-9798	141	19	.	.	PUNCT
bam-9798	142	1	swiss	swiss	ADJ
bam-9798	142	2	national	national	ADJ
bam-9798	142	3	guideline	guideline	NOUN
bam-9798	142	4	for	for	ADP
bam-9798	142	5	reimbursement	reimbursement	NOUN
bam-9798	142	6	of	of	ADP
bam-9798	142	7	enzyme	enzyme	NOUN
bam-9798	142	8	replacement	replacement	NOUN
bam-9798	142	9	therapy	therapy	NOUN
bam-9798	142	10	in	in	ADP
bam-9798	142	11	late	late	ADJ
bam-9798	142	12	-	-	PUNCT
bam-9798	142	13	onset	onset	NOUN
bam-9798	142	14	pompe	pompe	PROPN
bam-9798	142	15	disease	disease	NOUN
bam-9798	142	16	.	.	PUNCT
bam-9798	143	1	j	j	PROPN
bam-9798	143	2	neurol	neurol	PROPN
bam-9798	143	3	.	.	PUNCT
bam-9798	144	1	2013	2013	NUM
bam-9798	144	2	sep;260(9):2279	sep;260(9):2279	NOUN
bam-9798	144	3	-	-	PUNCT
bam-9798	144	4	85	85	NUM
bam-9798	144	5	.	.	PUNCT
bam-9798	145	1	doi	doi	NOUN
bam-9798	145	2	:	:	PUNCT
bam-9798	145	3	10.1007	10.1007	NUM
bam-9798	145	4	/	/	SYM
bam-9798	145	5	s00415	s00415	NOUN
bam-9798	145	6	-	-	PUNCT
bam-9798	145	7	013	013	NUM
bam-9798	145	8	-	-	PUNCT
bam-9798	145	9	6980	6980	NUM
bam-9798	145	10	-	-	SYM
bam-9798	145	11	5	5	NUM
bam-9798	145	12	.	.	PUNCT
bam-9798	146	1	epub	epub	PROPN
bam-9798	146	2	2013	2013	NUM
bam-9798	146	3	jun	jun	PROPN
bam-9798	146	4	8	8	NUM
bam-9798	146	5	.	.	NOUN
bam-9798	146	6	9	9	NUM
bam-9798	146	7	.	.	X
bam-9798	146	8	llerena	llerena	PROPN
bam-9798	146	9	jc	jc	PROPN
bam-9798	146	10	jr	jr	PROPN
bam-9798	146	11	,	,	PUNCT
bam-9798	146	12	horovitz	horovitz	PROPN
bam-9798	146	13	dm	dm	PROPN
bam-9798	146	14	,	,	PUNCT
bam-9798	146	15	marie	marie	PROPN
bam-9798	146	16	sk	sk	PROPN
bam-9798	146	17	,	,	PUNCT
bam-9798	146	18	porta	porta	NOUN
bam-9798	146	19	g	g	PROPN
bam-9798	146	20	,	,	PUNCT
bam-9798	146	21	giugliani	giugliani	PROPN
bam-9798	146	22	r	r	PROPN
bam-9798	146	23	,	,	PUNCT
bam-9798	146	24	rojas	rojas	PROPN
bam-9798	146	25	mv	mv	PROPN
bam-9798	146	26	,	,	PUNCT
bam-9798	146	27	martins	martin	NOUN
bam-9798	146	28	am	be	AUX
bam-9798	146	29	;	;	PUNCT
bam-9798	146	30	brazilian	brazilian	ADJ
bam-9798	146	31	network	network	NOUN
bam-9798	146	32	for	for	ADP
bam-9798	146	33	studies	study	NOUN
bam-9798	146	34	in	in	ADP
bam-9798	146	35	pompe	pompe	PROPN
bam-9798	146	36	disease	disease	PROPN
bam-9798	146	37	(	(	PUNCT
bam-9798	146	38	rebrpom	rebrpom	NOUN
bam-9798	146	39	)	)	PUNCT
bam-9798	146	40	.	.	PUNCT
bam-9798	147	1	the	the	DET
bam-9798	147	2	brazilian	brazilian	ADJ
bam-9798	147	3	consensus	consensus	NOUN
bam-9798	147	4	on	on	ADP
bam-9798	147	5	the	the	DET
bam-9798	147	6	management	management	NOUN
bam-9798	147	7	of	of	ADP
bam-9798	147	8	pompe	pompe	PROPN
bam-9798	147	9	disease	disease	PROPN
bam-9798	147	10	.	.	PUNCT
bam-9798	148	1	j	j	PROPN
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bam-9798	148	3	.	.	PUNCT
bam-9798	149	1	2009	2009	NUM
bam-9798	149	2	oct;155(4	oct;155(4	PROPN
bam-9798	149	3	suppl):s47	suppl):s47	PROPN
bam-9798	149	4	-	-	PUNCT
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bam-9798	149	6	.	.	PUNCT
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bam-9798	150	4	/	/	SYM
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bam-9798	150	6	.	.	PUNCT
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bam-9798	151	2	.	.	PUNCT
bam-9798	152	1	10	10	NUM
bam-9798	152	2	.	.	PUNCT
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bam-9798	152	4	a	a	PRON
bam-9798	152	5	,	,	PUNCT
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bam-9798	152	7	c	c	X
