1737Vol. 11 | No. 03 | May - June 2014 |U R O LO G Y J O U R N A L PICTORIAL Megalourethra: A Rare Clinical Entity Pawan Vasudeva, Niraj Kumar, Sanjeev Kumar Jha Corresponding Author: Pawan Vasudeva, MD Department of Urology, Vardh- man Mahavir Medical College and Safdarjang Hospital, New Delhi 110029, India. Tel: 011 2670 7426 Fax: 011 2619 0954 E-mail: drpawanvasudeva@gmail. com Received August 2013 Accepted December 2013 Department of Urology, Vardh- man Mahavir Medical College and Safdarjang Hospital, New Delhi 110029, India.a A 7 years old boy presented with history of poor urinary stream, ballooning of penis during micturition and post void dribbling since birth. Physical examination revealed an enlarged penis with redundant skin on the ventral surface (Figure 1). Both corpora cavernosa were normal. Ul- trasound of kidney, ureter and bladder demonstrated bilateral normal kidneys with negligible post void residual urine. Com- puterized tomographic (CT) voiding cystourethrogram demon- strated marked dilatation of penile urethra along with left side grade I vesicoureteral reflux (VUR) (Figure 2). A diagnosis of scaphoid megalourethra was made and the patient underwent reduction urethroplasty (Figure 3). At one year follow up, the patient is asymptomatic and the left VUR has resolved. Megalourethra, a rare congenital anomaly of the urethra, is characterized by a deficient corpus spongiosum with and without a deficient corpora cavernosum, leading to anterior urethral dilatation. Two varieties are recognized: scaphoid, in which corpus spongiosum alone is deficient and fusiform, in which both corpus spongiosum and corpus cavernosum are deficient.(1,2) Though the scaphoid variety is more com- monly seen, it is the fusiform variety which is commonly as- sociated with other congenital anomalies and hence carries a poorer prognosis.(2,3) REFERENCES 1. Kajbafzadeh A. Congenital urethral anomalies in boys. Part II. Urol J. 2005;2:125-31. 2. Khan RA, Wahab S, Ullah E. Clinics in diagnostic imaging (130). Congenital megalourethra. Singapore Med J. 2010;51:352-5. 3. Sharma AK, Shekhawat NS, Agarwal R, Upadhyay A, Mendoza WX, Harjai MM. Megalourethra: a report of four cases and review of the literature. Pediatr Surg Int. 1997;12:458-60. Figure 1. Penile appearance at presentation. Figure 3. Reduction urethroplasty: A, degloved penis showing mega- lourethra; B, urethra opened ventrally; C, urethra tapered; D, urethral repair over catheter. Figure 2. Computed tomography voiding cystourethrogram: left, two dimensional reformatted image demonstrating megalourethra; right, three dimensional reformatted image demonstrating megalourethra and left vesicoureteral reflux.