U J 02 - Spring 2012 - All 008- without adv.pdf


527Vol. 9   |   No. 2   |   Spring 2012   |U R O LO G Y   J O U R N A L

Keywords: ureter, embryology, vena cava, ureteral neoplasms

INTRODUCTION

T  The 
clinical and surgical implications.

CASE REPORT
A 75-year-old man presented to the emergency ward with recurrent macroscopic 
hematuria and irritative voiding symptoms. In our diagnostic process, urinalysis, 
urine cytology, intravenous urography, and cystoscopy were employed.
A tumor in the bladder and another one in the distal ureter were diagnosed. Tran-
surethral resection of the bladder tumor was initially performed and the pathology 

was subsequently performed for tumor staging, which incidentally revealed a left 

The urologic history of the patient started 5 years earlier when an urothelial pT1 
grade IIB tumor of the bladder was diagnosed. The treatment included transure-

-
cal instillations. The upper urinary tract had been examined that time with ultra-

Diomidis Kozyrakis,1 Ioannis Prombonas,1 Vasilios Kyrikos,1 Alkiviadis Grigorakis,1 Georgios 
Pliotas,2 Dimitrios Malovrouvas1

Left Retrocaval Ureter Associated With 
Urothelial Malignancy
Presentation of a Rare Case

Corresponding Author:

Diomidis Kozyrakis, MD
Sofokli Venizelou 77 St., 

Halandri, 15232, Athens, 
Greece

Tel: +30 210 681 9942
Fax: +30 210 681 1795

E-mail: dkozirakis@yahoo.
gr. 

Received April 2010
Accepted October 2010

Case Report

1Department of Urology, 
“Evagelismos” General 

Hospital of Athens, Athens, 
Greece

2Department of Urology, 
Western Attica Hospital, 

Athens, Greece



528 |

Left nephroureterectomy and radical cystoprosta-
tectomy were performed for the treatment of his 
urothelial malignancy. The nephroureterectomy 
was a laborious procedure, and accidently, an 
opening to the IVC was made, which was imme-

radical cystoprostatectomy was uncomplicated. 
The frozen section of the right ureteral margin 
was positive for urothelial malignancy and right 
distal ureterectomy with ileal loop diversion was 
performed.
The postoperative recovery was uneventful. One 
and a half year after the operation, no signs of tu-
mor recurrence, distant metastasis, or renal dys-

DISCUSSION 
In cases of a retrocaval ureter, the subcardinal vein 
generates the IVC, which results in a course of the 
ureter dorsally to this vein. The term preureteral 

for the vascular origin of the abnormality to be 
emphasized.  If the subcardinal vein persists at 

encountered.  Reviewing the international litera-

ture, only 6 cases have been reported so far.
Recurrent abdominal pain,  lumbar pain,  hydro-
nephrosis,  and nephrolithiasis  are the present-
ing symptoms of LPUVC. 
Traditionally, the combination of retrograde urog-
raphy with cavography can identify the PUVC. 
The spiral computed tomography can substantially 
contribute towards the correct diagnosis.  Should 
the use of intravenous radiopaque agents is con-
traindicated, magnetic resonance imaging can be 
performed instead.
The left IVC and PUVC may be misdiagnosed as a 
retroperitoneal lymphadenopathy or a primary tu-
mor of the retroperitoneal space.  They also pose 
a threat for vascular or tissue damage during op-
erations to the retroperitoneum, particularly when 
they are associated with situs inversus. The left re-
nal vein has a brief course, which does not cross 
the aorta and subsequently, in cases of nephrecto-
my, living renal donor surgery, and reno-vascular 

dissected from the surrounding tissues.
The treatment of PUVC is ureterotomy and relo-
cation of the ureter anteriorly to the IVC.  This 
operation is usually an open surgical procedure, 
but nowadays it can be performed laparoscopi-

Figure 1. Computed tomography of the abdomen with adminis-
tration of contrast agent. A left inferior vena cava (asterisk) and a 
retrocaval course of the left ureter (arrow) can be diagnosed.

Figure 2. Abnormal course of the left ureter, dorsally to the left 
inferior vena cava. The proximal ureter is grasped with a forceps. 
The big black arrow shows the inferior vena cava, while the small 
black one indicates the course of the ureter dorsally to the vein. 
The opening on the inferior vena cava was corrected (white 
arrow). 

Case Report



529Vol. 9   |   No. 2   |   Spring 2012   |U R O LO G Y   J O U R N A L

cally.
Apart from hematuria, no other symptoms were de-
scribed by our patient. Considering that his initial 

showed normal renal units and collecting systems 
bilaterally, it is estimated that the urothelial malig-
nancy and not the LPUVC generated a clinical evi-
dent obstruction of the left urinary tract. To the best 

PUVC is associated with urothelial malignancy.
Despite the pre-operative diagnosis, the left IVC 
and the abnormal ureteral course obscured the re-
troperitoneal structures. In our patient, an opening 
to the IVC was made. The surgeon must have a 
high index of suspicion and attention, and must be 
extremely meticulous during renal and ureteral dis-
section for any damage to the retroperitoneal or-
gans to be avoided and a source of intra-operative 
complications to be prevented.

CONFLICT OF INTEREST
None declared.

Left Retrocaval Ureter Associated With Urothelial Malignancy   |  Kozyrakis et al

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