bam-9798	152	8	,	,	PUNCT
bam-9798	152	9	deschauer	deschauer	PROPN
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bam-9798	152	11	,	,	PUNCT
bam-9798	152	12	vorgerd	vorgerd	NOUN
bam-9798	152	13	m	m	PROPN
bam-9798	152	14	,	,	PUNCT
bam-9798	152	15	schrank	schrank	PROPN
bam-9798	152	16	b	b	NOUN
bam-9798	152	17	,	,	PUNCT
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bam-9798	152	19	e	e	NOUN
bam-9798	152	20	,	,	PUNCT
bam-9798	152	21	lukacs	lukacs	PROPN
bam-9798	152	22	z	z	PROPN
bam-9798	152	23	,	,	PUNCT
bam-9798	152	24	gläser	gläser	NOUN
bam-9798	152	25	d	d	NOUN
bam-9798	152	26	,	,	PUNCT
bam-9798	152	27	young	young	ADJ
bam-9798	152	28	p	p	X
bam-9798	152	29	,	,	PUNCT
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bam-9798	152	32	,	,	PUNCT
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bam-9798	152	34	b.	b.	PROPN
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bam-9798	152	40	-	-	PUNCT
bam-9798	152	41	onset	onset	VERB
bam-9798	152	42	-	-	PUNCT
bam-9798	152	43	morbus	morbus	NOUN
bam-9798	152	44	-	-	PUNCT
bam-9798	152	45	pompe	pompe	NOUN
bam-9798	153	1	[	[	X
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bam-9798	153	4	therapy	therapy	NOUN
bam-9798	153	5	of	of	ADP
bam-9798	153	6	late	late	ADJ
bam-9798	153	7	onset	onset	ADJ
bam-9798	153	8	pompe	pompe	PROPN
bam-9798	153	9	disease	disease	PROPN
bam-9798	153	10	]	]	PUNCT
bam-9798	153	11	.	.	PUNCT
bam-9798	154	1	nervenarzt	nervenarzt	PROPN
bam-9798	154	2	.	.	PUNCT
bam-9798	155	1	2013	2013	NUM
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bam-9798	155	3	-	-	SYM
bam-9798	155	4	72	72	NUM
bam-9798	155	5	.	.	PUNCT
bam-9798	156	1	german	german	NOUN
bam-9798	156	2	.	.	PUNCT
bam-9798	157	1	doi	doi	NOUN
bam-9798	157	2	:	:	PUNCT
bam-9798	157	3	10.1007	10.1007	NUM
bam-9798	157	4	/	/	SYM
bam-9798	157	5	s00115	s00115	PROPN
bam-9798	157	6	-	-	PUNCT
bam-9798	157	7	013	013	NUM
bam-9798	157	8	-	-	PUNCT
bam-9798	157	9	3947	3947	NUM
bam-9798	157	10	-	-	SYM
bam-9798	157	11	9	9	NUM
bam-9798	157	12	.	.	NOUN
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bam-9798	157	14	.	.	PUNCT
bam-9798	158	1	van	van	PROPN
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bam-9798	158	3	ploeg	ploeg	PROPN
bam-9798	158	4	at	at	ADP
bam-9798	158	5	,	,	PUNCT
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bam-9798	158	7	me	i	PRON
bam-9798	158	8	,	,	PUNCT
bam-9798	158	9	toscano	toscano	PROPN
bam-9798	158	10	a	a	PRON
bam-9798	158	11	,	,	PUNCT
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bam-9798	158	13	p	p	NOUN
bam-9798	158	14	,	,	PUNCT
bam-9798	158	15	angelini	angelini	NOUN
bam-9798	158	16	c	c	NOUN
bam-9798	158	17	,	,	PUNCT
bam-9798	158	18	lachmann	lachmann	PROPN
bam-9798	158	19	rh	rh	PROPN
bam-9798	158	20	,	,	PUNCT
bam-9798	158	21	pascual	pascual	ADJ
bam-9798	158	22	pascual	pascual	ADJ
bam-9798	158	23	si	si	X
bam-9798	158	24	,	,	PUNCT
bam-9798	158	25	roberts	roberts	PROPN
bam-9798	158	26	m	m	PROPN
bam-9798	158	27	,	,	PUNCT
bam-9798	158	28	rösler	rösler	PROPN
bam-9798	158	29	k	k	PROPN
bam-9798	158	30	,	,	PUNCT
bam-9798	158	31	stulnig	stulnig	PROPN
bam-9798	158	32	t	t	PROPN
bam-9798	158	33	,	,	PUNCT
bam-9798	158	34	van	van	PROPN
bam-9798	158	35	doorn	doorn	PROPN
bam-9798	158	36	pa	pa	PROPN
bam-9798	158	37	,	,	PUNCT
bam-9798	158	38	van	van	PROPN
bam-9798	158	39	den	den	PROPN
bam-9798	158	40	bergh	bergh	PROPN
bam-9798	158	41	pyk	pyk	PROPN
bam-9798	158	42	,	,	PUNCT
bam-9798	158	43	vissing	visse	VERB
bam-9798	158	44	j	j	PROPN
bam-9798	158	45	,	,	PUNCT
bam-9798	158	46	schoser	schoser	NOUN
bam-9798	158	47	b	b	NOUN
bam-9798	158	48	;	;	PUNCT
bam-9798	158	49	european	european	PROPN
bam-9798	158	50	pompe	pompe	PROPN
bam-9798	158	51	consortium	consortium	PROPN
bam-9798	158	52	.	.	PUNCT
bam-9798	159	1	european	european	ADJ
bam-9798	159	2	consensus	consensus	NOUN
bam-9798	159	3	for	for	ADP
bam-9798	159	4	starting	start	VERB
bam-9798	159	5	and	and	CCONJ
bam-9798	159	6	stopping	stop	VERB
bam-9798	159	7	enzyme	enzyme	NOUN
bam-9798	159	8	replacement	replacement	NOUN
bam-9798	159	9	therapy	therapy	NOUN
bam-9798	159	10	in	in	ADP
bam-9798	159	11	adult	adult	NOUN
bam-9798	159	12	patients	patient	NOUN
bam-9798	159	13	with	with	ADP
bam-9798	159	14	pompe	pompe	PROPN
bam-9798	159	15	disease	disease	PROPN
bam-9798	159	16	:	:	PUNCT
bam-9798	159	17	a	a	DET
bam-9798	159	18	10	10	NUM
bam-9798	159	19	-	-	PUNCT
bam-9798	159	20	year	year	NOUN
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bam-9798	159	22	.	.	PUNCT
bam-9798	160	1	eur	eur	PROPN
bam-9798	160	2	j	j	PROPN
bam-9798	160	3	neurol	neurol	PROPN
bam-9798	160	4	.	.	PUNCT
bam-9798	161	1	2017	2017	NUM
bam-9798	161	2	jun;24(6):768	jun;24(6):768	PROPN
bam-9798	161	3	-	-	PUNCT
bam-9798	161	4	e31	e31	PROPN
bam-9798	161	5	.	.	PUNCT
bam-9798	162	1	doi	doi	NOUN
bam-9798	162	2	:	:	PUNCT
bam-9798	162	3	10.1111	10.1111	NUM
bam-9798	162	4	/	/	SYM
bam-9798	162	5	ene.13285	ene.13285	PROPN
bam-9798	162	6	.	.	PUNCT
bam-9798	163	1	epub	epub	PROPN
bam-9798	163	2	2017	2017	NUM
bam-9798	163	3	may	may	PROPN
bam-9798	163	4	6	6	NUM
bam-9798	163	5	.	.	NOUN
bam-9798	163	6	12	12	NUM
bam-9798	163	7	slonim	slonim	PROPN
bam-9798	163	8	ae	ae	PROPN
bam-9798	163	9	,	,	PUNCT
bam-9798	163	10	bulone	bulone	PROPN
bam-9798	163	11	l	l	PROPN
bam-9798	163	12	,	,	PUNCT
bam-9798	163	13	goldberg	goldberg	PROPN
bam-9798	163	14	t	t	PROPN
bam-9798	163	15	,	,	PUNCT
bam-9798	163	16	minikes	minike	VERB
bam-9798	163	17	j	j	PROPN
bam-9798	163	18	,	,	PUNCT
bam-9798	163	19	slonim	slonim	PROPN
bam-9798	163	20	e	e	PROPN
bam-9798	163	21	,	,	PUNCT
bam-9798	163	22	galanko	galanko	PROPN
bam-9798	163	23	j	j	PROPN
bam-9798	163	24	,	,	PUNCT
bam-9798	163	25	martiniuk	martiniuk	PROPN
bam-9798	163	26	f.	f.	PROPN
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bam-9798	163	29	the	the	DET
bam-9798	163	30	natural	natural	ADJ
bam-9798	163	31	history	history	NOUN
bam-9798	163	32	of	of	ADP
bam-9798	163	33	adult	adult	NOUN
bam-9798	163	34	-	-	PUNCT
bam-9798	163	35	onset	onset	NOUN
bam-9798	163	36	acid	acid	NOUN
bam-9798	163	37	maltase	maltase	NOUN
bam-9798	163	38	deficiency	deficiency	NOUN
bam-9798	163	39	by	by	ADP
bam-9798	163	40	nutrition	nutrition	NOUN
bam-9798	163	41	and	and	CCONJ
bam-9798	163	42	exercise	exercise	NOUN
bam-9798	163	43	therapy	therapy	NOUN
bam-9798	163	44	.	.	PUNCT
bam-9798	164	1	muscle	muscle	NOUN
bam-9798	164	2	nerve	nerve	NOUN
bam-9798	164	3	.	.	PUNCT
bam-9798	165	1	2007	2007	NUM
bam-9798	165	2	jan;35(1):70	jan;35(1):70	PROPN
bam-9798	165	3	-	-	PUNCT
bam-9798	165	4	7	7	PROPN
bam-9798	165	5	.	.	PUNCT
bam-9798	165	6	doi	doi	NOUN
bam-9798	165	7	:	:	PUNCT
bam-9798	165	8	10.1002	10.1002	NUM
bam-9798	165	9	/	/	SYM
bam-9798	165	10	mus.20665	mus.20665	SYM
bam-9798	165	11	13	13	NUM
bam-9798	165	12	angelini	angelini	NOUN
bam-9798	165	13	c	c	NOUN
bam-9798	165	14	,	,	PUNCT
bam-9798	165	15	semplicini	semplicini	PROPN
bam-9798	165	16	c	c	PROPN
bam-9798	165	17	,	,	PUNCT
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bam-9798	165	20	,	,	PUNCT
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bam-9798	165	23	,	,	PUNCT
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bam-9798	165	26	,	,	PUNCT
bam-9798	165	27	musumeci	musumeci	PROPN
bam-9798	165	28	o	o	NOUN
bam-9798	165	29	,	,	PUNCT
bam-9798	165	30	pegoraro	pegoraro	NOUN
bam-9798	165	31	e	e	NOUN
bam-9798	165	32	,	,	PUNCT
bam-9798	165	33	tonin	tonin	NOUN
bam-9798	165	34	p	p	NOUN
bam-9798	165	35	,	,	PUNCT
bam-9798	165	36	filosto	filosto	PROPN
bam-9798	165	37	m	m	PROPN
bam-9798	165	38	,	,	PUNCT
bam-9798	165	39	servidei	servidei	PROPN
bam-9798	165	40	s	s	PROPN
bam-9798	165	41	,	,	PUNCT
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bam-9798	165	43	l	l	PROPN
bam-9798	165	44	,	,	PUNCT
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bam-9798	165	46	g	g	PROPN
bam-9798	165	47	,	,	PUNCT
bam-9798	165	48	marrosu	marrosu	VERB
bam-9798	165	49	g	g	PROPN
bam-9798	165	50	,	,	PUNCT
bam-9798	165	51	siciliano	siciliano	PROPN
bam-9798	165	52	g	g	PROPN
bam-9798	165	53	,	,	PUNCT
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bam-9798	165	55	t	t	PROPN
bam-9798	165	56	,	,	PUNCT
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bam-9798	165	58	a	a	ADV
bam-9798	165	59	;	;	PUNCT
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bam-9798	165	64	.	.	PUNCT
bam-9798	166	1	new	new	ADJ
bam-9798	166	2	motor	motor	NOUN
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bam-9798	166	4	function	function	NOUN
bam-9798	166	5	measures	measure	NOUN
bam-9798	166	6	in	in	ADP
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bam-9798	166	10	-	-	PUNCT
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bam-9798	166	12	pompe	pompe	NOUN
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bam-9798	166	18	replacement	replacement	NOUN
bam-9798	166	19	therapy	therapy	NOUN
bam-9798	166	20	.	.	PUNCT
bam-9798	167	1	muscle	muscle	NOUN
bam-9798	167	2	nerve	nerve	NOUN
bam-9798	167	3	.	.	PUNCT
bam-9798	168	1	2012	2012	NUM
bam-9798	168	2	jun;45(6):831	jun;45(6):831	NOUN
bam-9798	168	3	-	-	SYM
bam-9798	168	4	4	4	NUM
bam-9798	168	5	.	.	PUNCT
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bam-9798	168	7	:	:	PUNCT
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bam-9798	168	9	/	/	SYM
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bam-9798	168	11	.	.	PUNCT
bam-9798	169	1	14	14	NUM
bam-9798	169	2	.	.	PUNCT
bam-9798	170	1	sechi	sechi	PROPN
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bam-9798	170	3	,	,	PUNCT
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bam-9798	170	6	,	,	PUNCT
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bam-9798	170	9	,	,	PUNCT
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bam-9798	170	11	r	r	NOUN
bam-9798	170	12	,	,	PUNCT
bam-9798	170	13	de	de	X
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bam-9798	170	15	r	r	PROPN
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bam-9798	170	18	m	m	PROPN
bam-9798	170	19	,	,	PUNCT
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bam-9798	170	25	,	,	PUNCT
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bam-9798	170	28	,	,	PUNCT
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bam-9798	170	31	,	,	PUNCT
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bam-9798	170	34	,	,	PUNCT
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bam-9798	170	37	,	,	PUNCT
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bam-9798	170	40	,	,	PUNCT
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bam-9798	170	43	,	,	PUNCT
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bam-9798	170	45	b.	b.	PROPN
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bam-9798	170	50	in	in	ADP
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bam-9798	170	71	.	.	PUNCT
bam-9798	171	1	orphanet	orphanet	PROPN
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bam-9798	171	5	.	.	PUNCT
bam-9798	172	1	2020	2020	NUM
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bam-9798	172	4	.	.	PUNCT
bam-9798	173	1	doi	doi	NOUN
bam-9798	173	2	:	:	PUNCT
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bam-9798	173	4	/	/	SYM
bam-9798	173	5	s13023	s13023	PROPN
bam-9798	173	6	-	-	PUNCT
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bam-9798	173	8	-	-	PUNCT
bam-9798	173	9	01416	01416	NUM
bam-9798	173	10	-	-	PUNCT
bam-9798	173	11	6	6	NUM
bam-9798	173	12	.	.	NOUN
bam-9798	173	13	15	15	NUM
bam-9798	173	14	.	.	PUNCT
bam-9798	174	1	angelini	angelini	PROPN
bam-9798	174	2	c	c	PROPN
bam-9798	174	3	,	,	PUNCT
bam-9798	174	4	semplicini	semplicini	PROPN
bam-9798	174	5	c	c	PROPN
bam-9798	174	6	,	,	PUNCT
bam-9798	174	7	tonin	tonin	NOUN
bam-9798	174	8	p	p	NOUN
bam-9798	174	9	,	,	PUNCT
bam-9798	174	10	filosto	filosto	PROPN
bam-9798	174	11	m	m	PROPN
bam-9798	174	12	,	,	PUNCT
bam-9798	174	13	pegoraro	pegoraro	NOUN
bam-9798	174	14	e	e	NOUN
bam-9798	174	15	,	,	PUNCT
bam-9798	174	16	sorarù	sorarù	PROPN
bam-9798	174	17	g	g	PROPN
bam-9798	174	18	,	,	PUNCT
bam-9798	174	19	fanin	fanin	ADJ
bam-9798	174	20	m.	m.	NOUN
bam-9798	174	21	progress	progress	NOUN
bam-9798	174	22	in	in	ADP
bam-9798	174	23	enzyme	enzyme	NOUN
bam-9798	174	24	replacement	replacement	NOUN
bam-9798	174	25	therapy	therapy	NOUN
bam-9798	174	26	in	in	ADP
bam-9798	174	27	glycogen	glycogen	NOUN
bam-9798	174	28	storage	storage	NOUN
bam-9798	174	29	disease	disease	NOUN
bam-9798	174	30	type	type	PROPN
bam-9798	174	31	ii	ii	PROPN
bam-9798	174	32	.	.	PUNCT
bam-9798	175	1	ther	ther	PROPN
bam-9798	175	2	adv	adv	PROPN
bam-9798	175	3	neurol	neurol	PROPN
bam-9798	175	4	disord	disord	PROPN
bam-9798	175	5	.	.	PUNCT
bam-9798	176	1	2009	2009	NUM
bam-9798	176	2	may;2(3):143	may;2(3):143	PROPN
bam-9798	176	3	-	-	PUNCT
bam-9798	176	4	53	53	NUM
bam-9798	176	5	.	.	PUNCT
bam-9798	177	1	doi	doi	NOUN
bam-9798	177	2	:	:	PUNCT
bam-9798	177	3	10.1177/175628560910	10.1177/175628560910	NUM
bam-9798	177	4	3324	3324	NUM
bam-9798	177	5	.	.	PUNCT
bam-9798	178	1	16	16	NUM
bam-9798	178	2	angelini	angelini	PROPN
bam-9798	178	3	c	c	PROPN
bam-9798	178	4	,	,	PUNCT
bam-9798	178	5	semplicini	semplicini	PROPN
bam-9798	178	6	c	c	PROPN
bam-9798	178	7	,	,	PUNCT
bam-9798	178	8	pegoraro	pegoraro	NOUN
bam-9798	178	9	e.	e.	PROPN
bam-9798	178	10	clinical	clinical	ADJ
bam-9798	178	11	follow	follow	NOUN
bam-9798	178	12	-	-	PUNCT
bam-9798	178	13	up	up	NOUN
bam-9798	178	14	and	and	CCONJ
bam-9798	178	15	efficacy	efficacy	NOUN
bam-9798	178	16	evaluation	evaluation	NOUN
bam-9798	178	17	in	in	ADP
bam-9798	178	18	ert	ert	PROPN
bam-9798	178	19	.	.	PROPN
bam-9798	178	20	advances	advance	NOUN
bam-9798	178	21	in	in	ADP
bam-9798	178	22	diagnosis	diagnosis	NOUN
bam-9798	178	23	and	and	CCONJ
bam-9798	178	24	management	management	NOUN
bam-9798	178	25	of	of	ADP
bam-9798	178	26	glycogenosis	glycogenosis	PROPN
bam-9798	178	27	ii	ii	PROPN
bam-9798	178	28	.	.	PUNCT
bam-9798	179	1	nova	nova	PROPN
bam-9798	179	2	science	science	NOUN
bam-9798	179	3	publishers	publisher	NOUN
bam-9798	179	4	,	,	PUNCT
bam-9798	179	5	inc	inc	PROPN
bam-9798	179	6	.	.	PROPN
bam-9798	179	7	hauppauge	hauppauge	PROPN
bam-9798	179	8	,	,	PUNCT
bam-9798	179	9	ny	ny	PROPN
bam-9798	179	10	,	,	PUNCT
bam-9798	179	11	usa	usa	PROPN
bam-9798	179	12	.	.	PROPN
bam-9798	179	13	2013	2013	NUM
bam-9798	179	14	;	;	PUNCT
bam-9798	179	15	pp	pp	X
bam-9798	179	16	.	.	PUNCT
bam-9798	180	1	137	137	NUM
bam-9798	180	2	-	-	SYM
bam-9798	180	3	144	144	NUM
bam-9798	180	4	.	.	PUNCT
bam-9798	181	1	17	17	NUM
bam-9798	181	2	.	.	PUNCT
bam-9798	182	1	angelini	angelini	PROPN
bam-9798	182	2	c	c	PROPN
bam-9798	182	3	,	,	PUNCT
bam-9798	182	4	nascimbeni	nascimbeni	PROPN
bam-9798	182	5	ac	ac	PROPN
bam-9798	182	6	,	,	PUNCT
bam-9798	182	7	semplicini	semplicini	PROPN
bam-9798	182	8	c.	c.	PROPN
bam-9798	182	9	therapeutic	therapeutic	PROPN
bam-9798	182	10	advances	advance	NOUN
bam-9798	182	11	in	in	ADP
bam-9798	182	12	the	the	DET
bam-9798	182	13	management	management	NOUN
bam-9798	182	14	of	of	ADP
bam-9798	182	15	pompe	pompe	PROPN
bam-9798	182	16	disease	disease	PROPN
bam-9798	182	17	and	and	CCONJ
bam-9798	182	18	other	other	ADJ
bam-9798	182	19	metabolic	metabolic	NOUN
bam-9798	182	20	myopathies	myopathy	NOUN
bam-9798	182	21	.	.	PUNCT
bam-9798	183	1	ther	ther	VERB
bam-9798	183	2	adv	adv	PROPN
bam-9798	183	3	neurol	neurol	PROPN
bam-9798	183	4	disord	disord	PROPN
bam-9798	183	5	.	.	PUNCT
bam-9798	184	1	2013	2013	NUM
bam-9798	185	1	sep;6(5):311	sep;6(5):311	NUM
bam-9798	185	2	-	-	SYM
bam-9798	185	3	21	21	NUM
bam-9798	185	4	.	.	PUNCT
bam-9798	186	1	doi	doi	NOUN
bam-9798	186	2	:	:	PUNCT
bam-9798	186	3	10.1177/1756285613487570	10.1177/1756285613487570	NUM
bam-9798	186	4	.	.	NOUN
bam-9798	186	5	18	18	NUM
bam-9798	186	6	.	.	PUNCT
bam-9798	186	7	angelini	angelini	PROPN
bam-9798	186	8	c	c	PROPN
bam-9798	186	9	,	,	PUNCT
bam-9798	186	10	semplicini	semplicini	PROPN
bam-9798	186	11	c	c	PROPN
bam-9798	186	12	,	,	PUNCT
bam-9798	186	13	ravaglia	ravaglia	PROPN
bam-9798	186	14	s	s	PROPN
bam-9798	186	15	,	,	PUNCT
bam-9798	186	16	bembi	bembi	PROPN
bam-9798	186	17	b	b	PROPN
bam-9798	186	18	,	,	PUNCT
bam-9798	186	19	servidei	servidei	PROPN
bam-9798	186	20	s	s	PROPN
bam-9798	186	21	,	,	PUNCT
bam-9798	186	22	pegoraro	pegoraro	NOUN
bam-9798	186	23	e	e	NOUN
bam-9798	186	24	,	,	PUNCT
bam-9798	186	25	moggio	moggio	PROPN
bam-9798	186	26	m	m	PROPN
bam-9798	186	27	,	,	PUNCT
bam-9798	186	28	filosto	filosto	PROPN
bam-9798	186	29	m	m	PROPN
bam-9798	186	30	,	,	PUNCT
bam-9798	186	31	sette	sette	PROPN
bam-9798	186	32	e	e	PROPN
bam-9798	186	33	,	,	PUNCT
bam-9798	186	34	crescimanno	crescimanno	VERB
bam-9798	186	35	g	g	NOUN
bam-9798	186	36	,	,	PUNCT
bam-9798	186	37	tonin	tonin	NOUN
bam-9798	186	38	p	p	NOUN
bam-9798	186	39	,	,	PUNCT
bam-9798	186	40	parini	parini	ADJ
bam-9798	186	41	r	r	NOUN
bam-9798	186	42	,	,	PUNCT
bam-9798	186	43	morandi	morandi	PROPN
bam-9798	186	44	l	l	PROPN
bam-9798	186	45	,	,	PUNCT
bam-9798	186	46	marrosu	marrosu	VERB
bam-9798	186	47	g	g	PROPN
bam-9798	186	48	,	,	PUNCT
bam-9798	186	49	greco	greco	PROPN
bam-9798	186	50	g	g	PROPN
bam-9798	186	51	,	,	PUNCT
bam-9798	186	52	musumeci	musumeci	PROPN
bam-9798	186	53	o	o	NOUN
bam-9798	186	54	,	,	PUNCT
bam-9798	186	55	di	di	X
bam-9798	186	56	iorio	iorio	PROPN
bam-9798	186	57	g	g	PROPN
bam-9798	186	58	,	,	PUNCT
bam-9798	186	59	siciliano	siciliano	PROPN
bam-9798	186	60	g	g	PROPN
bam-9798	186	61	,	,	PUNCT
bam-9798	186	62	donati	donati	PROPN
bam-9798	186	63	ma	ma	PROPN
bam-9798	186	64	,	,	PUNCT
bam-9798	186	65	carubbi	carubbi	VERB
bam-9798	186	66	f	f	PROPN
bam-9798	186	67	,	,	PUNCT
bam-9798	186	68	ermani	ermani	PROPN
bam-9798	186	69	m	m	PROPN
bam-9798	186	70	,	,	PUNCT
bam-9798	186	71	mongini	mongini	PROPN
bam-9798	186	72	t	t	PROPN
bam-9798	186	73	,	,	PUNCT
bam-9798	186	74	toscano	toscano	PROPN
bam-9798	186	75	a	a	ADV
bam-9798	186	76	;	;	PUNCT
bam-9798	186	77	italian	italian	ADJ
bam-9798	186	78	gsdii	gsdii	NOUN
bam-9798	186	79	group	group	NOUN
bam-9798	186	80	.	.	PUNCT
bam-9798	187	1	observational	observational	ADJ
bam-9798	187	2	clinical	clinical	ADJ
bam-9798	187	3	study	study	NOUN
bam-9798	187	4	in	in	ADP
bam-9798	187	5	juvenile	juvenile	ADJ
bam-9798	187	6	-	-	PUNCT
bam-9798	187	7	adult	adult	NOUN
bam-9798	187	8	glycogenosis	glycogenosis	NOUN
bam-9798	187	9	type	type	NOUN
bam-9798	187	10	2	2	NUM
bam-9798	187	11	patients	patient	NOUN
bam-9798	187	12	undergoing	undergo	VERB
bam-9798	187	13	enzyme	enzyme	NOUN
bam-9798	187	14	replacement	replacement	NOUN
bam-9798	187	15	therapy	therapy	NOUN
bam-9798	187	16	for	for	ADP
bam-9798	187	17	up	up	ADP
bam-9798	187	18	to	to	PART
bam-9798	187	19	4	4	NUM
bam-9798	187	20	years	year	NOUN
bam-9798	187	21	.	.	PUNCT
bam-9798	188	1	j	j	PROPN
bam-9798	188	2	neurol	neurol	PROPN
bam-9798	188	3	.	.	PUNCT
bam-9798	189	1	2012	2012	NUM
bam-9798	189	2	may;259(5):952	may;259(5):952	NOUN
bam-9798	189	3	-	-	PUNCT
bam-9798	189	4	8	8	NUM
bam-9798	189	5	.	.	PUNCT
bam-9798	190	1	doi	doi	NOUN
bam-9798	190	2	:	:	PUNCT
bam-9798	190	3	10.1007	10.1007	NUM
bam-9798	190	4	/	/	SYM
bam-9798	190	5	s00415	s00415	NOUN
bam-9798	190	6	-	-	PUNCT
bam-9798	190	7	0116293	0116293	NUM
bam-9798	190	8	-	-	SYM
bam-9798	190	9	5	5	NUM
bam-9798	190	10	.	.	PUNCT
bam-9798	191	1	epub	epub	NOUN
bam-9798	191	2	2011	2011	NUM
bam-9798	191	3	nov	nov	PROPN
bam-9798	191	4	12	12	NUM
bam-9798	191	5	.	.	PUNCT
bam-9798	192	1	19	19	NUM
bam-9798	192	2	.	.	PUNCT
bam-9798	192	3	vianello	vianello	PROPN
bam-9798	192	4	a	a	PRON
bam-9798	192	5	,	,	PUNCT
bam-9798	192	6	semplicini	semplicini	PROPN
bam-9798	192	7	c	c	PROPN
bam-9798	192	8	,	,	PUNCT
bam-9798	192	9	paladini	paladini	PROPN
bam-9798	192	10	l	l	PROPN
bam-9798	192	11	,	,	PUNCT
bam-9798	192	12	concas	concas	VERB
bam-9798	192	13	a	a	PRON
bam-9798	192	14	,	,	PUNCT
bam-9798	192	15	ravaglia	ravaglia	PROPN
bam-9798	192	16	s	s	PART
bam-9798	192	17	,	,	PUNCT
bam-9798	192	18	servidei	servidei	PROPN
bam-9798	192	19	s	s	PROPN
bam-9798	192	20	,	,	PUNCT
bam-9798	192	21	toscano	toscano	X
bam-9798	192	22	a	a	PRON
bam-9798	192	23	,	,	PUNCT
bam-9798	192	24	mongini	mongini	PROPN
bam-9798	192	25	t	t	PROPN
bam-9798	192	26	,	,	PUNCT
bam-9798	192	27	angelini	angelini	PROPN
bam-9798	192	28	c	c	NOUN
bam-9798	192	29	,	,	PUNCT
bam-9798	192	30	pegoraro	pegoraro	NOUN
bam-9798	192	31	e.	e.	PROPN
bam-9798	192	32	enzyme	enzyme	PROPN
bam-9798	192	33	replacement	replacement	NOUN
bam-9798	192	34	therapy	therapy	NOUN
bam-9798	192	35	improves	improve	VERB
bam-9798	192	36	respiratory	respiratory	ADJ
bam-9798	192	37	outcomes	outcome	NOUN
bam-9798	192	38	in	in	ADP
bam-9798	192	39	patients	patient	NOUN
bam-9798	192	40	with	with	ADP
bam-9798	192	41	late	late	ADJ
bam-9798	192	42	-	-	PUNCT
bam-9798	192	43	onset	onset	NOUN
bam-9798	192	44	type	type	NOUN
bam-9798	192	45	ii	ii	NOUN
bam-9798	192	46	glycogenosis	glycogenosis	NOUN
bam-9798	192	47	and	and	CCONJ
bam-9798	192	48	high	high	ADJ
bam-9798	192	49	ventilator	ventilator	NOUN
bam-9798	192	50	dependency	dependency	NOUN
bam-9798	192	51	.	.	PUNCT
bam-9798	193	1	lung	lung	NOUN
bam-9798	193	2	.	.	PUNCT
bam-9798	194	1	2013	2013	NUM
bam-9798	194	2	oct;191(5):53744	oct;191(5):53744	NOUN
bam-9798	194	3	.	.	PUNCT
bam-9798	195	1	doi	doi	NOUN
bam-9798	195	2	:	:	PUNCT
bam-9798	195	3	10.1007	10.1007	NUM
bam-9798	195	4	/	/	SYM
bam-9798	195	5	s00408	s00408	ADJ
bam-9798	195	6	-	-	PUNCT
bam-9798	195	7	013	013	NUM
bam-9798	195	8	-	-	PUNCT
bam-9798	195	9	9489	9489	NUM
bam-9798	195	10	-	-	PUNCT
bam-9798	195	11	x.	x.	NOUN
bam-9798	195	12	epub	epub	PROPN
bam-9798	195	13	2013	2013	NUM
bam-9798	195	14	jul	jul	PROPN
bam-9798	195	15	10	10	NUM
bam-9798	195	16	.	.	PUNCT
bam-9798	196	1	20	20	NUM
bam-9798	196	2	.	.	PUNCT
bam-9798	197	1	ricci	ricci	PROPN
bam-9798	197	2	g	g	PROPN
bam-9798	197	3	,	,	PUNCT
bam-9798	197	4	baldanzi	baldanzi	PROPN
bam-9798	197	5	s	s	PROPN
bam-9798	197	6	,	,	PUNCT
bam-9798	197	7	seidita	seidita	NOUN
bam-9798	197	8	f	f	NOUN
bam-9798	197	9	,	,	PUNCT
bam-9798	197	10	proietti	proietti	NOUN
bam-9798	197	11	c	c	PROPN
bam-9798	197	12	,	,	PUNCT
bam-9798	197	13	carlini	carlini	PROPN
bam-9798	197	14	f	f	PROPN
bam-9798	197	15	,	,	PUNCT
bam-9798	197	16	peviani	peviani	PROPN
bam-9798	197	17	s	s	PROPN
bam-9798	197	18	,	,	PUNCT
bam-9798	197	19	antonini	antonini	PROPN
bam-9798	197	20	g	g	NOUN
bam-9798	197	21	,	,	PUNCT
bam-9798	197	22	vianello	vianello	PROPN
bam-9798	197	23	a	a	X
bam-9798	197	24	,	,	PUNCT
bam-9798	197	25	siciliano	siciliano	PROPN
bam-9798	197	26	g	g	PROPN
bam-9798	197	27	;	;	PUNCT
bam-9798	197	28	italian	italian	PROPN
bam-9798	197	29	gsd	gsd	PROPN
bam-9798	197	30	ii	ii	PROPN
bam-9798	197	31	group	group	NOUN
bam-9798	197	32	.	.	PUNCT
bam-9798	198	1	a	a	DET
bam-9798	198	2	mobile	mobile	ADJ
bam-9798	198	3	app	app	NOUN
bam-9798	198	4	for	for	ADP
bam-9798	198	5	patients	patient	NOUN
bam-9798	198	6	with	with	ADP
bam-9798	198	7	pompe	pompe	PROPN
bam-9798	198	8	disease	disease	NOUN
bam-9798	198	9	and	and	CCONJ
bam-9798	198	10	its	its	PRON
bam-9798	198	11	possible	possible	ADJ
bam-9798	198	12	clinical	clinical	ADJ
bam-9798	198	13	applications	application	NOUN
bam-9798	198	14	.	.	PUNCT
bam-9798	199	1	neuromuscul	neuromuscul	PROPN
bam-9798	199	2	disord	disord	PROPN
bam-9798	199	3	.	.	PUNCT
bam-9798	200	1	2018	2018	NUM
bam-9798	200	2	jun;28(6):471	jun;28(6):471	PROPN
bam-9798	200	3	-	-	PUNCT
bam-9798	200	4	475	475	PROPN
bam-9798	200	5	.	.	PUNCT
bam-9798	201	1	doi	doi	NOUN
bam-9798	201	2	:	:	PUNCT
bam-9798	201	3	10.1016	10.1016	NUM
bam-9798	201	4	/	/	SYM
bam-9798	201	5	j.nmd.2018.03.005	j.nmd.2018.03.005	NOUN
bam-9798	201	6	.	.	PUNCT
bam-9798	202	1	epub	epub	PROPN
bam-9798	202	2	2018	2018	NUM
bam-9798	202	3	mar	mar	PROPN
bam-9798	202	4	12	12	NUM
bam-9798	202	5	.	.	PUNCT
bam-9798	203	1	submitted	submit	VERB
bam-9798	203	2	:	:	PUNCT
bam-9798	203	3	april	april	PROPN
bam-9798	203	4	04	04	NUM
bam-9798	203	5	,	,	PUNCT
bam-9798	203	6	2021	2021	NUM
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bam-9798	203	9	:	:	PUNCT
bam-9798	203	10	april	april	PROPN
bam-9798	203	11	21	21	NUM
bam-9798	203	12	,	,	PUNCT
bam-9798	203	13	2021	2021	NUM
bam-9798	203	14	accepted	accept	VERB
bam-9798	203	15	for	for	ADP
bam-9798	203	16	publication	publication	NOUN
bam-9798	203	17	:	:	PUNCT
bam-9798	203	18	april	april	PROPN
bam-9798	203	19	21	21	NUM
bam-9798	203	20	,	,	PUNCT
bam-9798	203	21	2021	2021	NUM
